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Pyloric stenosis

MedGen UID:
18780
Concept ID:
C0034194
Finding; Pathologic Function
Synonym: Pyloric stenosis (disease)
SNOMED CT: PS - Pyloric stenosis (367403001); Pyloric stenosis (367403001)
 
Monarch Initiative: MONDO:0001561

Definition

Narrowing of the pyloric lumen caused either by hypertrophy of the surrounding muscles or tissue scarring due to a chronic peptic ulcer. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVPyloric stenosis

Professional guidelines

PubMed

Zikic A, Schünemann H, Wi T, Lincetto O, Broutet N, Santesso N
J Pediatric Infect Dis Soc 2018 Aug 17;7(3):e107-e115. doi: 10.1093/jpids/piy060. PMID: 30007329Free PMC Article
Lauriti G, Cascini V, Chiesa PL, Pierro A, Zani A
Eur J Pediatr Surg 2018 Oct;28(5):393-399. Epub 2017 Jul 12 doi: 10.1055/s-0037-1604116. PMID: 28701002
Jobson M, Hall NJ
Semin Pediatr Surg 2016 Aug;25(4):219-24. Epub 2016 May 10 doi: 10.1053/j.sempedsurg.2016.05.004. PMID: 27521712

Recent clinical studies

Etiology

Gilna GP, Saberi RA, Huerta CT, O'Neil CF, Ramsey WA, Parreco JP, Thorson CM, Sola JE, Perez EA
J Pediatr Surg 2022 May;57(5):932-936. Epub 2022 Jan 13 doi: 10.1016/j.jpedsurg.2021.12.041. PMID: 35063253
Takayama H, Toyonaga T, Yoshizaki T, Abe H, Nakai T, Ueda C, Urakami S, Kaku H, Shimamoto Y, Matsumoto K, Tsuda K, Sakaguchi H, Matsuoka K, Baba S, Takihara H, Ikezawa N, Tanaka S, Takao M, Takao T, Morita Y, Kodama Y
J Gastroenterol Hepatol 2021 Nov;36(11):3158-3163. Epub 2021 Jun 25 doi: 10.1111/jgh.15582. PMID: 34129253
Galea R, Said E
Neonatal Netw 2018 Jul;37(4):197-204. Epub 2018 Jul 1 doi: 10.1891/0730-0832.37.4.197. PMID: 30567916
Hendricks CM, Edgerton CA, Lesher AP
Am Surg 2018 Sep 1;84(9):e354-e356. PMID: 30269705
Al-Ansari A, Altokhais TI
Pediatr Int 2016 Jul;58(7):619-21. Epub 2016 Jul 7 doi: 10.1111/ped.12958. PMID: 27389044

Diagnosis

Rich BS, Dolgin SE
Pediatr Rev 2021 Oct;42(10):539-545. doi: 10.1542/pir.2020-003277. PMID: 34599053
Jobson M, Hall NJ
Semin Pediatr Surg 2016 Aug;25(4):219-24. Epub 2016 May 10 doi: 10.1053/j.sempedsurg.2016.05.004. PMID: 27521712
St Peter SD, Snyder CL
Semin Pediatr Surg 2016 Aug;25(4):197. Epub 2016 May 24 doi: 10.1053/j.sempedsurg.2016.05.008. PMID: 27521707
Al-Ansari A, Altokhais TI
Pediatr Int 2016 Jul;58(7):619-21. Epub 2016 Jul 7 doi: 10.1111/ped.12958. PMID: 27389044
Bissonnette B, Sullivan PJ
Can J Anaesth 1991 Jul;38(5):668-76. doi: 10.1007/BF03008206. PMID: 1934223

Therapy

Disma N, Engelhardt T, Hansen TG, de Graaff JC, Virag K, Habre W; NECTARINE Group of the European Society of Anaesthesiology and Intensive; AUSTRIA (Maria Vittinghoff); BELGIUM (Francis Veyckemans); CROATIA (Sandra Kralik); CZECH REPUBLIC (Jiří Žurek); DENMARK (Tom Hansen); ESTONIA (Reet Kikas); FINLAND (Tuula Manner); FRANCE (Christophe Dadure, Anne Lafargue); GERMANY (Karin Becke, Claudia Hoehne); GREECE (Anna Malisiova); HUNGARY (Andrea Székely); IRELAND (Brendan O’Hare); ITALY (Nicola Disma); LATVIA (Zane Straume); LITHUANIA (Laura Lukosiene); LUXEMBOURG (Bernd Schmitz); MALTA (Francis Borg); NETHERLANDS (Jurgen de Graaff); NORWAY (Wenche B Boerke); POLAND (Marzena Zielinska); PORTUGAL (Maria Domingas Patuleia); ROMANIA (Radu Tabacaru); SERBIA (Dusica Simic); SLOVAKIA (Miloslav Hanula); SLOVENIA (Jelena Berger); SPAIN (Ignacio Gálvez Escalera); SWEDEN (Albert Castellheim); SWITZERLAND (Walid Habre); TURKEY (Dilek Özcengiz - Zehra Hatipoğlu); UKRAINE (Dmytro Dmytriiev); UNITED KINGDOM (Thomas Engelhardt, Suellen Walker); Management Team
Br J Anaesth 2022 Nov;129(5):734-739. Epub 2022 Sep 6 doi: 10.1016/j.bja.2022.07.041. PMID: 36085092
Zaghal A, El-Majzoub N, Jaafar R, Aoun B, Jradi N
Pediatr Ann 2021 Mar;50(3):e136-e141. Epub 2021 Mar 1 doi: 10.3928/19382359-20210215-01. PMID: 34038653
Lauriti G, Cascini V, Chiesa PL, Pierro A, Zani A
Eur J Pediatr Surg 2018 Oct;28(5):393-399. Epub 2017 Jul 12 doi: 10.1055/s-0037-1604116. PMID: 28701002
Jobson M, Hall NJ
Semin Pediatr Surg 2016 Aug;25(4):219-24. Epub 2016 May 10 doi: 10.1053/j.sempedsurg.2016.05.004. PMID: 27521712
Prisant LM, Spaulding VC
J Clin Hypertens (Greenwich) 2006 Apr;8(4):296-8. doi: 10.1111/j.1524-6175.2006.05179.x. PMID: 16596036Free PMC Article

Prognosis

Mazurak M, Patkowski D
J Pediatr Surg 2021 Oct;56(10):1904-1907. Epub 2021 May 26 doi: 10.1016/j.jpedsurg.2021.05.009. PMID: 34172284
Hendricks CM, Edgerton CA, Lesher AP
Am Surg 2018 Sep 1;84(9):e354-e356. PMID: 30269705
Al-Ansari A, Altokhais TI
Pediatr Int 2016 Jul;58(7):619-21. Epub 2016 Jul 7 doi: 10.1111/ped.12958. PMID: 27389044
Dinkevich E, Ozuah PO
Pediatr Rev 2000 Jul;21(7):249-50. doi: 10.1542/pir.21-7-249. PMID: 10878190
Downey EC Jr
Semin Pediatr Surg 1998 Nov;7(4):220-4. doi: 10.1016/s1055-8586(98)70034-4. PMID: 9840902

Clinical prediction guides

Takayama H, Toyonaga T, Yoshizaki T, Abe H, Nakai T, Ueda C, Urakami S, Kaku H, Shimamoto Y, Matsumoto K, Tsuda K, Sakaguchi H, Matsuoka K, Baba S, Takihara H, Ikezawa N, Tanaka S, Takao M, Takao T, Morita Y, Kodama Y
J Gastroenterol Hepatol 2021 Nov;36(11):3158-3163. Epub 2021 Jun 25 doi: 10.1111/jgh.15582. PMID: 34129253
Sullivan KJ, Chan E, Vincent J, Iqbal M, Wayne C, Nasr A; Canadian Association of Paediatric Surgeons Evidence-Based Resource
Pediatrics 2016 Jan;137(1) Epub 2015 Dec 30 doi: 10.1542/peds.2015-2550. PMID: 26719292
Brosens E, Ploeg M, van Bever Y, Koopmans AE, IJsselstijn H, Rottier RJ, Wijnen R, Tibboel D, de Klein A
Eur J Med Genet 2014 Aug;57(8):440-52. Epub 2014 Jun 13 doi: 10.1016/j.ejmg.2014.05.009. PMID: 24931924
Yusuf TE, Brugge WR
Curr Opin Gastroenterol 2006 Sep;22(5):570-3. doi: 10.1097/01.mog.0000239874.13867.41. PMID: 16891891
Downey EC Jr
Semin Pediatr Surg 1998 Nov;7(4):220-4. doi: 10.1016/s1055-8586(98)70034-4. PMID: 9840902

Recent systematic reviews

Wu P, Chu L, Yang Y, Yu Z, Tian Y
Int J Colorectal Dis 2023 May 8;38(1):118. doi: 10.1007/s00384-023-04402-z. PMID: 37154949
Obaid YY, Toubasi AA, Albustanji FH, Al-Qawasmeh AR
J Pediatr Surg 2023 Mar;58(3):458-466. Epub 2022 Aug 24 doi: 10.1016/j.jpedsurg.2022.08.016. PMID: 36137827
Lunger F, Staerkle RF, Muff JL, Fink L, Holland-Cunz SG, Vuille-Dit-Bille RN
J Surg Res 2022 Jun;274:1-8. Epub 2022 Feb 2 doi: 10.1016/j.jss.2021.12.042. PMID: 35104694
van den Bunder FAIM, van Wijk L, van Woensel JBM, Stevens MF, van Heurn LWE, Derikx JPM
Paediatr Anaesth 2020 Jul;30(7):749-758. Epub 2020 Jun 18 doi: 10.1111/pan.13879. PMID: 32298502Free PMC Article
Lauriti G, Cascini V, Chiesa PL, Pierro A, Zani A
Eur J Pediatr Surg 2018 Oct;28(5):393-399. Epub 2017 Jul 12 doi: 10.1055/s-0037-1604116. PMID: 28701002

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