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Pyoderma gangrenosum-acne-suppurative hidradenitis syndrome

MedGen UID:
1681766
•Concept ID:
C5191642
•
Disease or Syndrome
Synonyms: PASH (pyoderma gangrenosum, acne, suppurative hidradenitis) syndrome; PASH syndrome; pash syndrome; Pyoderma gangrenosum, acne, suppurative hidradenitis syndrome; pyoderma gangrenosum-acne-suppurative hidradenitis syndrome
SNOMED CT: PASH syndrome (785724007); Pyoderma gangrenosum, acne, suppurative hidradenitis syndrome (785724007); PASH (pyoderma gangrenosum, acne, suppurative hidradenitis) syndrome (785724007)
Modes of inheritance:
No inheritance data available
MedGen UID:
989178
•Concept ID:
CN307043
•
Finding
Source: Orphanet
No information is available in the scientific literature on heredity of the clinical entity.
See: This record
No inheritance data available (Orphanet)
 
Monarch Initiative: MONDO:0017332
Orphanet: ORPHA289478

Definition

A rare skin disease belonging to the spectrum of autoinflammatory syndromes with the triad of pyoderma gangrenosum (PG), suppurative hidradenitis (SH) and acne. [from SNOMEDCT_US]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVPyoderma gangrenosum-acne-suppurative hidradenitis syndrome

Recent clinical studies

Diagnosis

Phenotypes and Pathophysiology of Syndromic Hidradenitis Suppurativa: Different Faces of the Same Disease? A Systematic Review.
Nikolakis G, Kaleta KP, Vaiopoulos AG, Wolter K, Baroud S, Wojas-Pelc A, Zouboulis CC
Dermatology 2021;237(5):673-697. Epub 2020 Sep 17 doi: 10.1159/000509873. PMID: 32942279

Recent systematic reviews

Phenotypes and Pathophysiology of Syndromic Hidradenitis Suppurativa: Different Faces of the Same Disease? A Systematic Review.
Nikolakis G, Kaleta KP, Vaiopoulos AG, Wolter K, Baroud S, Wojas-Pelc A, Zouboulis CC
Dermatology 2021;237(5):673-697. Epub 2020 Sep 17 doi: 10.1159/000509873. PMID: 32942279

Supplemental Content

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    Clinical resources

    Reviews

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