U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Pulmonary vasculitis

MedGen UID:
1826226
•Concept ID:
C0234962
•
Disease or Syndrome
Synonym: Lung biopsy: vasculitis
 
HPO: HP:0034705

Definition

Cellular inflammation, vessel destruction, and tissue necrosis of the blood vessels of the lung. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVPulmonary vasculitis

Professional guidelines

PubMed

Rheumatoid arthritis-interstitial lung disease: manifestations and current concepts in pathogenesis and management.
Kadura S, Raghu G
Eur Respir Rev 2021 Jun 30;30(160) Epub 2021 Jun 23 doi: 10.1183/16000617.0011-2021. PMID: 34168062Free PMC Article
Pulmonary vasculitis: diagnosis and treatment.
Anaev EK, Baranova IA, Belevsky AS
Ter Arkh 2018 Apr 19;90(3):99-106. doi: 10.26442/terarkh201890399-106. PMID: 30701864
Treatment of Pulmonary Vasculitis.
Terrier B, Guillevin L
Semin Respir Crit Care Med 2018 Aug;39(4):504-510. Epub 2018 Nov 7 doi: 10.1055/s-0038-1669414. PMID: 30404117

Recent clinical studies

Etiology

Pulmonary endarterectomy in patients with occlusive isolated pulmonary vasculitis.
Ma J, Song W, Xu H, Zhong Z, Huyan Y, Liu S
Eur J Med Res 2023 Aug 7;28(1):269. doi: 10.1186/s40001-023-01239-8. PMID: 37550701Free PMC Article
Pulmonary vasculitis: diagnosis and treatment.
Anaev EK, Baranova IA, Belevsky AS
Ter Arkh 2018 Apr 19;90(3):99-106. doi: 10.26442/terarkh201890399-106. PMID: 30701864
Diagnosis and management of pulmonary vasculitis.
Yunt ZX, Frankel SK, Brown KK
Ther Adv Respir Dis 2012 Dec;6(6):375-90. Epub 2012 Aug 9 doi: 10.1177/1753465812454693. PMID: 22878624
The pulmonary vasculitides.
Frankel SK, Schwarz MI
Am J Respir Crit Care Med 2012 Aug 1;186(3):216-24. Epub 2012 Jun 7 doi: 10.1164/rccm.201203-0539CI. PMID: 22679011
Pulmonary vasculitis: clinical presentation, differential diagnosis, and management.
Ramsey J, Amari M, Kantrow SP
Curr Rheumatol Rep 2010 Dec;12(6):420-8. doi: 10.1007/s11926-010-0136-8. PMID: 20882372

Diagnosis

Lupus Vasculitis.
Butt NI, Ashfaq F, Mahmood K, Aftab S, Anwar A, Saeed M
J Ayub Med Coll Abbottabad 2023 Jul-Sep;35(3):475-478. doi: 10.55519/JAMC-03-10849. PMID: 38404096
Rheumatoid arthritis-interstitial lung disease: manifestations and current concepts in pathogenesis and management.
Kadura S, Raghu G
Eur Respir Rev 2021 Jun 30;30(160) Epub 2021 Jun 23 doi: 10.1183/16000617.0011-2021. PMID: 34168062Free PMC Article
Pulmonary vasculitis: diagnosis and treatment.
Anaev EK, Baranova IA, Belevsky AS
Ter Arkh 2018 Apr 19;90(3):99-106. doi: 10.26442/terarkh201890399-106. PMID: 30701864
Lymphoproliferative Disorders of the Lung.
Borie R, Wislez M, Antoine M, Cadranel J
Respiration 2017;94(2):157-175. Epub 2017 Jun 14 doi: 10.1159/000477740. PMID: 28609772
Pulmonary vasculitis.
Lally L, Spiera RF
Rheum Dis Clin North Am 2015 May;41(2):315-31. Epub 2015 Feb 27 doi: 10.1016/j.rdc.2015.01.004. PMID: 25836645

Therapy

Rheumatoid lung nodules with "feeding-vessel" sign.
Sharma A, Kasetty A, Kumar A
Clin Rheumatol 2021 Apr;40(4):1645-1647. Epub 2020 Aug 22 doi: 10.1007/s10067-020-05351-6. PMID: 32827281
Treatment of Pulmonary Vasculitis.
Terrier B, Guillevin L
Semin Respir Crit Care Med 2018 Aug;39(4):504-510. Epub 2018 Nov 7 doi: 10.1055/s-0038-1669414. PMID: 30404117
Pulmonary Vasculitis and Alveolar Hemorrhage.
Guillevin L
Semin Respir Crit Care Med 2018 Aug;39(4):411-412. Epub 2018 Nov 7 doi: 10.1055/s-0038-1673370. PMID: 30404108
Pulmonary affectation of vasculitis.
Martín-Suñé N, Ríos-Blanco JJ
Arch Bronconeumol 2012 Nov;48(11):410-8. Epub 2012 Jun 6 doi: 10.1016/j.arbres.2012.04.007. PMID: 22682604
Pulmonary vasculitis.
Leavitt RY, Fauci AS
Am Rev Respir Dis 1986 Jul;134(1):149-66. doi: 10.1164/arrd.1986.134.1.149. PMID: 2873770

Prognosis

Pulmonary endarterectomy in patients with occlusive isolated pulmonary vasculitis.
Ma J, Song W, Xu H, Zhong Z, Huyan Y, Liu S
Eur J Med Res 2023 Aug 7;28(1):269. doi: 10.1186/s40001-023-01239-8. PMID: 37550701Free PMC Article
Vasculitis update: pathogenesis and biomarkers.
Brogan P, Eleftheriou D
Pediatr Nephrol 2018 Feb;33(2):187-198. Epub 2017 Aug 7 doi: 10.1007/s00467-017-3597-4. PMID: 28785984Free PMC Article
Lymphoproliferative Disorders of the Lung.
Borie R, Wislez M, Antoine M, Cadranel J
Respiration 2017;94(2):157-175. Epub 2017 Jun 14 doi: 10.1159/000477740. PMID: 28609772
Pulmonary affectation of vasculitis.
Martín-Suñé N, Ríos-Blanco JJ
Arch Bronconeumol 2012 Nov;48(11):410-8. Epub 2012 Jun 6 doi: 10.1016/j.arbres.2012.04.007. PMID: 22682604
Pulmonary vasculitis.
Leavitt RY, Fauci AS
Am Rev Respir Dis 1986 Jul;134(1):149-66. doi: 10.1164/arrd.1986.134.1.149. PMID: 2873770

Clinical prediction guides

Pulmonary endarterectomy in patients with occlusive isolated pulmonary vasculitis.
Ma J, Song W, Xu H, Zhong Z, Huyan Y, Liu S
Eur J Med Res 2023 Aug 7;28(1):269. doi: 10.1186/s40001-023-01239-8. PMID: 37550701Free PMC Article
Pathogenesis of ANCA-Associated Pulmonary Vasculitis.
Alba MA, Jennette JC, Falk RJ
Semin Respir Crit Care Med 2018 Aug;39(4):413-424. Epub 2018 Nov 7 doi: 10.1055/s-0038-1673386. PMID: 30404109Free PMC Article
Vasculitis update: pathogenesis and biomarkers.
Brogan P, Eleftheriou D
Pediatr Nephrol 2018 Feb;33(2):187-198. Epub 2017 Aug 7 doi: 10.1007/s00467-017-3597-4. PMID: 28785984Free PMC Article
Pulmonary vasculitis.
Lally L, Spiera RF
Rheum Dis Clin North Am 2015 May;41(2):315-31. Epub 2015 Feb 27 doi: 10.1016/j.rdc.2015.01.004. PMID: 25836645
What to do when you suspect your patient suffers from pulmonary vasculitis?
Cohen Tervaert JW
Expert Opin Med Diagn 2013 Jan;7(1):1-4. Epub 2012 Nov 20 doi: 10.1517/17530059.2013.739604. PMID: 23530839

Recent systematic reviews

Pulmonary manifestations in VEXAS (vacuoles, E1 enzyme, X-linked, autoinflammatory, somatic) syndrome: a systematic review.
Kouranloo K, Ashley A, Zhao SS, Dey M
Rheumatol Int 2023 Jun;43(6):1023-1032. Epub 2023 Jan 8 doi: 10.1007/s00296-022-05266-2. PMID: 36617363Free PMC Article
Prognostic factors for survival in systemic lupus erythematosus associated pulmonary hypertension.
Chow SL, Chandran V, Fazelzad R, Johnson SR
Lupus 2012 Apr;21(4):353-64. Epub 2011 Nov 29 doi: 10.1177/0961203311429815. PMID: 22127457

Supplemental Content

Table of contents

    Clinical resources

    Practice guidelines

    • PubMed
      See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Consumer resources

    Reviews

    Recent activity

    Clear Turn Off Turn On

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...