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Gastric leiomyosarcoma

MedGen UID:
196652
Concept ID:
C0744295
Neoplastic Process
Synonyms: Gastric Leiomyosarcoma; gastric leiomyosarcoma; gastric leiomyosarcoma (disease); Leiomyosarcoma of stomach; leiomyosarcoma of stomach; stomach leiomyosarcoma
SNOMED CT: Leiomyosarcoma of stomach (447785000)
 
HPO: HP:0031025
Monarch Initiative: MONDO:0003367

Definition

A malignant neoplasm of the stomach that grows submucosally in the gastric wall. Necrosis and hemorrhage may be visible radiologically. Histologically, spindle cells with abnormal mitotic activity may be visible. [from HPO]

Term Hierarchy

Professional guidelines

PubMed

Carson W, Karakousis C, Douglass H, Rao U, Palmer ML
Ann Surg Oncol 1994 May;1(3):244-51. doi: 10.1007/BF02303530. PMID: 7531105

Recent clinical studies

Etiology

Kawaguchi K, Igarashi K, Murakami T, Kiyuna T, Nelson SD, Dry SM, Li Y, Russell TA, Singh AS, Chmielowski B, Unno M, Eilber FC, Hoffman RM
Cell Cycle 2017 Jun 3;16(11):1063-1069. Epub 2017 Apr 20 doi: 10.1080/15384101.2017.1314406. PMID: 28426279Free PMC Article
Masaoka A, Yamakawa Y, Niwa H, Fukai I, Saito Y, Tokudome S, Nakahara K, Fujii Y
Eur J Cardiothorac Surg 1994;8(5):251-3. doi: 10.1016/1010-7940(94)90155-4. PMID: 8043287
Lee DH, Choi BI, Lee MG, Park CM, Park KS, Ko YT, Lim JH, Auh YH
AJR Am J Roentgenol 1994 Jul;163(1):77-80. doi: 10.2214/ajr.163.1.8010252. PMID: 8010252
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Nauert TC, Zornoza J, Ordonez N
AJR Am J Roentgenol 1982 Aug;139(2):291-7. doi: 10.2214/ajr.139.2.291. PMID: 6979881

Diagnosis

Yamamoto A, Tateishi Y, Aikou S, Seto Y, Ushiku T
Pathol Int 2021 Dec;71(12):837-843. Epub 2021 Sep 14 doi: 10.1111/pin.13165. PMID: 34520615
Garg R, AlRajjal A, Berri R, Barawi M
J Gastrointest Cancer 2020 Mar;51(1):335-340. doi: 10.1007/s12029-019-00269-y. PMID: 31227984
Hasnaoui A, Jouini R, Haddad D, Zaafouri H, Bouhafa A, Ben Maamer A, Ben Brahim E
BMC Surg 2018 Aug 17;18(1):62. doi: 10.1186/s12893-018-0393-4. PMID: 30119659Free PMC Article
Masaoka A, Yamakawa Y, Niwa H, Fukai I, Saito Y, Tokudome S, Nakahara K, Fujii Y
Eur J Cardiothorac Surg 1994;8(5):251-3. doi: 10.1016/1010-7940(94)90155-4. PMID: 8043287
Nauert TC, Zornoza J, Ordonez N
AJR Am J Roentgenol 1982 Aug;139(2):291-7. doi: 10.2214/ajr.139.2.291. PMID: 6979881

Therapy

Kawaguchi K, Igarashi K, Murakami T, Kiyuna T, Nelson SD, Dry SM, Li Y, Russell TA, Singh AS, Chmielowski B, Unno M, Eilber FC, Hoffman RM
Cell Cycle 2017 Jun 3;16(11):1063-1069. Epub 2017 Apr 20 doi: 10.1080/15384101.2017.1314406. PMID: 28426279Free PMC Article
Fetscher S, Brugger W, Bertz H, Krieger G, Kanz L, Mertelsmann R, Lange W
Bone Marrow Transplant 1997 Nov;20(9):787-8. doi: 10.1038/sj.bmt.1700970. PMID: 9384483
Masaoka A, Yamakawa Y, Niwa H, Fukai I, Saito Y, Tokudome S, Nakahara K, Fujii Y
Eur J Cardiothorac Surg 1994;8(5):251-3. doi: 10.1016/1010-7940(94)90155-4. PMID: 8043287
Gold JE, Malamud SC, LaRosa F, Osband ME
Am J Hematol 1993 Sep;44(1):42-7. doi: 10.1002/ajh.2830440109. PMID: 8342564
Campbell DR, Mason WF, Flemming BK, Fraser DB
J Can Assoc Radiol 1985 Sep;36(3):212-5. PMID: 4044615

Prognosis

Hasnaoui A, Jouini R, Haddad D, Zaafouri H, Bouhafa A, Ben Maamer A, Ben Brahim E
BMC Surg 2018 Aug 17;18(1):62. doi: 10.1186/s12893-018-0393-4. PMID: 30119659Free PMC Article
Weledji EP, Enoworock G, Ngowe MN
BMC Res Notes 2014 Jul 29;7:479. doi: 10.1186/1756-0500-7-479. PMID: 25069607Free PMC Article
Hsieh CC, Shih CS, Wu YC, Huang BS, Hsu WH, Huang MH, Wang LS
Zhonghua Yi Xue Za Zhi (Taipei) 1999 Jul;62(7):418-24. PMID: 10418174
Masaoka A, Yamakawa Y, Niwa H, Fukai I, Saito Y, Tokudome S, Nakahara K, Fujii Y
Eur J Cardiothorac Surg 1994;8(5):251-3. doi: 10.1016/1010-7940(94)90155-4. PMID: 8043287
Nauert TC, Zornoza J, Ordonez N
AJR Am J Roentgenol 1982 Aug;139(2):291-7. doi: 10.2214/ajr.139.2.291. PMID: 6979881

Clinical prediction guides

Yamamoto A, Tateishi Y, Aikou S, Seto Y, Ushiku T
Pathol Int 2021 Dec;71(12):837-843. Epub 2021 Sep 14 doi: 10.1111/pin.13165. PMID: 34520615
Katai H, Sasako M, Sano T, Maruyama K
Ann Chir Gynaecol 1998;87(4):293-6. PMID: 9891769
Masaoka A, Yamakawa Y, Niwa H, Fukai I, Saito Y, Tokudome S, Nakahara K, Fujii Y
Eur J Cardiothorac Surg 1994;8(5):251-3. doi: 10.1016/1010-7940(94)90155-4. PMID: 8043287
Scatarige JC, Fishman EK, Jones B, Cameron JL, Sanders RC, Siegelman SS
J Comput Assist Tomogr 1985 Mar-Apr;9(2):320-7. doi: 10.1097/00004728-198503000-00017. PMID: 3973157
Lindsay PC, Ordonez N, Raaf JH
J Surg Oncol 1981;18(4):399-421. doi: 10.1002/jso.2930180409. PMID: 6172674

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