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Refractory Adult T-Cell Leukemia/Lymphoma

MedGen UID:
167720
Concept ID:
C0854818
Neoplastic Process
Synonyms: Adult T-Cell Lymphoma/Leukemia Refractory; Refractory Adult T-Cell Lymphoma/Leukemia

Definition

Adult T-cell leukemia/lymphoma that is resistant to treatment. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVRefractory Adult T-Cell Leukemia/Lymphoma

Professional guidelines

PubMed

Winsett FT, Lewis DJ, Duvic M
Expert Rev Hematol 2017 Sep;10(9):757-760. Epub 2017 Aug 21 doi: 10.1080/17474086.2017.1361819. PMID: 28756726

Recent clinical studies

Etiology

Utsunomiya A, Izutsu K, Jo T, Yoshida S, Tsukasaki K, Ando K, Choi I, Imaizumi Y, Kato K, Kurosawa M, Kusumoto S, Miyagi T, Ohtsuka E, Sasaki O, Shibayama H, Shimoda K, Takamatsu Y, Takano K, Yonekura K, Makita S, Taguchi J, Gillings M, Onogi H, Tobinai K
Cancer Sci 2022 Aug;113(8):2778-2787. Epub 2022 Jun 7 doi: 10.1111/cas.15431. PMID: 35579212Free PMC Article
Nosaka K, Crawford B, Yi J, Kuan W, Matsumoto T, Takahashi T
Eur J Haematol 2022 Mar;108(3):212-222. Epub 2021 Dec 8 doi: 10.1111/ejh.13728. PMID: 34862665Free PMC Article
Ishitsuka K, Yurimoto S, Tsuji Y, Iwabuchi M, Takahashi T, Tobinai K
Eur J Haematol 2019 May;102(5):407-415. Epub 2019 Mar 12 doi: 10.1111/ejh.13220. PMID: 30740787Free PMC Article
Phillips AA, Fields PA, Hermine O, Ramos JC, Beltran BE, Pereira J, Wandroo F, Feldman T, Taylor GP, Sawas A, Humphrey J, Kurman M, Moriya J, Dwyer K, Leoni M, Conlon K, Cook L, Gonsky J, Horwitz SM; 0761-009 Study Group
Haematologica 2019 May;104(5):993-1003. Epub 2018 Dec 20 doi: 10.3324/haematol.2018.205096. PMID: 30573506Free PMC Article
Ishitsuka K, Yurimoto S, Kawamura K, Tsuji Y, Iwabuchi M, Takahashi T, Tobinai K
Int J Hematol 2017 Oct;106(4):522-532. Epub 2017 Jun 9 doi: 10.1007/s12185-017-2270-9. PMID: 28597329

Diagnosis

Nosaka K, Crawford B, Yi J, Kuan W, Matsumoto T, Takahashi T
Eur J Haematol 2022 Mar;108(3):212-222. Epub 2021 Dec 8 doi: 10.1111/ejh.13728. PMID: 34862665Free PMC Article
Tobinai K, Uike N, Saburi Y, Chou T, Etoh T, Masuda M, Kawano F, Matsuoka M, Taguchi H, Makino T, Asano Y, Tamura K, Ohashi Y; Cladribine/ATL Study Group, Japan
Int J Hematol 2003 Jun;77(5):512-7. doi: 10.1007/BF02986621. PMID: 12841391

Therapy

Izutsu K, Makita S, Nosaka K, Yoshimitsu M, Utsunomiya A, Kusumoto S, Morishima S, Tsukasaki K, Kawamata T, Ono T, Rai S, Katsuya H, Ishikawa J, Yamada H, Kato K, Tachibana M, Kakurai Y, Adachi N, Tobinai K, Yonekura K, Ishitsuka K
Blood 2023 Mar 9;141(10):1159-1168. doi: 10.1182/blood.2022016862. PMID: 36150143Free PMC Article
Utsunomiya A, Izutsu K, Jo T, Yoshida S, Tsukasaki K, Ando K, Choi I, Imaizumi Y, Kato K, Kurosawa M, Kusumoto S, Miyagi T, Ohtsuka E, Sasaki O, Shibayama H, Shimoda K, Takamatsu Y, Takano K, Yonekura K, Makita S, Taguchi J, Gillings M, Onogi H, Tobinai K
Cancer Sci 2022 Aug;113(8):2778-2787. Epub 2022 Jun 7 doi: 10.1111/cas.15431. PMID: 35579212Free PMC Article
Ishitsuka K, Yurimoto S, Tsuji Y, Iwabuchi M, Takahashi T, Tobinai K
Eur J Haematol 2019 May;102(5):407-415. Epub 2019 Mar 12 doi: 10.1111/ejh.13220. PMID: 30740787Free PMC Article
Phillips AA, Fields PA, Hermine O, Ramos JC, Beltran BE, Pereira J, Wandroo F, Feldman T, Taylor GP, Sawas A, Humphrey J, Kurman M, Moriya J, Dwyer K, Leoni M, Conlon K, Cook L, Gonsky J, Horwitz SM; 0761-009 Study Group
Haematologica 2019 May;104(5):993-1003. Epub 2018 Dec 20 doi: 10.3324/haematol.2018.205096. PMID: 30573506Free PMC Article
Winsett FT, Lewis DJ, Duvic M
Expert Rev Hematol 2017 Sep;10(9):757-760. Epub 2017 Aug 21 doi: 10.1080/17474086.2017.1361819. PMID: 28756726

Prognosis

Izutsu K, Makita S, Nosaka K, Yoshimitsu M, Utsunomiya A, Kusumoto S, Morishima S, Tsukasaki K, Kawamata T, Ono T, Rai S, Katsuya H, Ishikawa J, Yamada H, Kato K, Tachibana M, Kakurai Y, Adachi N, Tobinai K, Yonekura K, Ishitsuka K
Blood 2023 Mar 9;141(10):1159-1168. doi: 10.1182/blood.2022016862. PMID: 36150143Free PMC Article
Phillips AA, Fields PA, Hermine O, Ramos JC, Beltran BE, Pereira J, Wandroo F, Feldman T, Taylor GP, Sawas A, Humphrey J, Kurman M, Moriya J, Dwyer K, Leoni M, Conlon K, Cook L, Gonsky J, Horwitz SM; 0761-009 Study Group
Haematologica 2019 May;104(5):993-1003. Epub 2018 Dec 20 doi: 10.3324/haematol.2018.205096. PMID: 30573506Free PMC Article
Winsett FT, Lewis DJ, Duvic M
Expert Rev Hematol 2017 Sep;10(9):757-760. Epub 2017 Aug 21 doi: 10.1080/17474086.2017.1361819. PMID: 28756726
Kawano N, Kuriyama T, Yoshida S, Kawano S, Yamano Y, Marutsuka K, Minato S, Yamashita K, Ochiai H, Shimoda K, Ishikawa F, Kikuchi I
J Clin Exp Hematop 2017;56(3):135-144. doi: 10.3960/jslrt.56.135. PMID: 28331127Free PMC Article
Hermine O, Dombret H, Poupon J, Arnulf B, Lefrère F, Rousselot P, Damaj G, Delarue R, Fermand JP, Brouet JC, Degos L, Varet B, de Thé H, Bazarbachi A
Hematol J 2004;5(2):130-4. doi: 10.1038/sj.thj.6200374. PMID: 15048063

Clinical prediction guides

Ishitsuka K, Yurimoto S, Tsuji Y, Iwabuchi M, Takahashi T, Tobinai K
Eur J Haematol 2019 May;102(5):407-415. Epub 2019 Mar 12 doi: 10.1111/ejh.13220. PMID: 30740787Free PMC Article
Phillips AA, Fields PA, Hermine O, Ramos JC, Beltran BE, Pereira J, Wandroo F, Feldman T, Taylor GP, Sawas A, Humphrey J, Kurman M, Moriya J, Dwyer K, Leoni M, Conlon K, Cook L, Gonsky J, Horwitz SM; 0761-009 Study Group
Haematologica 2019 May;104(5):993-1003. Epub 2018 Dec 20 doi: 10.3324/haematol.2018.205096. PMID: 30573506Free PMC Article
Winsett FT, Lewis DJ, Duvic M
Expert Rev Hematol 2017 Sep;10(9):757-760. Epub 2017 Aug 21 doi: 10.1080/17474086.2017.1361819. PMID: 28756726

Recent systematic reviews

Nosaka K, Crawford B, Yi J, Kuan W, Matsumoto T, Takahashi T
Eur J Haematol 2022 Mar;108(3):212-222. Epub 2021 Dec 8 doi: 10.1111/ejh.13728. PMID: 34862665Free PMC Article

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