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Primary polyarteritis nodosa

MedGen UID:
1842954
•Concept ID:
C5680052
•
Disease or Syndrome
Synonyms: Primary PAN; primary PAN; Primary periarteritis nodosa; primary periarteritis nodosa; primary polyarteritis nodosa
Modes of inheritance:
Not genetically inherited
MedGen UID:
988794
•Concept ID:
CN307044
•
Finding
Source: Orphanet
clinical entity without genetic inheritance.
See: This record
Not genetically inherited (Orphanet)
 
Monarch Initiative: MONDO:0018593
Orphanet: ORPHA439737

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVPrimary polyarteritis nodosa

Professional guidelines

PubMed

Treatment Guidelines in Vasculitis.
Kermani TA, Warrington KJ, Dua AB
Rheum Dis Clin North Am 2022 Aug;48(3):705-724. Epub 2022 Jul 5 doi: 10.1016/j.rdc.2022.03.006. PMID: 35953232
Treatment of systemic necrotizing vasculitides: recent advances and important clinical considerations.
Pagnoux C, Mendel A
Expert Rev Clin Immunol 2019 Sep;15(9):939-949. Epub 2019 Aug 26 doi: 10.1080/1744666X.2019.1656527. PMID: 31414912
Therapeutic advances in the treatment of vasculitis.
Eleftheriou D, Brogan PA
Pediatr Rheumatol Online J 2016 Apr 26;14(1):26. doi: 10.1186/s12969-016-0082-8. PMID: 27112923Free PMC Article

Recent clinical studies

Etiology

Childhood rheumatic diseases: bites not only the joint, but also the heart.
Thomas KN, Aggarwal A
Clin Rheumatol 2023 Oct;42(10):2703-2715. Epub 2023 May 9 doi: 10.1007/s10067-023-06621-9. PMID: 37160484Free PMC Article
Treatment Guidelines in Vasculitis.
Kermani TA, Warrington KJ, Dua AB
Rheum Dis Clin North Am 2022 Aug;48(3):705-724. Epub 2022 Jul 5 doi: 10.1016/j.rdc.2022.03.006. PMID: 35953232
Nonatherosclerotic Abdominal Vasculopathies.
Skeik N, Hyde JR, Olson SL, Thaler CM, Abuatiyeh W, Ahmed AK, Lyon DR, Witt DR, Garberich R, Sullivan T
Ann Vasc Surg 2019 Oct;60:128-146. Epub 2019 Jun 12 doi: 10.1016/j.avsg.2019.04.004. PMID: 31200053
CNS vasculitis.
Kelley RE
Front Biosci 2004 Jan 1;9:946-55. doi: 10.2741/1259. PMID: 14766421
Vasculitis.
Watts RA, Scott DG
Baillieres Clin Rheumatol 1995 Aug;9(3):529-54. doi: 10.1016/s0950-3579(05)80257-2. PMID: 7497537

Diagnosis

Polyarteritis nodosa: an evolving primary systemic vasculitis.
Springer JM, Byram K
Postgrad Med 2023 Jan;135(sup1):61-68. Epub 2022 Jun 22 doi: 10.1080/00325481.2022.2088940. PMID: 35709399
Treatment Guidelines in Vasculitis.
Kermani TA, Warrington KJ, Dua AB
Rheum Dis Clin North Am 2022 Aug;48(3):705-724. Epub 2022 Jul 5 doi: 10.1016/j.rdc.2022.03.006. PMID: 35953232
Polyarteritis nodosa revisited: a review of historical approaches, subphenotypes and a research agenda.
Karadag O, Jayne DJ
Clin Exp Rheumatol 2018 Mar-Apr;36 Suppl 111(2):135-142. Epub 2018 Feb 20 PMID: 29465365
Headache and vasculitis.
Lopez JI, Holdridge A, Chalela J
Curr Pain Headache Rep 2013 Mar;17(3):320. doi: 10.1007/s11916-012-0320-9. PMID: 23338772
Vasculitis.
Watts RA, Scott DG
Baillieres Clin Rheumatol 1995 Aug;9(3):529-54. doi: 10.1016/s0950-3579(05)80257-2. PMID: 7497537

Therapy

Efficacy and safety of treatments in cutaneous polyarteritis nodosa: A French observational retrospective study.
Bettuzzi T, Jachiet M, Sbidian E, Frumholtz L, Cordoliani F, Mouthon L, Chasset F, Paule R, Bouaziz JD, Guillevin L, Terrier B, Aractingi S, Dupin N, Régent A
J Am Acad Dermatol 2022 May;86(5):1035-1041. Epub 2021 Jul 2 doi: 10.1016/j.jaad.2021.06.872. PMID: 34224771
Nonatherosclerotic Abdominal Vasculopathies.
Skeik N, Hyde JR, Olson SL, Thaler CM, Abuatiyeh W, Ahmed AK, Lyon DR, Witt DR, Garberich R, Sullivan T
Ann Vasc Surg 2019 Oct;60:128-146. Epub 2019 Jun 12 doi: 10.1016/j.avsg.2019.04.004. PMID: 31200053
Systemic vasculitis and the gut.
Hatemi I, Hatemi G, Çelik AF
Curr Opin Rheumatol 2017 Jan;29(1):33-38. doi: 10.1097/BOR.0000000000000344. PMID: 27684357
Therapeutic advances in the treatment of vasculitis.
Eleftheriou D, Brogan PA
Pediatr Rheumatol Online J 2016 Apr 26;14(1):26. doi: 10.1186/s12969-016-0082-8. PMID: 27112923Free PMC Article
Vasculitic neuropathies.
Burns TM, Schaublin GA, Dyck PJ
Neurol Clin 2007 Feb;25(1):89-113. doi: 10.1016/j.ncl.2006.11.002. PMID: 17324722

Prognosis

Polyarteritis nodosa: an evolving primary systemic vasculitis.
Springer JM, Byram K
Postgrad Med 2023 Jan;135(sup1):61-68. Epub 2022 Jun 22 doi: 10.1080/00325481.2022.2088940. PMID: 35709399
Clusters in Pediatric Rheumatic Diseases.
Sag E, Demir S, Ozen S
Curr Rheumatol Rep 2020 May 20;22(7):28. doi: 10.1007/s11926-020-00908-5. PMID: 32436006
Measuring Vasculitis with Numbers: Outcome Scores.
Batu ED, Ozen S
Curr Rheumatol Rev 2020;16(1):21-28. doi: 10.2174/1573397115666191126093927. PMID: 31804163
Polyarteritis nodosa revisited: a review of historical approaches, subphenotypes and a research agenda.
Karadag O, Jayne DJ
Clin Exp Rheumatol 2018 Mar-Apr;36 Suppl 111(2):135-142. Epub 2018 Feb 20 PMID: 29465365
CNS vasculitis.
Kelley RE
Front Biosci 2004 Jan 1;9:946-55. doi: 10.2741/1259. PMID: 14766421

Clinical prediction guides

New-onset autoimmune disease after COVID-19.
Hileman CO, Malakooti SK, Patil N, Singer NG, McComsey GA
Front Immunol 2024;15:1337406. Epub 2024 Feb 8 doi: 10.3389/fimmu.2024.1337406. PMID: 38390319Free PMC Article
Clusters in Pediatric Rheumatic Diseases.
Sag E, Demir S, Ozen S
Curr Rheumatol Rep 2020 May 20;22(7):28. doi: 10.1007/s11926-020-00908-5. PMID: 32436006
Measuring Vasculitis with Numbers: Outcome Scores.
Batu ED, Ozen S
Curr Rheumatol Rev 2020;16(1):21-28. doi: 10.2174/1573397115666191126093927. PMID: 31804163
Systemic vasculitis and the gut.
Hatemi I, Hatemi G, Çelik AF
Curr Opin Rheumatol 2017 Jan;29(1):33-38. doi: 10.1097/BOR.0000000000000344. PMID: 27684357
Vasculitis.
Watts RA, Scott DG
Baillieres Clin Rheumatol 1995 Aug;9(3):529-54. doi: 10.1016/s0950-3579(05)80257-2. PMID: 7497537

Recent systematic reviews

Systematic review of childhood-onset polyarteritis nodosa and DADA2.
Kasap Cuceoglu M, Sener S, Batu ED, Kaya Akca U, Demir S, Sag E, Atalay E, Balık Z, Basaran O, Bilginer Y, Ozen S
Semin Arthritis Rheum 2021 Jun;51(3):559-564. Epub 2021 Apr 19 doi: 10.1016/j.semarthrit.2021.04.009. PMID: 33901990
Haemophagocytic syndrome in rheumatic patients. A systematic review.
Atteritano M, David A, Bagnato G, Beninati C, Frisina A, Iaria C, Bagnato G, Cascio A
Eur Rev Med Pharmacol Sci 2012 Oct;16(10):1414-24. PMID: 23104659

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