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Adrenal Cortical Sarcomatoid Carcinoma

MedGen UID:
1612498
Concept ID:
C0279579
Neoplastic Process
Synonyms: Adrenal Cortex Anaplastic Carcinoma; Adrenal Cortex Sarcomatoid Carcinoma

Definition

A carcinoma that arises from the adrenal cortex and is characterized by the partial or complete loss of adrenal cortical differentiation. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVAdrenal Cortical Sarcomatoid Carcinoma

Professional guidelines

PubMed

Fassnacht M, Dekkers OM, Else T, Baudin E, Berruti A, de Krijger R, Haak HR, Mihai R, Assie G, Terzolo M
Eur J Endocrinol 2018 Oct 1;179(4):G1-G46. doi: 10.1530/EJE-18-0608. PMID: 30299884
Stickel F, Datz C, Hampe J, Bataller R
Gut Liver 2017 Mar 15;11(2):173-188. doi: 10.5009/gnl16477. PMID: 28274107Free PMC Article
Spain L, Diem S, Larkin J
Cancer Treat Rev 2016 Mar;44:51-60. Epub 2016 Feb 6 doi: 10.1016/j.ctrv.2016.02.001. PMID: 26874776

Recent clinical studies

Etiology

Mete O, Erickson LA, Juhlin CC, de Krijger RR, Sasano H, Volante M, Papotti MG
Endocr Pathol 2022 Mar;33(1):155-196. Epub 2022 Mar 14 doi: 10.1007/s12022-022-09710-8. PMID: 35288842Free PMC Article
Kiseljak-Vassiliades K, Bancos I, Hamrahian A, Habra M, Vaidya A, Levine AC, Else T
Endocr Pract 2020 Nov;26(11):1366-1383. Epub 2020 Dec 14 doi: 10.4158/DSCR-2020-0567. PMID: 33875173Free PMC Article
Puglisi S, Calabrese A, Basile V, Pia A, Reimondo G, Perotti P, Terzolo M
Best Pract Res Clin Endocrinol Metab 2020 May;34(3):101415. Epub 2020 Mar 5 doi: 10.1016/j.beem.2020.101415. PMID: 32179008
Gaujoux S, Weinandt M, Bonnet S, Reslinger V, Bertherat J, Dousset B
J Visc Surg 2017 Oct;154(5):335-343. Epub 2017 Jul 25 doi: 10.1016/j.jviscsurg.2017.06.010. PMID: 28754418
Baudin E; Endocrine Tumor Board of Gustave Roussy
Endocrinol Metab Clin North Am 2015 Jun;44(2):411-34. doi: 10.1016/j.ecl.2015.03.001. PMID: 26038209

Diagnosis

Gambella A, Volante M, Papotti M
Adv Anat Pathol 2023 Jan 1;30(1):34-46. Epub 2022 Sep 8 doi: 10.1097/PAP.0000000000000363. PMID: 36084635
Mete O, Erickson LA, Juhlin CC, de Krijger RR, Sasano H, Volante M, Papotti MG
Endocr Pathol 2022 Mar;33(1):155-196. Epub 2022 Mar 14 doi: 10.1007/s12022-022-09710-8. PMID: 35288842Free PMC Article
Kastenberg ZJ, Scaife ER
Semin Pediatr Surg 2020 Jun;29(3):150927. Epub 2020 May 17 doi: 10.1016/j.sempedsurg.2020.150927. PMID: 32571512
Sherlock M, Scarsbrook A, Abbas A, Fraser S, Limumpornpetch P, Dineen R, Stewart PM
Endocr Rev 2020 Dec 1;41(6):775-820. doi: 10.1210/endrev/bnaa008. PMID: 32266384Free PMC Article
Longui CA
Rev Paul Pediatr 2019 Jan-Mar;37(1):2-3. doi: 10.1590/1984-0462/;2019;37;1;00021. PMID: 30726455Free PMC Article

Therapy

Ilanchezhian M, Varghese DG, Glod JW, Reilly KM, Widemann BC, Pommier Y, Kaplan RN, Del Rivero J
Front Endocrinol (Lausanne) 2022;13:961650. Epub 2022 Oct 31 doi: 10.3389/fendo.2022.961650. PMID: 36387865Free PMC Article
Kiseljak-Vassiliades K, Bancos I, Hamrahian A, Habra M, Vaidya A, Levine AC, Else T
Endocr Pract 2020 Nov;26(11):1366-1383. Epub 2020 Dec 14 doi: 10.4158/DSCR-2020-0567. PMID: 33875173Free PMC Article
Puglisi S, Calabrese A, Basile V, Pia A, Reimondo G, Perotti P, Terzolo M
Best Pract Res Clin Endocrinol Metab 2020 May;34(3):101415. Epub 2020 Mar 5 doi: 10.1016/j.beem.2020.101415. PMID: 32179008
Long SE, Miller BS
Surg Clin North Am 2019 Aug;99(4):759-771. Epub 2019 May 27 doi: 10.1016/j.suc.2019.04.012. PMID: 31255205
Baudin E; Endocrine Tumor Board of Gustave Roussy
Endocrinol Metab Clin North Am 2015 Jun;44(2):411-34. doi: 10.1016/j.ecl.2015.03.001. PMID: 26038209

Prognosis

Gambella A, Volante M, Papotti M
Adv Anat Pathol 2023 Jan 1;30(1):34-46. Epub 2022 Sep 8 doi: 10.1097/PAP.0000000000000363. PMID: 36084635
Mete O, Erickson LA, Juhlin CC, de Krijger RR, Sasano H, Volante M, Papotti MG
Endocr Pathol 2022 Mar;33(1):155-196. Epub 2022 Mar 14 doi: 10.1007/s12022-022-09710-8. PMID: 35288842Free PMC Article
Longui CA
Rev Paul Pediatr 2019 Jan-Mar;37(1):2-3. doi: 10.1590/1984-0462/;2019;37;1;00021. PMID: 30726455Free PMC Article
Else T, Kim AC, Sabolch A, Raymond VM, Kandathil A, Caoili EM, Jolly S, Miller BS, Giordano TJ, Hammer GD
Endocr Rev 2014 Apr;35(2):282-326. Epub 2013 Dec 20 doi: 10.1210/er.2013-1029. PMID: 24423978Free PMC Article
Dackiw AP, Lee JE, Gagel RF, Evans DB
World J Surg 2001 Jul;25(7):914-26. doi: 10.1007/s00268-001-0030-7. PMID: 11572033

Clinical prediction guides

Gambella A, Volante M, Papotti M
Adv Anat Pathol 2023 Jan 1;30(1):34-46. Epub 2022 Sep 8 doi: 10.1097/PAP.0000000000000363. PMID: 36084635
Mete O, Erickson LA, Juhlin CC, de Krijger RR, Sasano H, Volante M, Papotti MG
Endocr Pathol 2022 Mar;33(1):155-196. Epub 2022 Mar 14 doi: 10.1007/s12022-022-09710-8. PMID: 35288842Free PMC Article
Igaz P
Curr Opin Endocrinol Diabetes Obes 2019 Jun;26(3):155-159. doi: 10.1097/MED.0000000000000472. PMID: 30801265
Waszut U, Szyszka P, Dworakowska D
J Physiol Pharmacol 2017 Feb;68(1):13-26. PMID: 28456766
Baudin E; Endocrine Tumor Board of Gustave Roussy
Endocrinol Metab Clin North Am 2015 Jun;44(2):411-34. doi: 10.1016/j.ecl.2015.03.001. PMID: 26038209

Recent systematic reviews

Yeoh P, Czuber-Dochan W, Aylwin S, Sturt J
Endocrinol Diabetes Metab 2022 Jul;5(4):e341. Epub 2022 Jun 6 doi: 10.1002/edm2.341. PMID: 35670031Free PMC Article
Vanbrabant T, Fassnacht M, Assie G, Dekkers OM
Eur J Endocrinol 2018 Dec 1;179(6):429-436. doi: 10.1530/EJE-18-0450. PMID: 30325179
Xu X, Sergi C
Contemp Clin Trials 2016 Sep;50:37-44. Epub 2016 Jul 14 doi: 10.1016/j.cct.2016.07.011. PMID: 27424218
Machado NO, Al Qadhi H, Al Wahaibi K, Rizvi SG
JSLS 2015 Jul-Sep;19(3) doi: 10.4293/JSLS.2015.00036. PMID: 26175553Free PMC Article
Mearini L, Del Sordo R, Costantini E, Nunzi E, Porena M
Urol Int 2013;91(2):125-33. Epub 2012 Nov 8 doi: 10.1159/000345141. PMID: 23147196

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