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Unresectable Adrenal Cortical Carcinoma

MedGen UID:
1653709
Concept ID:
C4725848
Neoplastic Process
Synonym: Unresectable Adrenal Cortex Carcinoma

Definition

Adrenal cortical carcinoma that is not amenable to surgical resection. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVUnresectable Adrenal Cortical Carcinoma

Professional guidelines

PubMed

Tierney JF, Chivukula SV, Poirier J, Pappas SG, Schadde E, Hertl M, Kebebew E, Keutgen X
J Clin Endocrinol Metab 2019 Dec 1;104(12):5948-5956. doi: 10.1210/jc.2019-00915. PMID: 31361313
Dickson PV, Kim L, Yen TWF, Yang A, Grubbs EG, Patel D, Solórzano CC
Ann Surg Oncol 2018 Nov;25(12):3453-3459. Epub 2018 Sep 14 doi: 10.1245/s10434-018-6750-9. PMID: 30218246
Kopf D, Goretzki PE, Lehnert H
J Cancer Res Clin Oncol 2001;127(3):143-55. doi: 10.1007/s004320000170. PMID: 11260859

Recent clinical studies

Etiology

Oesterreich R, Varela MF, Moldes J, Lobos P
Pediatr Surg Int 2022 Oct;38(10):1435-1444. Epub 2022 Jul 25 doi: 10.1007/s00383-022-05188-x. PMID: 35876904
Dickson PV, Kim L, Yen TWF, Yang A, Grubbs EG, Patel D, Solórzano CC
Ann Surg Oncol 2018 Nov;25(12):3453-3459. Epub 2018 Sep 14 doi: 10.1245/s10434-018-6750-9. PMID: 30218246
Sabolch A, Feng M, Griffith K, Hammer G, Doherty G, Ben-Josef E
Int J Radiat Oncol Biol Phys 2011 Aug 1;80(5):1477-84. Epub 2010 Aug 1 doi: 10.1016/j.ijrobp.2010.04.030. PMID: 20675074
Gertner ME, Kebebew E
Curr Treat Options Oncol 2004 Aug;5(4):315-25. doi: 10.1007/s11864-004-0022-6. PMID: 15233908
Cohn K, Gottesman L, Brennan M
Surgery 1986 Dec;100(6):1170-7. PMID: 3787475

Diagnosis

Oesterreich R, Varela MF, Moldes J, Lobos P
Pediatr Surg Int 2022 Oct;38(10):1435-1444. Epub 2022 Jul 25 doi: 10.1007/s00383-022-05188-x. PMID: 35876904
Koschker AC, Fassnacht M, Hahner S, Weismann D, Allolio B
Exp Clin Endocrinol Diabetes 2006 Feb;114(2):45-51. doi: 10.1055/s-2006-923808. PMID: 16570232
Rescorla FJ
Semin Pediatr Surg 2006 Feb;15(1):48-56. doi: 10.1053/j.sempedsurg.2005.11.008. PMID: 16458846
Roman S
Curr Opin Oncol 2006 Jan;18(1):36-42. doi: 10.1097/01.cco.0000198976.43992.14. PMID: 16357562
Kopf D, Goretzki PE, Lehnert H
J Cancer Res Clin Oncol 2001;127(3):143-55. doi: 10.1007/s004320000170. PMID: 11260859

Therapy

Dickson PV, Kim L, Yen TWF, Yang A, Grubbs EG, Patel D, Solórzano CC
Ann Surg Oncol 2018 Nov;25(12):3453-3459. Epub 2018 Sep 14 doi: 10.1245/s10434-018-6750-9. PMID: 30218246
Koschker AC, Fassnacht M, Hahner S, Weismann D, Allolio B
Exp Clin Endocrinol Diabetes 2006 Feb;114(2):45-51. doi: 10.1055/s-2006-923808. PMID: 16570232
Roman S
Curr Opin Oncol 2006 Jan;18(1):36-42. doi: 10.1097/01.cco.0000198976.43992.14. PMID: 16357562
Wood BJ, Abraham J, Hvizda JL, Alexander HR, Fojo T
Cancer 2003 Feb 1;97(3):554-60. doi: 10.1002/cncr.11084. PMID: 12548596Free PMC Article
Kopf D, Goretzki PE, Lehnert H
J Cancer Res Clin Oncol 2001;127(3):143-55. doi: 10.1007/s004320000170. PMID: 11260859

Prognosis

Torres MB, Diggs LP, Wei JS, Khan J, Miettinen M, Fasaye GA, Gillespie A, Widemann BC, Kaplan RN, Davis JL, Hernandez JM, Rivero JD
Cancer Genet 2021 Aug;256-257:21-25. Epub 2021 Mar 24 doi: 10.1016/j.cancergen.2021.03.003. PMID: 33836455
Xie H, Yin J, Shah MH, Menefee ME, Bible KC, Reidy-Lagunes D, Kane MA, Quinn DI, Gandara DR, Erlichman C, Adjei AA
Invest New Drugs 2019 Aug;37(4):755-762. Epub 2019 Jun 6 doi: 10.1007/s10637-019-00797-1. PMID: 31172443Free PMC Article
Rescorla FJ
Semin Pediatr Surg 2006 Feb;15(1):48-56. doi: 10.1053/j.sempedsurg.2005.11.008. PMID: 16458846
Gertner ME, Kebebew E
Curr Treat Options Oncol 2004 Aug;5(4):315-25. doi: 10.1007/s11864-004-0022-6. PMID: 15233908
Percarpio B, Knowlton AH
Acta Radiol Ther Phys Biol 1976 Aug;15(4):288-92. doi: 10.3109/02841867609131965. PMID: 62490

Clinical prediction guides

Baur J, Büntemeyer TO, Megerle F, Deutschbein T, Spitzweg C, Quinkler M, Nawroth P, Kroiss M, Germer CT, Fassnacht M, Steger U; German Adrenocortical Carcinoma Study Group
BMC Cancer 2017 Aug 4;17(1):522. doi: 10.1186/s12885-017-3506-z. PMID: 28778197Free PMC Article

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