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Myelodysplastic Syndrome, Unclassifiable, with Single Lineage Dysplasia

MedGen UID:
1719622
Concept ID:
C5239595
Neoplastic Process

Definition

Myelodysplastic syndrome, unclassifiable characterized by unilineage dysplasia and associated pancytopenia. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVMyelodysplastic Syndrome, Unclassifiable, with Single Lineage Dysplasia

Recent clinical studies

Etiology

AlMozain N, Mashi A, Alneami Q, Al-Omran A, Bakshi N, Owaidah T, Khalil S, Khogeer H, Hashmi S, Al-Sweedan S, Morris T, AlNounou R
Hematol Oncol Stem Cell Ther 2022 Jun 1;15(2):39-44. doi: 10.1016/j.hemonc.2020.11.001. PMID: 33227261
Takeuchi A, Imataki O, Kubo H, Kondo A, Seo K, Uemura M, Yamaoka G, Murao K, Takeuchi A
Acta Haematol 2020;143(2):140-145. Epub 2019 Jul 22 doi: 10.1159/000501147. PMID: 31330512
Grignano E, Jachiet V, Fenaux P, Ades L, Fain O, Mekinian A
Ann Hematol 2018 Nov;97(11):2015-2023. Epub 2018 Aug 8 doi: 10.1007/s00277-018-3472-9. PMID: 30091023
Geyer JT, Tam W, Liu YC, Chen Z, Wang SA, Bueso-Ramos C, Oak J, Arber DA, Hsi E, Rogers HJ, Levinson K, Bagg A, Hassane DC, Hasserjian RP, Orazi A
Mod Pathol 2017 Sep;30(9):1213-1222. Epub 2017 May 26 doi: 10.1038/modpathol.2017.45. PMID: 28548124

Diagnosis

AlMozain N, Mashi A, Alneami Q, Al-Omran A, Bakshi N, Owaidah T, Khalil S, Khogeer H, Hashmi S, Al-Sweedan S, Morris T, AlNounou R
Hematol Oncol Stem Cell Ther 2022 Jun 1;15(2):39-44. doi: 10.1016/j.hemonc.2020.11.001. PMID: 33227261
Takeuchi A, Imataki O, Kubo H, Kondo A, Seo K, Uemura M, Yamaoka G, Murao K, Takeuchi A
Acta Haematol 2020;143(2):140-145. Epub 2019 Jul 22 doi: 10.1159/000501147. PMID: 31330512
Geyer JT, Tam W, Liu YC, Chen Z, Wang SA, Bueso-Ramos C, Oak J, Arber DA, Hsi E, Rogers HJ, Levinson K, Bagg A, Hassane DC, Hasserjian RP, Orazi A
Mod Pathol 2017 Sep;30(9):1213-1222. Epub 2017 May 26 doi: 10.1038/modpathol.2017.45. PMID: 28548124
Font P, Loscertales J, Benavente C, Bermejo A, Callejas M, Garcia-Alonso L, Garcia-Marcilla A, Gil S, Lopez-Rubio M, Martin E, Muñoz C, Ricard P, Soto C, Balsalobre P, Villegas A
Ann Hematol 2013 Jan;92(1):19-24. Epub 2012 Sep 5 doi: 10.1007/s00277-012-1565-4. PMID: 22948274

Prognosis

AlMozain N, Mashi A, Alneami Q, Al-Omran A, Bakshi N, Owaidah T, Khalil S, Khogeer H, Hashmi S, Al-Sweedan S, Morris T, AlNounou R
Hematol Oncol Stem Cell Ther 2022 Jun 1;15(2):39-44. doi: 10.1016/j.hemonc.2020.11.001. PMID: 33227261
Grignano E, Jachiet V, Fenaux P, Ades L, Fain O, Mekinian A
Ann Hematol 2018 Nov;97(11):2015-2023. Epub 2018 Aug 8 doi: 10.1007/s00277-018-3472-9. PMID: 30091023
Geyer JT, Tam W, Liu YC, Chen Z, Wang SA, Bueso-Ramos C, Oak J, Arber DA, Hsi E, Rogers HJ, Levinson K, Bagg A, Hassane DC, Hasserjian RP, Orazi A
Mod Pathol 2017 Sep;30(9):1213-1222. Epub 2017 May 26 doi: 10.1038/modpathol.2017.45. PMID: 28548124
Font P, Loscertales J, Benavente C, Bermejo A, Callejas M, Garcia-Alonso L, Garcia-Marcilla A, Gil S, Lopez-Rubio M, Martin E, Muñoz C, Ricard P, Soto C, Balsalobre P, Villegas A
Ann Hematol 2013 Jan;92(1):19-24. Epub 2012 Sep 5 doi: 10.1007/s00277-012-1565-4. PMID: 22948274

Clinical prediction guides

AlMozain N, Mashi A, Alneami Q, Al-Omran A, Bakshi N, Owaidah T, Khalil S, Khogeer H, Hashmi S, Al-Sweedan S, Morris T, AlNounou R
Hematol Oncol Stem Cell Ther 2022 Jun 1;15(2):39-44. doi: 10.1016/j.hemonc.2020.11.001. PMID: 33227261
Geyer JT, Tam W, Liu YC, Chen Z, Wang SA, Bueso-Ramos C, Oak J, Arber DA, Hsi E, Rogers HJ, Levinson K, Bagg A, Hassane DC, Hasserjian RP, Orazi A
Mod Pathol 2017 Sep;30(9):1213-1222. Epub 2017 May 26 doi: 10.1038/modpathol.2017.45. PMID: 28548124
Font P, Loscertales J, Benavente C, Bermejo A, Callejas M, Garcia-Alonso L, Garcia-Marcilla A, Gil S, Lopez-Rubio M, Martin E, Muñoz C, Ricard P, Soto C, Balsalobre P, Villegas A
Ann Hematol 2013 Jan;92(1):19-24. Epub 2012 Sep 5 doi: 10.1007/s00277-012-1565-4. PMID: 22948274

Supplemental Content

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