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Pulmonary Artery Intimal Sarcoma

MedGen UID:
1643290
Concept ID:
C4684845
Neoplastic Process
Synonyms: Intimal Sarcoma of the Pulmonary Artery; Pulmonary Artery Sarcoma; Pulmonary Intimal Sarcoma

Definition

A sarcoma arising from the arterial intima of pulmonary arteries. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVPulmonary Artery Intimal Sarcoma

Professional guidelines

PubMed

Attinà D, Niro F, Tchouanté P, Mineo G, Russo V, Palazzini M, Galiè N, Fanti S, Lovato L, Zompatori M
Radiol Med 2013 Dec;118(8):1259-68. Epub 2013 Jun 25 doi: 10.1007/s11547-013-0943-x. PMID: 23801391

Recent clinical studies

Etiology

Kim C, Kim MY, Kang JW, Song JS, Lee KY, Kim SS
Korean J Radiol 2018 Jul-Aug;19(4):792-802. Epub 2018 Jun 14 doi: 10.3348/kjr.2018.19.4.792. PMID: 29962886Free PMC Article
Gaumann A, Bode-Lesniewska B, Zimmermann DR, Fanburg-Smith JC, Kirkpatrick CJ, Hofstädter F, Woenckhaus M, Stoehr R, Obermann EC, Dietmaier W, Hartmann A
Virchows Arch 2008 Nov;453(5):473-84. Epub 2008 Sep 20 doi: 10.1007/s00428-008-0671-0. PMID: 18807072

Diagnosis

Jiang W, Liu M, Guo X, Li J, Gong J, Yang M, Liu Y, Gu S, Li Y, Yang Y, Lv X
Heart Lung Circ 2023 Sep;32(9):1080-1088. Epub 2023 Jun 22 doi: 10.1016/j.hlc.2023.05.013. PMID: 37355431
Zhao M, Nie P, Guo Y, Chen H
Am J Med Sci 2022 Nov;364(5):655-660. Epub 2022 May 16 doi: 10.1016/j.amjms.2022.05.009. PMID: 35588894
Li YC, Li LY, Tong HC, Xu HT, Ma S, Yang LH, Zhang WL, Sotolongo G, Wang E
Medicine (Baltimore) 2021 Feb 12;100(6):e24699. doi: 10.1097/MD.0000000000024699. PMID: 33578605Free PMC Article
Masuda S, Itagaki K, Naganuma M, Suzuki N, Kurotaki H, Nagaya K
Asian Cardiovasc Thorac Ann 2020 Jun;28(5):282-285. Epub 2020 Jun 2 doi: 10.1177/0218492320932746. PMID: 32483975
Kim C, Kim MY, Kang JW, Song JS, Lee KY, Kim SS
Korean J Radiol 2018 Jul-Aug;19(4):792-802. Epub 2018 Jun 14 doi: 10.3348/kjr.2018.19.4.792. PMID: 29962886Free PMC Article

Therapy

Masuda S, Itagaki K, Naganuma M, Suzuki N, Kurotaki H, Nagaya K
Asian Cardiovasc Thorac Ann 2020 Jun;28(5):282-285. Epub 2020 Jun 2 doi: 10.1177/0218492320932746. PMID: 32483975
Attinà D, Niro F, Tchouanté P, Mineo G, Russo V, Palazzini M, Galiè N, Fanti S, Lovato L, Zompatori M
Radiol Med 2013 Dec;118(8):1259-68. Epub 2013 Jun 25 doi: 10.1007/s11547-013-0943-x. PMID: 23801391

Prognosis

Bai X, Ruan L
Eur J Med Res 2021 Aug 9;26(1):89. doi: 10.1186/s40001-021-00568-w. PMID: 34372932Free PMC Article
Li YC, Li LY, Tong HC, Xu HT, Ma S, Yang LH, Zhang WL, Sotolongo G, Wang E
Medicine (Baltimore) 2021 Feb 12;100(6):e24699. doi: 10.1097/MD.0000000000024699. PMID: 33578605Free PMC Article
Masuda S, Itagaki K, Naganuma M, Suzuki N, Kurotaki H, Nagaya K
Asian Cardiovasc Thorac Ann 2020 Jun;28(5):282-285. Epub 2020 Jun 2 doi: 10.1177/0218492320932746. PMID: 32483975
Umezawa K, Takamura K, Yamamoto M, Kikuchi K
Am J Respir Crit Care Med 2014 Dec 15;190(12):e67-8. doi: 10.1164/rccm.201407-1311IM. PMID: 25496110
Attinà D, Niro F, Tchouanté P, Mineo G, Russo V, Palazzini M, Galiè N, Fanti S, Lovato L, Zompatori M
Radiol Med 2013 Dec;118(8):1259-68. Epub 2013 Jun 25 doi: 10.1007/s11547-013-0943-x. PMID: 23801391

Clinical prediction guides

Luo R, Jiang Y, Huang Y, Chen X, Wang F
J Cardiothorac Surg 2020 Sep 1;15(1):233. doi: 10.1186/s13019-020-01271-3. PMID: 32873341Free PMC Article
Masuda S, Itagaki K, Naganuma M, Suzuki N, Kurotaki H, Nagaya K
Asian Cardiovasc Thorac Ann 2020 Jun;28(5):282-285. Epub 2020 Jun 2 doi: 10.1177/0218492320932746. PMID: 32483975
Ro A, Mori S, Sugiura H, Furukawa T, Asakura K, Kimura S, Kageyama N, Chiba S, Mukai T
Cardiovasc Pathol 2019 Nov-Dec;43:107143. Epub 2019 Jul 26 doi: 10.1016/j.carpath.2019.07.002. PMID: 31437715

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