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Abnormal extrahepatic bile duct morphology

MedGen UID:
1842019
•Concept ID:
C5826835
•
Anatomical Abnormality
HPO: HP:0035013

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVAbnormal extrahepatic bile duct morphology

Professional guidelines

PubMed

Diagnostic criteria for pancreaticobiliary maljunction 2013.
Kamisawa T, Ando H, Hamada Y, Fujii H, Koshinaga T, Urushihara N, Itoi T, Shimada H; Japanese Study Group on Pancreaticobiliary Maljunction
J Hepatobiliary Pancreat Sci 2014 Mar;21(3):159-61. Epub 2013 Dec 5 doi: 10.1002/jhbp.57. PMID: 24307541
Diagnosis and treatment of pancreaticobiliary maljunction in children.
Ono S, Fumino S, Iwai N
Surg Today 2011 May;41(5):601-5. Epub 2011 May 1 doi: 10.1007/s00595-010-4492-9. PMID: 21533929
Sphincter of Oddi dysfunction and other functional biliary disorders: evaluation and treatment.
Prajapati DN, Hogan WJ
Gastroenterol Clin North Am 2003 Jun;32(2):601-18. doi: 10.1016/s0889-8553(03)00025-6. PMID: 12858608

Recent clinical studies

Etiology

Biliary carcinogenesis in pancreaticobiliary maljunction.
Kamisawa T, Kuruma S, Chiba K, Tabata T, Koizumi S, Kikuyama M
J Gastroenterol 2017 Feb;52(2):158-163. Epub 2016 Oct 4 doi: 10.1007/s00535-016-1268-z. PMID: 27704265
Genome-wide association studies in biliary atresia.
Ningappa M, Min J, Higgs BW, Ashokkumar C, Ranganathan S, Sindhi R
Wiley Interdiscip Rev Syst Biol Med 2015 Sep-Oct;7(5):267-73. Epub 2015 May 11 doi: 10.1002/wsbm.1303. PMID: 25963027
Imaging of choledochal cysts.
Lewis VA, Adam SZ, Nikolaidis P, Wood C, Wu JG, Yaghmai V, Miller FH
Abdom Imaging 2015 Aug;40(6):1567-80. doi: 10.1007/s00261-015-0381-4. PMID: 25682292
Biliary atresia.
Chardot C
Orphanet J Rare Dis 2006 Jul 26;1:28. doi: 10.1186/1750-1172-1-28. PMID: 16872500Free PMC Article
Biliary atresia revisited.
Kahn E
Pediatr Dev Pathol 2004 Mar-Apr;7(2):109-24. Epub 2004 Mar 4 doi: 10.1007/s10024-003-0307-y. PMID: 14994122

Diagnosis

Portal biliopathy.
Khuroo MS, Rather AA, Khuroo NS, Khuroo MS
World J Gastroenterol 2016 Sep 21;22(35):7973-82. doi: 10.3748/wjg.v22.i35.7973. PMID: 27672292Free PMC Article
Pancreaticobiliary maljunction.
Kamisawa T, Takuma K, Anjiki H, Egawa N, Kurata M, Honda G, Tsuruta K, Sasaki T
Clin Gastroenterol Hepatol 2009 Nov;7(11 Suppl):S84-8. doi: 10.1016/j.cgh.2009.08.024. PMID: 19896105
Biliary atresia.
Mieli-Vergani G, Vergani D
Semin Immunopathol 2009 Sep;31(3):371-81. Epub 2009 Jun 17 doi: 10.1007/s00281-009-0171-6. PMID: 19533128
Choledochal cyst.
Gafur MA, Rahman MZ
Mymensingh Med J 2007 Jan;16(1):113-6. doi: 10.3329/mmj.v16i1.264. PMID: 17344793
Biliary atresia.
Lefkowitch JH
Mayo Clin Proc 1998 Jan;73(1):90-5. doi: 10.1016/S0025-6196(11)63625-2. PMID: 9443685

Therapy

Portal biliopathy.
Khuroo MS, Rather AA, Khuroo NS, Khuroo MS
World J Gastroenterol 2016 Sep 21;22(35):7973-82. doi: 10.3748/wjg.v22.i35.7973. PMID: 27672292Free PMC Article
Utility of fluorescent cholangiography during laparoscopic cholecystectomy: A systematic review.
Pesce A, Piccolo G, La Greca G, Puleo S
World J Gastroenterol 2015 Jul 7;21(25):7877-83. doi: 10.3748/wjg.v21.i25.7877. PMID: 26167088Free PMC Article
Graft cholangiopathy: etiology, diagnosis, and therapeutic strategies.
Luo Y, Ji WB, Duan WD, Ye S, Dong JH
Hepatobiliary Pancreat Dis Int 2014 Feb;13(1):10-7. doi: 10.1016/s1499-3872(14)60001-1. PMID: 24463074
Biliary atresia: will blocking inflammation tame the disease?
Bessho K, Bezerra JA
Annu Rev Med 2011;62:171-85. doi: 10.1146/annurev-med-042909-093734. PMID: 21226614Free PMC Article
Pancreaticobiliary maljunction.
Kamisawa T, Takuma K, Anjiki H, Egawa N, Kurata M, Honda G, Tsuruta K, Sasaki T
Clin Gastroenterol Hepatol 2009 Nov;7(11 Suppl):S84-8. doi: 10.1016/j.cgh.2009.08.024. PMID: 19896105

Prognosis

Choledochal malformations: global research, scientific advances and key controversies.
Friedmacher F, Ford KE, Davenport M
Pediatr Surg Int 2019 Mar;35(3):273-282. Epub 2018 Nov 7 doi: 10.1007/s00383-018-4392-4. PMID: 30406431
Utility of fluorescent cholangiography during laparoscopic cholecystectomy: A systematic review.
Pesce A, Piccolo G, La Greca G, Puleo S
World J Gastroenterol 2015 Jul 7;21(25):7877-83. doi: 10.3748/wjg.v21.i25.7877. PMID: 26167088Free PMC Article
Biliary atresia.
Mieli-Vergani G, Vergani D
Semin Immunopathol 2009 Sep;31(3):371-81. Epub 2009 Jun 17 doi: 10.1007/s00281-009-0171-6. PMID: 19533128
Contemporary surgery of biliary atresia.
Lilly JR, Karrer FM
Pediatr Clin North Am 1985 Oct;32(5):1233-46. doi: 10.1016/s0031-3955(16)34902-1. PMID: 3897988
Neonatal cholestasis.
Balistreri WF
J Pediatr 1985 Feb;106(2):171-84. doi: 10.1016/s0022-3476(85)80282-1. PMID: 3881579

Clinical prediction guides

Association between anatomic variations of extrahepatic and intrahepatic bile ducts: Do look up!
Renzulli M, Brandi N, Brocchi S, Balacchi C, Lanza C, Pettinari I, Stefanini B, Carrafiello G, Piscaglia F, Golfieri R, Marasco G
J Anat 2023 Apr;242(4):683-694. Epub 2023 Jan 20 doi: 10.1111/joa.13808. PMID: 36670522Free PMC Article
Choledochal cysts: Similarities and differences between Asian and Western countries.
Baison GN, Bonds MM, Helton WS, Kozarek RA
World J Gastroenterol 2019 Jul 14;25(26):3334-3343. doi: 10.3748/wjg.v25.i26.3334. PMID: 31341359Free PMC Article
"Biliary Diseases with Pancreatic Counterparts": Cross-sectional Imaging Findings.
Katabathina VS, Flaherty EM, Dasyam AK, Menias CO, Riddle ND, Lath N, Kozaka K, Matsui O, Nakanuma Y, Prasad SR
Radiographics 2016 Mar-Apr;36(2):374-92. Epub 2016 Feb 1 doi: 10.1148/rg.2016150071. PMID: 26824512
Utility of fluorescent cholangiography during laparoscopic cholecystectomy: A systematic review.
Pesce A, Piccolo G, La Greca G, Puleo S
World J Gastroenterol 2015 Jul 7;21(25):7877-83. doi: 10.3748/wjg.v21.i25.7877. PMID: 26167088Free PMC Article
Destructive intrahepatic bile duct diseases.
Desmet VJ
Recenti Prog Med 1990 Jun;81(6):392-8. PMID: 2251446

Recent systematic reviews

Defining an optimal surveillance strategy for patients following choledochal cyst resection: results of a systematic review.
Koea J, O'Grady M, Agraval J, Srinivasa S
ANZ J Surg 2022 Jun;92(6):1356-1364. Epub 2022 May 17 doi: 10.1111/ans.17775. PMID: 35579057
Left-sided gallbladder: a systematic review of a rare biliary anomaly.
Pereira R, Singh T, Avramovic J, Baker S, Eslick GD, Cox MR
ANZ J Surg 2019 Nov;89(11):1392-1397. Epub 2019 Mar 5 doi: 10.1111/ans.15041. PMID: 30836441
A systematic review of the anatomical findings of multiple gallbladders.
Darnis B, Mohkam K, Cauchy F, Cazauran JB, Bancel B, Rode A, Ducerf C, Lesurtel M, Mabrut JY
HPB (Oxford) 2018 Nov;20(11):985-991. Epub 2018 Jun 7 doi: 10.1016/j.hpb.2018.04.002. PMID: 29887260
Therapeutic approaches for portal biliopathy: A systematic review.
Franceschet I, Zanetto A, Ferrarese A, Burra P, Senzolo M
World J Gastroenterol 2016 Dec 7;22(45):9909-9920. doi: 10.3748/wjg.v22.i45.9909. PMID: 28018098Free PMC Article
Utility of fluorescent cholangiography during laparoscopic cholecystectomy: A systematic review.
Pesce A, Piccolo G, La Greca G, Puleo S
World J Gastroenterol 2015 Jul 7;21(25):7877-83. doi: 10.3748/wjg.v21.i25.7877. PMID: 26167088Free PMC Article

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