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Pseudomyxoma peritonei(PMP)

MedGen UID:
18726
Concept ID:
C0033822
Neoplastic Process
Synonyms: PMP; Syndrome of pseudomyxoma peritonei
SNOMED CT: Pseudomyxoma peritonei (112679004); Pseudomyxoma peritonei (307601000)
Modes of inheritance:
Unknown inheritance
MedGen UID:
989040
Concept ID:
CN307042
Finding
Source: Orphanet
Hereditary clinical entity whose mode of inheritance is unknown.
 
Monarch Initiative: MONDO:0017048
Orphanet: ORPHA26790

Definition

Pseudomyxoma peritonei is characterized by disseminated intra-peritoneal mucinous tumors and mucinous ascites in the abdomen and pelvis. [from ORDO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVPseudomyxoma peritonei
Follow this link to review classifications for Pseudomyxoma peritonei in Orphanet.

Professional guidelines

PubMed

Govaerts K, Lurvink RJ, De Hingh IHJT, Van der Speeten K, Villeneuve L, Kusamura S, Kepenekian V, Deraco M, Glehen O, Moran BJ; PSOGI
Eur J Surg Oncol 2021 Jan;47(1):11-35. Epub 2020 Feb 28 doi: 10.1016/j.ejso.2020.02.012. PMID: 32199769
Chicago Consensus Working Group
Cancer 2020 Jun 1;126(11):2525-2533. Epub 2020 Apr 13 doi: 10.1002/cncr.32881. PMID: 32282073
Carr NJ, Bibeau F, Bradley RF, Dartigues P, Feakins RM, Geisinger KR, Gui X, Isaac S, Milione M, Misdraji J, Pai RK, Rodriguez-Justo M, Sobin LH, van Velthuysen MF, Yantiss RK
Histopathology 2017 Dec;71(6):847-858. Epub 2017 Sep 19 doi: 10.1111/his.13324. PMID: 28746986

Recent clinical studies

Etiology

Kusamura S, Barretta F, Yonemura Y, Sugarbaker PH, Moran BJ, Levine EA, Goere D, Baratti D, Nizri E, Morris DL, Glehen O, Sardi A, Barrios P, Quénet F, Villeneuve L, Gómez-Portilla A, de Hingh I, Ceelen W, Pelz JOW, Piso P, González-Moreno S, Van Der Speeten K, Deraco M; Peritoneal Surface Oncology Group International (PSOGI) and the French National Registry of Rare Peritoneal Surface Malignancies (RENAPE)
JAMA Surg 2021 Mar 1;156(3):e206363. Epub 2021 Mar 10 doi: 10.1001/jamasurg.2020.6363. PMID: 33502455Free PMC Article
Govaerts K, Lurvink RJ, De Hingh IHJT, Van der Speeten K, Villeneuve L, Kusamura S, Kepenekian V, Deraco M, Glehen O, Moran BJ; PSOGI
Eur J Surg Oncol 2021 Jan;47(1):11-35. Epub 2020 Feb 28 doi: 10.1016/j.ejso.2020.02.012. PMID: 32199769
Chicago Consensus Working Group
Cancer 2020 Jun 1;126(11):2525-2533. Epub 2020 Apr 13 doi: 10.1002/cncr.32881. PMID: 32282073
Carr NJ, Bibeau F, Bradley RF, Dartigues P, Feakins RM, Geisinger KR, Gui X, Isaac S, Milione M, Misdraji J, Pai RK, Rodriguez-Justo M, Sobin LH, van Velthuysen MF, Yantiss RK
Histopathology 2017 Dec;71(6):847-858. Epub 2017 Sep 19 doi: 10.1111/his.13324. PMID: 28746986
Carr NJ, Cecil TD, Mohamed F, Sobin LH, Sugarbaker PH, González-Moreno S, Taflampas P, Chapman S, Moran BJ; Peritoneal Surface Oncology Group International
Am J Surg Pathol 2016 Jan;40(1):14-26. doi: 10.1097/PAS.0000000000000535. PMID: 26492181

Diagnosis

Kusamura S, Barretta F, Yonemura Y, Sugarbaker PH, Moran BJ, Levine EA, Goere D, Baratti D, Nizri E, Morris DL, Glehen O, Sardi A, Barrios P, Quénet F, Villeneuve L, Gómez-Portilla A, de Hingh I, Ceelen W, Pelz JOW, Piso P, González-Moreno S, Van Der Speeten K, Deraco M; Peritoneal Surface Oncology Group International (PSOGI) and the French National Registry of Rare Peritoneal Surface Malignancies (RENAPE)
JAMA Surg 2021 Mar 1;156(3):e206363. Epub 2021 Mar 10 doi: 10.1001/jamasurg.2020.6363. PMID: 33502455Free PMC Article
Govaerts K, Lurvink RJ, De Hingh IHJT, Van der Speeten K, Villeneuve L, Kusamura S, Kepenekian V, Deraco M, Glehen O, Moran BJ; PSOGI
Eur J Surg Oncol 2021 Jan;47(1):11-35. Epub 2020 Feb 28 doi: 10.1016/j.ejso.2020.02.012. PMID: 32199769
Bartoška P, Antoš F, Vítek P, Marx J, Kopic J, Holečková P
Klin Onkol 2019 Fall;32(5):329-332. doi: 10.14735/amko2019329. PMID: 31610663
Carr NJ, Bibeau F, Bradley RF, Dartigues P, Feakins RM, Geisinger KR, Gui X, Isaac S, Milione M, Misdraji J, Pai RK, Rodriguez-Justo M, Sobin LH, van Velthuysen MF, Yantiss RK
Histopathology 2017 Dec;71(6):847-858. Epub 2017 Sep 19 doi: 10.1111/his.13324. PMID: 28746986
Carr NJ, Cecil TD, Mohamed F, Sobin LH, Sugarbaker PH, González-Moreno S, Taflampas P, Chapman S, Moran BJ; Peritoneal Surface Oncology Group International
Am J Surg Pathol 2016 Jan;40(1):14-26. doi: 10.1097/PAS.0000000000000535. PMID: 26492181

Therapy

Kusamura S, Barretta F, Yonemura Y, Sugarbaker PH, Moran BJ, Levine EA, Goere D, Baratti D, Nizri E, Morris DL, Glehen O, Sardi A, Barrios P, Quénet F, Villeneuve L, Gómez-Portilla A, de Hingh I, Ceelen W, Pelz JOW, Piso P, González-Moreno S, Van Der Speeten K, Deraco M; Peritoneal Surface Oncology Group International (PSOGI) and the French National Registry of Rare Peritoneal Surface Malignancies (RENAPE)
JAMA Surg 2021 Mar 1;156(3):e206363. Epub 2021 Mar 10 doi: 10.1001/jamasurg.2020.6363. PMID: 33502455Free PMC Article
Govaerts K, Lurvink RJ, De Hingh IHJT, Van der Speeten K, Villeneuve L, Kusamura S, Kepenekian V, Deraco M, Glehen O, Moran BJ; PSOGI
Eur J Surg Oncol 2021 Jan;47(1):11-35. Epub 2020 Feb 28 doi: 10.1016/j.ejso.2020.02.012. PMID: 32199769
Kahn AB, Tulla KA, Tzvetanov IG
Gastroenterol Clin North Am 2019 Dec;48(4):575-583. Epub 2019 Oct 4 doi: 10.1016/j.gtc.2019.08.010. PMID: 31668184
Fallis SA, Moran BJ
J BUON 2015 May;20 Suppl 1:S47-55. PMID: 26051332
Hinson FL, Ambrose NS
Br J Surg 1998 Oct;85(10):1332-9. doi: 10.1046/j.1365-2168.1998.00882.x. PMID: 9782010

Prognosis

Kusamura S, Barretta F, Yonemura Y, Sugarbaker PH, Moran BJ, Levine EA, Goere D, Baratti D, Nizri E, Morris DL, Glehen O, Sardi A, Barrios P, Quénet F, Villeneuve L, Gómez-Portilla A, de Hingh I, Ceelen W, Pelz JOW, Piso P, González-Moreno S, Van Der Speeten K, Deraco M; Peritoneal Surface Oncology Group International (PSOGI) and the French National Registry of Rare Peritoneal Surface Malignancies (RENAPE)
JAMA Surg 2021 Mar 1;156(3):e206363. Epub 2021 Mar 10 doi: 10.1001/jamasurg.2020.6363. PMID: 33502455Free PMC Article
Carr NJ, Cecil TD, Mohamed F, Sobin LH, Sugarbaker PH, González-Moreno S, Taflampas P, Chapman S, Moran BJ; Peritoneal Surface Oncology Group International
Am J Surg Pathol 2016 Jan;40(1):14-26. doi: 10.1097/PAS.0000000000000535. PMID: 26492181
Smeenk RM, Verwaal VJ, Zoetmulder FA
Cancer Treat Rev 2007 Apr;33(2):138-45. Epub 2006 Dec 19 doi: 10.1016/j.ctrv.2006.11.001. PMID: 17182192
Hinson FL, Ambrose NS
Br J Surg 1998 Oct;85(10):1332-9. doi: 10.1046/j.1365-2168.1998.00882.x. PMID: 9782010
Sugarbaker PH
Cancer Treat Res 1996;81:105-19. doi: 10.1007/978-1-4613-1245-1_10. PMID: 8834579

Clinical prediction guides

Akay E, Arslan A, Eren SK, Özhan N, Karaman H
Indian J Pathol Microbiol 2022 Jul-Sep;65(3):565-571. doi: 10.4103/ijpm.ijpm_827_21. PMID: 35900483
Hissong E, Yantiss RK
Am J Surg Pathol 2022 Jan 1;46(1):e27-e42. doi: 10.1097/PAS.0000000000001662. PMID: 33417324
Kong JC, Flood MP, Guerra GR, Liesegang A, Wong WJ, Mitchell C, Warrier SK, Naidu S, Meade B, Lutton N, Heriot AG
Colorectal Dis 2021 Sep;23(9):2368-2375. Epub 2021 Jul 12 doi: 10.1111/codi.15778. PMID: 34157209
Kusamura S, Barretta F, Yonemura Y, Sugarbaker PH, Moran BJ, Levine EA, Goere D, Baratti D, Nizri E, Morris DL, Glehen O, Sardi A, Barrios P, Quénet F, Villeneuve L, Gómez-Portilla A, de Hingh I, Ceelen W, Pelz JOW, Piso P, González-Moreno S, Van Der Speeten K, Deraco M; Peritoneal Surface Oncology Group International (PSOGI) and the French National Registry of Rare Peritoneal Surface Malignancies (RENAPE)
JAMA Surg 2021 Mar 1;156(3):e206363. Epub 2021 Mar 10 doi: 10.1001/jamasurg.2020.6363. PMID: 33502455Free PMC Article
Carr NJ, Cecil TD, Mohamed F, Sobin LH, Sugarbaker PH, González-Moreno S, Taflampas P, Chapman S, Moran BJ; Peritoneal Surface Oncology Group International
Am J Surg Pathol 2016 Jan;40(1):14-26. doi: 10.1097/PAS.0000000000000535. PMID: 26492181

Recent systematic reviews

Murage NW, Ahmed NM, Underwood TJ, Walters ZS, Breininger SP
Cancer Metastasis Rev 2023 Mar;42(1):335-359. Epub 2023 Feb 1 doi: 10.1007/s10555-023-10088-0. PMID: 36723696Free PMC Article
Floriano I, Silvinato A, Reis JC, Cafalli C, Bernardo WM
Clinics (Sao Paulo) 2022;77:100039. Epub 2022 May 13 doi: 10.1016/j.clinsp.2022.100039. PMID: 35576869Free PMC Article
McBride K, McFadden D, Osler T
J Surg Res 2013 Jul;183(1):246-52. Epub 2013 Jan 10 doi: 10.1016/j.jss.2012.12.040. PMID: 23490141
Murphy EM, Farquharson SM, Moran BJ
Br J Surg 2006 Jul;93(7):783-92. doi: 10.1002/bjs.5385. PMID: 16775823
Bryant J, Clegg AJ, Sidhu MK, Brodin H, Royle P, Davidson P
Br J Surg 2005 Feb;92(2):153-8. doi: 10.1002/bjs.4862. PMID: 15685704

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