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Hypoplastic right atrium

MedGen UID:
1624318
Concept ID:
C4531222
Congenital Abnormality
HPO: HP:0031294

Definition

Underdeveloped, small right heart atrium. [from HPO]

Term Hierarchy

Professional guidelines

PubMed

Peng R, Xie HN, Zhu YX, Li LJ, Du L, Zheng J
J Ultrasound Med 2014 Jul;33(7):1155-61. doi: 10.7863/ultra.33.7.1155. PMID: 24958401
Glatz JA, Tabbutt S, Gaynor JW, Rome JJ, Montenegro L, Spray TL, Rychik J
Ann Thorac Surg 2007 Nov;84(5):1633-8. doi: 10.1016/j.athoracsur.2007.06.061. PMID: 17954074
Bacha EA, Kreutzer J
J Interv Cardiol 2001 Jun;14(3):367-75. doi: 10.1111/j.1540-8183.2001.tb00346.x. PMID: 12053398

Recent clinical studies

Etiology

Ito T, Aoki M, Hagino I, Koshiyama H
Gen Thorac Cardiovasc Surg 2023 Jul;71(7):391-395. Epub 2023 Jan 3 doi: 10.1007/s11748-022-01897-1. PMID: 36595159
Vena F, Bartolone M, D'Alberti E, Vasta A, Mazza A, D'Ambrosio V, Mascio DD, Sulce B, Pajno C, Brunelli R, Pizzuti A, Giancotti A
J Clin Ultrasound 2023 Feb;51(2):240-248. Epub 2022 Dec 5 doi: 10.1002/jcu.23304. PMID: 36468281
Giannakou A, Sicko RJ, Kay DM, Zhang W, Romitti PA, Caggana M, Shaw GM, Jelliffe-Pawlowski LL, Mills JL
Am J Med Genet A 2018 Dec;176(12):2760-2767. Epub 2018 Oct 5 doi: 10.1002/ajmg.a.40527. PMID: 30289599
Cheatham SL, Deyo GM
Crit Care Nurse 2016 Oct;36(5):48-55. doi: 10.4037/ccn2016894. PMID: 27694357
Bo I, Carvalho JS, Cheasty E, Rubens M, Rigby ML
Cardiol Young 2016 Jun;26(5):941-7. Epub 2015 Sep 16 doi: 10.1017/S1047951115001651. PMID: 26374351

Diagnosis

Vena F, Bartolone M, D'Alberti E, Vasta A, Mazza A, D'Ambrosio V, Mascio DD, Sulce B, Pajno C, Brunelli R, Pizzuti A, Giancotti A
J Clin Ultrasound 2023 Feb;51(2):240-248. Epub 2022 Dec 5 doi: 10.1002/jcu.23304. PMID: 36468281
Cheatham SL, Deyo GM
Crit Care Nurse 2016 Oct;36(5):48-55. doi: 10.4037/ccn2016894. PMID: 27694357
Bo I, Carvalho JS, Cheasty E, Rubens M, Rigby ML
Cardiol Young 2016 Jun;26(5):941-7. Epub 2015 Sep 16 doi: 10.1017/S1047951115001651. PMID: 26374351
Peng R, Xie HN, Zhu YX, Li LJ, Du L, Zheng J
J Ultrasound Med 2014 Jul;33(7):1155-61. doi: 10.7863/ultra.33.7.1155. PMID: 24958401
Bardo DM, Frankel DG, Applegate KE, Murphy DJ, Saneto RP
Radiographics 2001 May-Jun;21(3):705-17. doi: 10.1148/radiographics.21.3.g01ma09705. PMID: 11353117

Therapy

Powel JE, Kraus E, Reddy C, Lannaman K
Fetal Diagn Ther 2022;49(5-6):245-249. Epub 2022 Jun 21 doi: 10.1159/000525593. PMID: 35728558
Januszewska K, Schuh A, Lehner A, Dalla-Pozza R, Malec E
Pediatr Cardiol 2017 Apr;38(4):712-718. Epub 2017 Feb 10 doi: 10.1007/s00246-017-1571-3. PMID: 28184977
Wehman B, Siddiqui O, Jack G, Vesely M, Li T, Mishra R, Sharma S, Taylor BS, Griffith BP, Kaushal S
Semin Thorac Cardiovasc Surg 2016 Winter;28(4):817-824. Epub 2016 Oct 14 doi: 10.1053/j.semtcvs.2016.10.003. PMID: 28417870
Fredenburg TB, Johnson TR, Cohen MD
Radiographics 2011 Mar-Apr;31(2):453-63. doi: 10.1148/rg.312105027. PMID: 21415190
Maluf MA, Carvalho AC, Carvalho WB
Rev Bras Cir Cardiovasc 2010 Oct-Dec;25(4):466-73. doi: 10.1590/s0102-76382010000400009. PMID: 21340375

Prognosis

Vena F, Bartolone M, D'Alberti E, Vasta A, Mazza A, D'Ambrosio V, Mascio DD, Sulce B, Pajno C, Brunelli R, Pizzuti A, Giancotti A
J Clin Ultrasound 2023 Feb;51(2):240-248. Epub 2022 Dec 5 doi: 10.1002/jcu.23304. PMID: 36468281
Serrano RM, Hussain S, Brown B, Ebenroth ES, Farrell A
Cardiol Young 2020 Jun;30(6):790-798. Epub 2020 May 14 doi: 10.1017/S1047951120001006. PMID: 32406345
Cheatham SL, Deyo GM
Crit Care Nurse 2016 Oct;36(5):48-55. doi: 10.4037/ccn2016894. PMID: 27694357
Bo I, Carvalho JS, Cheasty E, Rubens M, Rigby ML
Cardiol Young 2016 Jun;26(5):941-7. Epub 2015 Sep 16 doi: 10.1017/S1047951115001651. PMID: 26374351
Maluf MA, Carvalho AC, Carvalho WB
Rev Bras Cir Cardiovasc 2010 Oct-Dec;25(4):466-73. doi: 10.1590/s0102-76382010000400009. PMID: 21340375

Clinical prediction guides

Ito T, Aoki M, Hagino I, Koshiyama H
Gen Thorac Cardiovasc Surg 2023 Jul;71(7):391-395. Epub 2023 Jan 3 doi: 10.1007/s11748-022-01897-1. PMID: 36595159
Melovitz-Vasan C, White A, Huff S, Vasan N
Folia Morphol (Warsz) 2023;82(4):980-987. Epub 2022 Dec 6 doi: 10.5603/FM.a2022.0098. PMID: 36472398
Kobayashi Y, Kotani Y, Kuroko Y, Kawabata T, Sano S, Kasahara S
Eur J Cardiothorac Surg 2020 Aug 1;58(2):230-236. doi: 10.1093/ejcts/ezaa041. PMID: 32211760
Tang C, Duan H, Zhou K, Hua Y, Liu X, Li Y, Wang C
Medicine (Baltimore) 2018 Aug;97(34):e11882. doi: 10.1097/MD.0000000000011882. PMID: 30142786Free PMC Article
Anderson RH, Wilkinson JL, Gerlis LM, Smith A, Becker AE
Br Heart J 1977 Apr;39(4):414-28. doi: 10.1136/hrt.39.4.414. PMID: 869977Free PMC Article

Recent systematic reviews

Dorobantu DM, Amir NH, Wadey CA, Sharma C, Stuart AG, Williams CA, Pieles GE
J Am Soc Echocardiogr 2024 Feb;37(2):216-225. Epub 2023 Nov 14 doi: 10.1016/j.echo.2023.11.003. PMID: 37972793

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