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Mucinous cystic neoplasm of the pancreas

MedGen UID:
1627886
Concept ID:
C4531085
Neoplastic Process
HPO: HP:0031496

Definition

Mucin-producing and septated cyst-forming epithelial neoplasia of the pancreas with a distinctive ovarian-type stroma. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVMucinous cystic neoplasm of the pancreas

Professional guidelines

PubMed

Tanaka M, Fernández-del Castillo C, Adsay V, Chari S, Falconi M, Jang JY, Kimura W, Levy P, Pitman MB, Schmidt CM, Shimizu M, Wolfgang CL, Yamaguchi K, Yamao K; International Association of Pancreatology
Pancreatology 2012 May-Jun;12(3):183-97. Epub 2012 Apr 16 doi: 10.1016/j.pan.2012.04.004. PMID: 22687371
Testini M, Gurrado A, Lissidini G, Venezia P, Greco L, Piccinni G
World J Gastroenterol 2010 Dec 7;16(45):5682-92. doi: 10.3748/wjg.v16.i45.5682. PMID: 21128317Free PMC Article

Recent clinical studies

Etiology

Hozaka Y, Ohtsuka T, Nakamura M, Hijioka S, Unno M, Shimizu Y, Tanabe M, Nagakawa Y, Hatano E, Kawai M, Sano T, Koshita S, Katanuma A, Kita E, Hanada K, Nakai Y, Aoki T, Serikawa M, Okamoto K, Takeyama Y
Pancreas 2023 May 1;52(5):e288-e292. Epub 2023 Nov 3 doi: 10.1097/MPA.0000000000002254. PMID: 37922344
Park JW, Jang JY, Kang MJ, Kwon W, Chang YR, Kim SW
Pancreatology 2014 Mar-Apr;14(2):131-6. Epub 2014 Jan 8 doi: 10.1016/j.pan.2013.12.006. PMID: 24650968
Tanaka M, Fernández-del Castillo C, Adsay V, Chari S, Falconi M, Jang JY, Kimura W, Levy P, Pitman MB, Schmidt CM, Shimizu M, Wolfgang CL, Yamaguchi K, Yamao K; International Association of Pancreatology
Pancreatology 2012 May-Jun;12(3):183-97. Epub 2012 Apr 16 doi: 10.1016/j.pan.2012.04.004. PMID: 22687371
Crippa S, Salvia R, Warshaw AL, Domínguez I, Bassi C, Falconi M, Thayer SP, Zamboni G, Lauwers GY, Mino-Kenudson M, Capelli P, Pederzoli P, Castillo CF
Ann Surg 2008 Apr;247(4):571-9. doi: 10.1097/SLA.0b013e31811f4449. PMID: 18362619Free PMC Article
Fujiwara H, Ajiki T, Fukuoka K, Mitsutsuji M, Yamamoto M, Kuroda Y
J Hepatobiliary Pancreat Surg 2000;7(1):92-6. doi: 10.1007/s005340050160. PMID: 10982598

Diagnosis

Hozaka Y, Ohtsuka T, Nakamura M, Hijioka S, Unno M, Shimizu Y, Tanabe M, Nagakawa Y, Hatano E, Kawai M, Sano T, Koshita S, Katanuma A, Kita E, Hanada K, Nakai Y, Aoki T, Serikawa M, Okamoto K, Takeyama Y
Pancreas 2023 May 1;52(5):e288-e292. Epub 2023 Nov 3 doi: 10.1097/MPA.0000000000002254. PMID: 37922344
Hisanaga E, Sano T, Yoshida Y, Ishii N, Shirabe K, Ikota H
Clin J Gastroenterol 2021 Jun;14(3):910-917. Epub 2021 Mar 12 doi: 10.1007/s12328-021-01380-z. PMID: 33710503
Mederos MA, Villafañe N, Dhingra S, Farinas C, McElhany A, Fisher WE, Van Buren Ii G
World J Gastroenterol 2017 Feb 14;23(6):1113-1118. doi: 10.3748/wjg.v23.i6.1113. PMID: 28246486Free PMC Article
Asberry DE, Youngberg GA, Al-Abbadi MA
Saudi Med J 2013 Jan;34(1):80-5. PMID: 23299164
Testini M, Gurrado A, Lissidini G, Venezia P, Greco L, Piccinni G
World J Gastroenterol 2010 Dec 7;16(45):5682-92. doi: 10.3748/wjg.v16.i45.5682. PMID: 21128317Free PMC Article

Therapy

Miwa H, Sugimori K, Ishii T, Funaoka A, Tsuchiya H, Suzuki Y, Sugimori M, Nishimura M, Tozuka Y, Komiyama S, Sato T, Kaneko T, Numata K, Maeda S
Intern Med 2021 Aug 15;60(16):2607-2612. Epub 2021 Mar 1 doi: 10.2169/internalmedicine.6755-20. PMID: 33642489Free PMC Article
Holloman C, Carlan SJ, Sundharkrishnan L, Guzman A, Madruga M
J Med Case Rep 2017 Jul 11;11(1):188. doi: 10.1186/s13256-017-1343-y. PMID: 28693619Free PMC Article
Testini M, Gurrado A, Lissidini G, Venezia P, Greco L, Piccinni G
World J Gastroenterol 2010 Dec 7;16(45):5682-92. doi: 10.3748/wjg.v16.i45.5682. PMID: 21128317Free PMC Article
Kimura W, Ma J, Takeshita A, Yamamoto T, Moriya T, Hirai I, Fuse A
Hepatogastroenterology 2007 Dec;54(80):2203-8. PMID: 18265633

Prognosis

Ahmad M, Maegawa FB, De La Rosa E, Davis B, Tyroch A, Konstantinidis IT
Am J Surg 2020 Dec;220(6):1433-1437. Epub 2020 Sep 6 doi: 10.1016/j.amjsurg.2020.09.006. PMID: 32938530
Ohtsuka T, Nakamura M, Hijioka S, Shimizu Y, Unno M, Tanabe M, Nagakawa Y, Takaori K, Hirono S, Gotohda N, Kimura W, Ito K, Katanuma A, Sano T, Urata T, Kita E, Hanada K, Tada M, Aoki T, Serikawa M, Okamoto K, Isayama H, Gotoh Y, Ishigami K, Yamaguchi H, Yamao K, Sugiyama M, Okazaki K
Pancreas 2020 Feb;49(2):181-186. doi: 10.1097/MPA.0000000000001475. PMID: 32011526
Tsuda H, Kotani T, Sumigama S, Mano Y, Shimoyama Y, Kikkawa F
Taiwan J Obstet Gynecol 2012 Dec;51(4):635-8. doi: 10.1016/j.tjog.2012.09.022. PMID: 23276571
Testini M, Gurrado A, Lissidini G, Venezia P, Greco L, Piccinni G
World J Gastroenterol 2010 Dec 7;16(45):5682-92. doi: 10.3748/wjg.v16.i45.5682. PMID: 21128317Free PMC Article
Crippa S, Salvia R, Warshaw AL, Domínguez I, Bassi C, Falconi M, Thayer SP, Zamboni G, Lauwers GY, Mino-Kenudson M, Capelli P, Pederzoli P, Castillo CF
Ann Surg 2008 Apr;247(4):571-9. doi: 10.1097/SLA.0b013e31811f4449. PMID: 18362619Free PMC Article

Clinical prediction guides

Ohtsuka T, Nakamura M, Hijioka S, Shimizu Y, Unno M, Tanabe M, Nagakawa Y, Takaori K, Hirono S, Gotohda N, Kimura W, Ito K, Katanuma A, Sano T, Urata T, Kita E, Hanada K, Tada M, Aoki T, Serikawa M, Okamoto K, Isayama H, Gotoh Y, Ishigami K, Yamaguchi H, Yamao K, Sugiyama M, Okazaki K
Pancreas 2020 Feb;49(2):181-186. doi: 10.1097/MPA.0000000000001475. PMID: 32011526
Matsumoto Y, Miyamoto H, Fukuya A, Nakamura F, Goji T, Kitamura S, Kimura T, Okamoto K, Sogabe M, Muguruma N, Shimada M, Bando Y, Takayama T
Clin J Gastroenterol 2017 Apr;10(2):185-190. Epub 2017 Jan 4 doi: 10.1007/s12328-016-0711-2. PMID: 28054178
Park JW, Jang JY, Kang MJ, Kwon W, Chang YR, Kim SW
Pancreatology 2014 Mar-Apr;14(2):131-6. Epub 2014 Jan 8 doi: 10.1016/j.pan.2013.12.006. PMID: 24650968
Tsuda H, Kotani T, Sumigama S, Mano Y, Shimoyama Y, Kikkawa F
Taiwan J Obstet Gynecol 2012 Dec;51(4):635-8. doi: 10.1016/j.tjog.2012.09.022. PMID: 23276571
Testini M, Gurrado A, Lissidini G, Venezia P, Greco L, Piccinni G
World J Gastroenterol 2010 Dec 7;16(45):5682-92. doi: 10.3748/wjg.v16.i45.5682. PMID: 21128317Free PMC Article

Recent systematic reviews

Testini M, Gurrado A, Lissidini G, Venezia P, Greco L, Piccinni G
World J Gastroenterol 2010 Dec 7;16(45):5682-92. doi: 10.3748/wjg.v16.i45.5682. PMID: 21128317Free PMC Article

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