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Decreased RV/TLC ratio

MedGen UID:
1785836
Concept ID:
C5539804
Finding
HPO: HP:0033773

Definition

An abnormally low ratio of residual volume (RV) to total lung capacity (TLC) on pulmonary function testing. RV is the amount of air remaining after maximal expiration and TLC is the total amount of air in the lungs at full inspiration. These volumes cannot be determined by spirometry, but can be measured by inert gas dilution, nitrogen washout, and body plethysmography. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVDecreased RV/TLC ratio

Recent clinical studies

Etiology

Maniscalco M, Candia C, Calabrese C, D'Amato M, Matera MG, Molino A, Cazzola M
Respir Med 2024 Apr-May;225:107578. Epub 2024 Mar 1 doi: 10.1016/j.rmed.2024.107578. PMID: 38431058
Radicioni G, Ceppe A, Ford AA, Alexis NE, Barr RG, Bleecker ER, Christenson SA, Cooper CB, Han MK, Hansel NN, Hastie AT, Hoffman EA, Kanner RE, Martinez FJ, Ozkan E, Paine R 3rd, Woodruff PG, O'Neal WK, Boucher RC, Kesimer M
Lancet Respir Med 2021 Nov;9(11):1241-1254. Epub 2021 May 28 doi: 10.1016/S2213-2600(21)00079-5. PMID: 34058148Free PMC Article
Yang J, Kingsford RA, Horwood J, Epton MJ, Swanney MP, Stanton J, Darlow BA
Pediatrics 2020 Feb;145(2) Epub 2020 Jan 3 doi: 10.1542/peds.2019-2359. PMID: 31900317
Ishii H, Watanabe K, Kushima H, Baba T, Watanabe S, Yamada Y, Arai T, Tsushima K, Kondoh Y, Nakamura Y, Terasaki Y, Hebisawa A, Johkoh T, Sakai F, Takemura T, Kawabata Y, Ogura T; Tokyo Diffuse Lung Disease Study Group
Respir Med 2018 Aug;141:190-197. Epub 2018 Jun 27 doi: 10.1016/j.rmed.2018.06.022. PMID: 30053966
Sørensen JK, Buchvald F, Berg AK, Robinson PD, Nielsen KG
Respir Med 2018 Jul;140:94-100. Epub 2018 Jun 6 doi: 10.1016/j.rmed.2018.06.006. PMID: 29957288

Diagnosis

Radicioni G, Ceppe A, Ford AA, Alexis NE, Barr RG, Bleecker ER, Christenson SA, Cooper CB, Han MK, Hansel NN, Hastie AT, Hoffman EA, Kanner RE, Martinez FJ, Ozkan E, Paine R 3rd, Woodruff PG, O'Neal WK, Boucher RC, Kesimer M
Lancet Respir Med 2021 Nov;9(11):1241-1254. Epub 2021 May 28 doi: 10.1016/S2213-2600(21)00079-5. PMID: 34058148Free PMC Article
Calmes D, Huynen P, Paulus V, Henket M, Guissard F, Moermans C, Louis R, Schleich F
Respir Res 2021 Feb 26;22(1):72. doi: 10.1186/s12931-021-01635-w. PMID: 33637072Free PMC Article
Nilsson AM, Aaltonen HL, Olsson P, Persson HL, Hesselstrand R, Theander E, Wollmer P, Mandl T
J Rheumatol 2021 Feb;48(2):232-240. Epub 2020 Jun 15 doi: 10.3899/jrheum.200247. PMID: 32541077
Ishii H, Watanabe K, Kushima H, Baba T, Watanabe S, Yamada Y, Arai T, Tsushima K, Kondoh Y, Nakamura Y, Terasaki Y, Hebisawa A, Johkoh T, Sakai F, Takemura T, Kawabata Y, Ogura T; Tokyo Diffuse Lung Disease Study Group
Respir Med 2018 Aug;141:190-197. Epub 2018 Jun 27 doi: 10.1016/j.rmed.2018.06.022. PMID: 30053966
Paganin F, Mangiapan G, Proust A, Prudhomme A, Attia J, Marchand-Adam S, Pellet F, Milhe F, Melloni B, Bernady A, Raspaud C, Nocent C, Berger P, Guilleminault L
Allergy 2017 Dec;72(12):1953-1961. Epub 2017 Jun 14 doi: 10.1111/all.13202. PMID: 28517027

Therapy

Maniscalco M, Candia C, Calabrese C, D'Amato M, Matera MG, Molino A, Cazzola M
Respir Med 2024 Apr-May;225:107578. Epub 2024 Mar 1 doi: 10.1016/j.rmed.2024.107578. PMID: 38431058
Lim JU, Park S, Yoon JH, Lee SE, Cho BS, Kim YJ, Lee S, Kim HJ, Rhee CK
Respir Med 2023 Nov;218:107410. Epub 2023 Sep 9 doi: 10.1016/j.rmed.2023.107410. PMID: 37696312
Sørensen JK, Buchvald F, Berg AK, Robinson PD, Nielsen KG
Respir Med 2018 Jul;140:94-100. Epub 2018 Jun 6 doi: 10.1016/j.rmed.2018.06.006. PMID: 29957288
Paganin F, Mangiapan G, Proust A, Prudhomme A, Attia J, Marchand-Adam S, Pellet F, Milhe F, Melloni B, Bernady A, Raspaud C, Nocent C, Berger P, Guilleminault L
Allergy 2017 Dec;72(12):1953-1961. Epub 2017 Jun 14 doi: 10.1111/all.13202. PMID: 28517027
Come CE, Divo MJ, San José Estépar R, Sciurba FC, Criner GJ, Marchetti N, Scharf SM, Mosenifar Z, Make BJ, Keller CA, Minai OA, Martinez FJ, Han MK, Reilly JJ, Celli BR, Washko GR; NETT Research Group
Respir Med 2012 Jan;106(1):109-19. Epub 2011 Aug 16 doi: 10.1016/j.rmed.2011.07.012. PMID: 21843930Free PMC Article

Prognosis

Shimada A, Kawata N, Sato H, Ikari J, Suzuki E, Anazawa R, Suzuki M, Masuda Y, Haneishi H, Tatsumi K
Acad Radiol 2022 Feb;29 Suppl 2:S215-S225. Epub 2021 Jun 16 doi: 10.1016/j.acra.2021.03.034. PMID: 34144888
Radicioni G, Ceppe A, Ford AA, Alexis NE, Barr RG, Bleecker ER, Christenson SA, Cooper CB, Han MK, Hansel NN, Hastie AT, Hoffman EA, Kanner RE, Martinez FJ, Ozkan E, Paine R 3rd, Woodruff PG, O'Neal WK, Boucher RC, Kesimer M
Lancet Respir Med 2021 Nov;9(11):1241-1254. Epub 2021 May 28 doi: 10.1016/S2213-2600(21)00079-5. PMID: 34058148Free PMC Article
Nilsson AM, Aaltonen HL, Olsson P, Persson HL, Hesselstrand R, Theander E, Wollmer P, Mandl T
J Rheumatol 2021 Feb;48(2):232-240. Epub 2020 Jun 15 doi: 10.3899/jrheum.200247. PMID: 32541077
Ishii H, Watanabe K, Kushima H, Baba T, Watanabe S, Yamada Y, Arai T, Tsushima K, Kondoh Y, Nakamura Y, Terasaki Y, Hebisawa A, Johkoh T, Sakai F, Takemura T, Kawabata Y, Ogura T; Tokyo Diffuse Lung Disease Study Group
Respir Med 2018 Aug;141:190-197. Epub 2018 Jun 27 doi: 10.1016/j.rmed.2018.06.022. PMID: 30053966
Sørensen JK, Buchvald F, Berg AK, Robinson PD, Nielsen KG
Respir Med 2018 Jul;140:94-100. Epub 2018 Jun 6 doi: 10.1016/j.rmed.2018.06.006. PMID: 29957288

Clinical prediction guides

Maniscalco M, Candia C, Calabrese C, D'Amato M, Matera MG, Molino A, Cazzola M
Respir Med 2024 Apr-May;225:107578. Epub 2024 Mar 1 doi: 10.1016/j.rmed.2024.107578. PMID: 38431058
Radicioni G, Ceppe A, Ford AA, Alexis NE, Barr RG, Bleecker ER, Christenson SA, Cooper CB, Han MK, Hansel NN, Hastie AT, Hoffman EA, Kanner RE, Martinez FJ, Ozkan E, Paine R 3rd, Woodruff PG, O'Neal WK, Boucher RC, Kesimer M
Lancet Respir Med 2021 Nov;9(11):1241-1254. Epub 2021 May 28 doi: 10.1016/S2213-2600(21)00079-5. PMID: 34058148Free PMC Article
Nilsson AM, Aaltonen HL, Olsson P, Persson HL, Hesselstrand R, Theander E, Wollmer P, Mandl T
J Rheumatol 2021 Feb;48(2):232-240. Epub 2020 Jun 15 doi: 10.3899/jrheum.200247. PMID: 32541077
Ishii H, Watanabe K, Kushima H, Baba T, Watanabe S, Yamada Y, Arai T, Tsushima K, Kondoh Y, Nakamura Y, Terasaki Y, Hebisawa A, Johkoh T, Sakai F, Takemura T, Kawabata Y, Ogura T; Tokyo Diffuse Lung Disease Study Group
Respir Med 2018 Aug;141:190-197. Epub 2018 Jun 27 doi: 10.1016/j.rmed.2018.06.022. PMID: 30053966
Sørensen JK, Buchvald F, Berg AK, Robinson PD, Nielsen KG
Respir Med 2018 Jul;140:94-100. Epub 2018 Jun 6 doi: 10.1016/j.rmed.2018.06.006. PMID: 29957288

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