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Small intestine leiomyosarcoma

MedGen UID:
183086
•Concept ID:
C0920305
•
Neoplastic Process
Synonyms: Leiomyosarcoma of Small Bowel; leiomyosarcoma of small bowel; Leiomyosarcoma of small intestine; Leiomyosarcoma of Small Intestine; leiomyosarcoma of small intestine; Leiomyosarcoma of the Small Bowel; leiomyosarcoma of the small bowel; Leiomyosarcoma of the Small Intestine; leiomyosarcoma of the small intestine; Small Bowel Leiomyosarcoma; small bowel leiomyosarcoma; Small Intestinal Leiomyosarcoma; small intestinal leiomyosarcoma; Small Intestine Leiomyosarcoma; small intestine leiomyosarcoma; smooth muscle connective tissue tumor; smooth muscle connective tissue tumour
SNOMED CT: Leiomyosarcoma of small intestine (716651004)
 
Monarch Initiative: MONDO:0003360
Orphanet: ORPHA104076

Definition

A rare type of small bowel malignancy, originating in the smooth muscle cells within the muscularis propria or the muscularis mucosa, most often found in the jejunum, and presenting with gastrointestinal bleeding and anemia and sometimes with other non-specific symptoms such as vomiting, nausea, abdominal pain and weakness and spreading to regional lymph nodes in 14% of cases. [from SNOMEDCT_US]

Professional guidelines

PubMed

Effect of Double-Balloon Enteroscopy on Diagnosis and Treatment of Small-Bowel Diseases.
Tang L, Huang LY, Cui J, Wu CR
Chin Med J (Engl) 2018 Jun 5;131(11):1321-1326. doi: 10.4103/0366-6999.232802. PMID: 29786046Free PMC Article
Gastrointestinal stromal tumors--definition, clinical, histological, immunohistochemical, and molecular genetic features and differential diagnosis.
Miettinen M, Lasota J
Virchows Arch 2001 Jan;438(1):1-12. doi: 10.1007/s004280000338. PMID: 11213830
Gastrointestinal stromal tumors: current diagnosis, biologic behavior, and management.
Pidhorecky I, Cheney RT, Kraybill WG, Gibbs JF
Ann Surg Oncol 2000 Oct;7(9):705-12. doi: 10.1007/s10434-000-0705-6. PMID: 11034250

Recent clinical studies

Diagnosis

Small intestine leiomyosarcoma mimicking gastrointestinal stromal tumour.
Fawaz M, Kataria K, Singh A, Samadder S
BMJ Case Rep 2021 Sep 13;14(9) doi: 10.1136/bcr-2021-244381. PMID: 34518183Free PMC Article
Laparoscopic resection of small bowel sarcoma.
Hamm JK, Chaudhery SI, Kim RH
Surg Laparosc Endosc Percutan Tech 2013 Jun;23(3):e138-40. doi: 10.1097/SLE.0b013e318280638e. PMID: 23752024

Prognosis

Small intestine leiomyosarcoma mimicking gastrointestinal stromal tumour.
Fawaz M, Kataria K, Singh A, Samadder S
BMJ Case Rep 2021 Sep 13;14(9) doi: 10.1136/bcr-2021-244381. PMID: 34518183Free PMC Article

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