U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Unroofed coronary sinus

MedGen UID:
1638932
Concept ID:
C4551626
Congenital Abnormality
SNOMED CT: Unroofed coronary sinus (40272001)
 
HPO: HP:0031297

Definition

Unroofed coronary sinus (CS) is a rare congenital cardiac anomaly in which there is partial (either focal or fenestrated) or complete absence of the roof of the CS, which results in a communication between the CS and the LA. Unroofed CS is the rarest type of atrial septal defect. It is often associated with persistent left superior vena cava (LSVC) and other forms of complex congenital heart disease, usually heterotaxia syndromes. The morphological types have been classified into 4 groups [from HPO]

Term Hierarchy

Professional guidelines

PubMed

Cinteză EE, Filip C, Duică G, Nicolae G, Nicolescu AM, Bălgrădean M
Rom J Morphol Embryol 2019;60(1):33-40. PMID: 31263825
Wang JK, Chen SJ, Hsu JY, Lin SM, Lin MT, Chiu SN, Chen CA, Wu MH
Catheter Cardiovasc Interv 2014 Feb;83(2):243-9. Epub 2013 Oct 30 doi: 10.1002/ccd.25185. PMID: 24038929
Xie MX, Yang YL, Cheng TO, Wang XF, Li K, Ren PP, Lü Q, Lin H, Li L
Int J Cardiol 2013 Sep 30;168(2):1258-63. Epub 2012 Dec 23 doi: 10.1016/j.ijcard.2012.11.113. PMID: 23266300

Recent clinical studies

Etiology

Zou F, Worley SJ, Steen T, McKillop M, Padala S, O'Donoghue S, Candemir B, Kanjwal K, Kaufman M, Mouram S, Sellers M, Strouse D, Thomaides A, Nair D, Hadadi CA, Kushnir A
Heart Rhythm 2021 Jul;18(7):1064-1073. Epub 2021 May 8 doi: 10.1016/j.hrthm.2021.05.004. PMID: 33971333
Sun L, Juan YH, Chen J, Zhuang J, Xie J, Li H, Liu H
AJR Am J Roentgenol 2018 Aug;211(2):314-320. Epub 2018 Jun 27 doi: 10.2214/AJR.17.19128. PMID: 29949414
Ouchi K, Sakuma T, Kawai M, Fukuda K
Jpn J Radiol 2016 Oct;34(10):684-690. Epub 2016 Aug 11 doi: 10.1007/s11604-016-0574-y. PMID: 27516063
Xie MX, Yang YL, Cheng TO, Wang XF, Li K, Ren PP, Lü Q, Lin H, Li L
Int J Cardiol 2013 Sep 30;168(2):1258-63. Epub 2012 Dec 23 doi: 10.1016/j.ijcard.2012.11.113. PMID: 23266300
Kim H, Choe YH, Park SW, Jun TG, Kang IS, Yang JH, Eo H, Lee HJ
AJR Am J Roentgenol 2010 Nov;195(5):W331-6. doi: 10.2214/AJR.09.3689. PMID: 20966297

Diagnosis

Ma J, Zheng Y, Xu S, Teng H, Lv L, Li Y, Liang Y, Zhang Y
BMC Cardiovasc Disord 2022 Dec 2;22(1):516. doi: 10.1186/s12872-022-02966-2. PMID: 36460953Free PMC Article
Shi H, Yan J, Wang Q, Hua Z, Li S, Zhang J
J Card Surg 2021 Feb;36(2):589-595. Epub 2020 Dec 23 doi: 10.1111/jocs.15269. PMID: 33355957
Cinteză EE, Filip C, Duică G, Nicolae G, Nicolescu AM, Bălgrădean M
Rom J Morphol Embryol 2019;60(1):33-40. PMID: 31263825
Karavelioglu Y, Cagli K, Yetim M, Bekar L, Golbasi Z
Echocardiography 2019 Mar;36(3):613-614. Epub 2019 Feb 8 doi: 10.1111/echo.14274. PMID: 30735270
Xie MX, Yang YL, Cheng TO, Wang XF, Li K, Ren PP, Lü Q, Lin H, Li L
Int J Cardiol 2013 Sep 30;168(2):1258-63. Epub 2012 Dec 23 doi: 10.1016/j.ijcard.2012.11.113. PMID: 23266300

Therapy

Castiglione A, Küffer T, Gräni C, Servatius H, Reichlin T, Roten L
J Cardiovasc Electrophysiol 2023 May;34(5):1183-1191. Epub 2023 Apr 26 doi: 10.1111/jce.15900. PMID: 37003265
Mohammad Nijres B, Al-Kubaisi M, Bokowski J, Abdulla RI, Awad S
Pediatr Cardiol 2017 Jun;38(5):1084-1086. Epub 2017 Apr 10 doi: 10.1007/s00246-017-1613-x. PMID: 28396933
Mohammad Nijres B, Kenny D, Kazmouz S, Hijazi ZM
Catheter Cardiovasc Interv 2017 Dec 1;90(7):1154-1157. Epub 2017 Mar 15 doi: 10.1002/ccd.26996. PMID: 28296217
Wang JK, Chen SJ, Hsu JY, Lin SM, Lin MT, Chiu SN, Chen CA, Wu MH
Catheter Cardiovasc Interv 2014 Feb;83(2):243-9. Epub 2013 Oct 30 doi: 10.1002/ccd.25185. PMID: 24038929
Giuliani-Poncini C, Perez MH, Cotting J, Hurni M, Sekarski N, Pfammatter JP, Di Bernardo S
Pediatr Cardiol 2014 Jan;35(1):71-6. Epub 2013 Jul 3 doi: 10.1007/s00246-013-0743-z. PMID: 23821295

Prognosis

Ojukwu O, Zook S, Kleiman N, Lawrie G, Kassi M
Methodist Debakey Cardiovasc J 2022;18(4):89-93. Epub 2022 Sep 6 doi: 10.14797/mdcvj.1159. PMID: 36188096Free PMC Article
Chen C, Xu L, Xu Y, Li P, Liu S, You B
Heart Lung Circ 2018 Jun;27(6):731-738. Epub 2017 Jun 22 doi: 10.1016/j.hlc.2017.05.144. PMID: 28709918
Ouchi K, Sakuma T, Kawai M, Fukuda K
Jpn J Radiol 2016 Oct;34(10):684-690. Epub 2016 Aug 11 doi: 10.1007/s11604-016-0574-y. PMID: 27516063
Santoro G, Gaio G, Russo MG
Catheter Cardiovasc Interv 2013 Apr;81(5):849-52. Epub 2012 Sep 7 doi: 10.1002/ccd.24519. PMID: 22718686
Cannavale G, Higgins CB, Ordovas KG
Int J Cardiovasc Imaging 2010 Dec;26(8):841-2. Epub 2010 Jul 8 doi: 10.1007/s10554-010-9667-3. PMID: 20614189

Clinical prediction guides

Shi H, Yan J, Wang Q, Hua Z, Li S, Zhang J
J Card Surg 2021 Feb;36(2):589-595. Epub 2020 Dec 23 doi: 10.1111/jocs.15269. PMID: 33355957
Sun L, Juan YH, Chen J, Zhuang J, Xie J, Li H, Liu H
AJR Am J Roentgenol 2018 Aug;211(2):314-320. Epub 2018 Jun 27 doi: 10.2214/AJR.17.19128. PMID: 29949414
Santoro G, Gaio G, Russo MG
Catheter Cardiovasc Interv 2013 Apr;81(5):849-52. Epub 2012 Sep 7 doi: 10.1002/ccd.24519. PMID: 22718686
Cannavale G, Higgins CB, Ordovas KG
Int J Cardiovasc Imaging 2010 Dec;26(8):841-2. Epub 2010 Jul 8 doi: 10.1007/s10554-010-9667-3. PMID: 20614189
Chen MC, Hung JS, Chang KC, Lo PH, Chen YC, Fu M
J Ultrasound Med 1996 Dec;15(12):875-9. doi: 10.7863/jum.1996.15.12.875. PMID: 8947865

Supplemental Content

Table of contents

    Clinical resources

    Practice guidelines

    • PubMed
      See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Consumer resources

    Recent activity

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...