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Unresectable Rhabdoid Tumor

MedGen UID:
1749124
•Concept ID:
C5418826
•
Neoplastic Process

Definition

A rhabdoid tumor that is not amenable to surgical resection. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVUnresectable Rhabdoid Tumor

Recent clinical studies

Etiology

Diagnosis of thoracic SMARCA4-deficient undifferentiated tumor in cytology.
Kezlarian B, Montecalvo J, Bodd FM, Chang JC, Riedel E, White C, Rekhtman N, Sauter JL
Cancer Cytopathol 2023 Aug;131(8):526-534. Epub 2023 Jun 6 doi: 10.1002/cncy.22709. PMID: 37278102Free PMC Article
Neck Rhabdoid Tumors: Clinical Features and Consideration of Autologous Stem Cell Transplant.
Wolfe AD, Capitini CM, Salamat SM, DeSantes K, Bradley KA, Kennedy T, Dehner LP, Patel NJ
J Pediatr Hematol Oncol 2018 Jan;40(1):e50-e54. doi: 10.1097/MPH.0000000000000829. PMID: 28375943Free PMC Article
High dose alkylator therapy for extracranial malignant rhabdoid tumors in children.
Venkatramani R, Shoureshi P, Malvar J, Zhou S, Mascarenhas L
Pediatr Blood Cancer 2014 Aug;61(8):1357-61. Epub 2014 Apr 30 doi: 10.1002/pbc.25093. PMID: 24789740
Primary malignant liver tumors in children.
Agarwala S
Indian J Pediatr 2012 Jun;79(6):793-800. Epub 2012 Mar 1 doi: 10.1007/s12098-012-0704-1. PMID: 22382512
Small cell undifferentiated variant of hepatoblastoma: adverse clinical and molecular features similar to rhabdoid tumors.
Trobaugh-Lotrario AD, Tomlinson GE, Finegold MJ, Gore L, Feusner JH
Pediatr Blood Cancer 2009 Mar;52(3):328-34. doi: 10.1002/pbc.21834. PMID: 18985717Free PMC Article

Diagnosis

Diagnosis of thoracic SMARCA4-deficient undifferentiated tumor in cytology.
Kezlarian B, Montecalvo J, Bodd FM, Chang JC, Riedel E, White C, Rekhtman N, Sauter JL
Cancer Cytopathol 2023 Aug;131(8):526-534. Epub 2023 Jun 6 doi: 10.1002/cncy.22709. PMID: 37278102Free PMC Article
High dose alkylator therapy for extracranial malignant rhabdoid tumors in children.
Venkatramani R, Shoureshi P, Malvar J, Zhou S, Mascarenhas L
Pediatr Blood Cancer 2014 Aug;61(8):1357-61. Epub 2014 Apr 30 doi: 10.1002/pbc.25093. PMID: 24789740
Primary malignant liver tumors in children.
Agarwala S
Indian J Pediatr 2012 Jun;79(6):793-800. Epub 2012 Mar 1 doi: 10.1007/s12098-012-0704-1. PMID: 22382512
Treatment of unresectable malignant rhabdoid tumor of the orbit with tandem high-dose chemotherapy and gamma-knife radiosurgery.
Watanabe H, Watanabe T, Kaneko M, Suzuya H, Onishi T, Okamoto Y, Miyake H, Yasuo K, Hirose T, Kagami S
Pediatr Blood Cancer 2006 Nov;47(6):846-50. doi: 10.1002/pbc.20699. PMID: 16534791

Therapy

Neck Rhabdoid Tumors: Clinical Features and Consideration of Autologous Stem Cell Transplant.
Wolfe AD, Capitini CM, Salamat SM, DeSantes K, Bradley KA, Kennedy T, Dehner LP, Patel NJ
J Pediatr Hematol Oncol 2018 Jan;40(1):e50-e54. doi: 10.1097/MPH.0000000000000829. PMID: 28375943Free PMC Article
High dose alkylator therapy for extracranial malignant rhabdoid tumors in children.
Venkatramani R, Shoureshi P, Malvar J, Zhou S, Mascarenhas L
Pediatr Blood Cancer 2014 Aug;61(8):1357-61. Epub 2014 Apr 30 doi: 10.1002/pbc.25093. PMID: 24789740
Small cell undifferentiated variant of hepatoblastoma: adverse clinical and molecular features similar to rhabdoid tumors.
Trobaugh-Lotrario AD, Tomlinson GE, Finegold MJ, Gore L, Feusner JH
Pediatr Blood Cancer 2009 Mar;52(3):328-34. doi: 10.1002/pbc.21834. PMID: 18985717Free PMC Article
Successful management of rhabdoid tumor of the liver.
Jayaram A, Finegold MJ, Parham DM, Jasty R
J Pediatr Hematol Oncol 2007 Jun;29(6):406-8. doi: 10.1097/MPH.0b013e3180601011. PMID: 17551403
Treatment of unresectable malignant rhabdoid tumor of the orbit with tandem high-dose chemotherapy and gamma-knife radiosurgery.
Watanabe H, Watanabe T, Kaneko M, Suzuya H, Onishi T, Okamoto Y, Miyake H, Yasuo K, Hirose T, Kagami S
Pediatr Blood Cancer 2006 Nov;47(6):846-50. doi: 10.1002/pbc.20699. PMID: 16534791

Prognosis

Neck Rhabdoid Tumors: Clinical Features and Consideration of Autologous Stem Cell Transplant.
Wolfe AD, Capitini CM, Salamat SM, DeSantes K, Bradley KA, Kennedy T, Dehner LP, Patel NJ
J Pediatr Hematol Oncol 2018 Jan;40(1):e50-e54. doi: 10.1097/MPH.0000000000000829. PMID: 28375943Free PMC Article
High dose alkylator therapy for extracranial malignant rhabdoid tumors in children.
Venkatramani R, Shoureshi P, Malvar J, Zhou S, Mascarenhas L
Pediatr Blood Cancer 2014 Aug;61(8):1357-61. Epub 2014 Apr 30 doi: 10.1002/pbc.25093. PMID: 24789740
Primary malignant liver tumors in children.
Agarwala S
Indian J Pediatr 2012 Jun;79(6):793-800. Epub 2012 Mar 1 doi: 10.1007/s12098-012-0704-1. PMID: 22382512
Small cell undifferentiated variant of hepatoblastoma: adverse clinical and molecular features similar to rhabdoid tumors.
Trobaugh-Lotrario AD, Tomlinson GE, Finegold MJ, Gore L, Feusner JH
Pediatr Blood Cancer 2009 Mar;52(3):328-34. doi: 10.1002/pbc.21834. PMID: 18985717Free PMC Article
Treatment of unresectable malignant rhabdoid tumor of the orbit with tandem high-dose chemotherapy and gamma-knife radiosurgery.
Watanabe H, Watanabe T, Kaneko M, Suzuya H, Onishi T, Okamoto Y, Miyake H, Yasuo K, Hirose T, Kagami S
Pediatr Blood Cancer 2006 Nov;47(6):846-50. doi: 10.1002/pbc.20699. PMID: 16534791

Clinical prediction guides

Small cell undifferentiated variant of hepatoblastoma: adverse clinical and molecular features similar to rhabdoid tumors.
Trobaugh-Lotrario AD, Tomlinson GE, Finegold MJ, Gore L, Feusner JH
Pediatr Blood Cancer 2009 Mar;52(3):328-34. doi: 10.1002/pbc.21834. PMID: 18985717Free PMC Article
Treatment of unresectable malignant rhabdoid tumor of the orbit with tandem high-dose chemotherapy and gamma-knife radiosurgery.
Watanabe H, Watanabe T, Kaneko M, Suzuya H, Onishi T, Okamoto Y, Miyake H, Yasuo K, Hirose T, Kagami S
Pediatr Blood Cancer 2006 Nov;47(6):846-50. doi: 10.1002/pbc.20699. PMID: 16534791

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