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Acute interstitial pneumonia

MedGen UID:
224822
Concept ID:
C1279945
Disease or Syndrome
Synonyms: Acute interstitial pneumonitis; Hamman-Rich syndrome
SNOMED CT: Acute interstitial pneumonia (236302005); Acute interstitial pneumonitis (35037009)
Modes of inheritance:
Unknown inheritance
MedGen UID:
989040
Concept ID:
CN307042
Finding
Source: Orphanet
Hereditary clinical entity whose mode of inheritance is unknown.
 
Monarch Initiative: MONDO:0019203
Orphanet: ORPHA79126

Definition

A rare rapidly progressive and histologically distinct form of idiopathic interstitial pneumonia. [from ORDO]

Professional guidelines

PubMed

Nishino M, Kusumoto M, Bankier AA, Kurihara Y, Zhang L, Rasheed Z, Meinhardt G, Arunachalam M, Taitt C, Wang Q, Powell CA
JCO Precis Oncol 2023 Sep;7:e2300391. doi: 10.1200/PO.23.00391. PMID: 38061008
Kalisz KR, Ramaiya NH, Laukamp KR, Gupta A
Radiographics 2019 Nov-Dec;39(7):1923-1937. Epub 2019 Oct 4 doi: 10.1148/rg.2019190036. PMID: 31584861
Vassallo R, Thomas CF
Curr Opin Rheumatol 2004 May;16(3):186-91. doi: 10.1097/00002281-200405000-00004. PMID: 15103243

Recent clinical studies

Etiology

Batra K, Adams TN
J Thorac Imaging 2023 Nov 1;38(Suppl 1):S19-S29. Epub 2023 Jul 12 doi: 10.1097/RTI.0000000000000728. PMID: 37505195
Gomerčić Palčić M, Turalija I, Vrbanić L, Folnožić I, Basioli Kasap E, Ulamec M
Acta Clin Croat 2022 Dec;61(4):722-726. doi: 10.20471/acc.2022.61.04.21. PMID: 37868166Free PMC Article
Shepherd HM, Terada Y, Takahashi T, Pasque MK, Kulkarni HS, Guillamet RV, Witt CA, Nava RG, Puri V, Kreisel D, Patterson GA, Hachem RR
Transplant Proc 2022 Oct;54(8):2313-2316. Epub 2022 Sep 6 doi: 10.1016/j.transproceed.2022.07.010. PMID: 36075742
Samarelli AV, Tonelli R, Marchioni A, Bruzzi G, Gozzi F, Andrisani D, Castaniere I, Manicardi L, Moretti A, Tabbì L, Cerri S, Beghè B, Dominici M, Clini E
Int J Mol Sci 2021 Aug 19;22(16) doi: 10.3390/ijms22168952. PMID: 34445658Free PMC Article
Silva CI, Müller NL
J Thorac Imaging 2009 Nov;24(4):260-73. doi: 10.1097/RTI.0b013e3181c1a9eb. PMID: 19935223

Diagnosis

Samarelli AV, Tonelli R, Marchioni A, Bruzzi G, Gozzi F, Andrisani D, Castaniere I, Manicardi L, Moretti A, Tabbì L, Cerri S, Beghè B, Dominici M, Clini E
Int J Mol Sci 2021 Aug 19;22(16) doi: 10.3390/ijms22168952. PMID: 34445658Free PMC Article
Kalisz KR, Ramaiya NH, Laukamp KR, Gupta A
Radiographics 2019 Nov-Dec;39(7):1923-1937. Epub 2019 Oct 4 doi: 10.1148/rg.2019190036. PMID: 31584861
Taniguchi H, Kondoh Y
Respirology 2016 Jul;21(5):810-20. Epub 2016 Apr 28 doi: 10.1111/resp.12786. PMID: 27123874
Vourlekis JS
Clin Chest Med 2004 Dec;25(4):739-47, vii. doi: 10.1016/j.ccm.2004.07.001. PMID: 15564019
Bouros D, Nicholson AC, Polychronopoulos V, du Bois RM
Eur Respir J 2000 Feb;15(2):412-8. doi: 10.1034/j.1399-3003.2000.15b31.x. PMID: 10706513

Therapy

Gomerčić Palčić M, Turalija I, Vrbanić L, Folnožić I, Basioli Kasap E, Ulamec M
Acta Clin Croat 2022 Dec;61(4):722-726. doi: 10.20471/acc.2022.61.04.21. PMID: 37868166Free PMC Article
Shepherd HM, Terada Y, Takahashi T, Pasque MK, Kulkarni HS, Guillamet RV, Witt CA, Nava RG, Puri V, Kreisel D, Patterson GA, Hachem RR
Transplant Proc 2022 Oct;54(8):2313-2316. Epub 2022 Sep 6 doi: 10.1016/j.transproceed.2022.07.010. PMID: 36075742
Kalisz KR, Ramaiya NH, Laukamp KR, Gupta A
Radiographics 2019 Nov-Dec;39(7):1923-1937. Epub 2019 Oct 4 doi: 10.1148/rg.2019190036. PMID: 31584861
Taniguchi H, Kondoh Y
Respirology 2016 Jul;21(5):810-20. Epub 2016 Apr 28 doi: 10.1111/resp.12786. PMID: 27123874
Vourlekis JS
Clin Chest Med 2004 Dec;25(4):739-47, vii. doi: 10.1016/j.ccm.2004.07.001. PMID: 15564019

Prognosis

Kalisz KR, Ramaiya NH, Laukamp KR, Gupta A
Radiographics 2019 Nov-Dec;39(7):1923-1937. Epub 2019 Oct 4 doi: 10.1148/rg.2019190036. PMID: 31584861
Silva CI, Müller NL
J Thorac Imaging 2009 Nov;24(4):260-73. doi: 10.1097/RTI.0b013e3181c1a9eb. PMID: 19935223
Swigris JJ, Brown KK
Semin Respir Crit Care Med 2006 Dec;27(6):659-67. doi: 10.1055/s-2006-957337. PMID: 17195142
Vourlekis JS
Clin Chest Med 2004 Dec;25(4):739-47, vii. doi: 10.1016/j.ccm.2004.07.001. PMID: 15564019
Bouros D, Nicholson AC, Polychronopoulos V, du Bois RM
Eur Respir J 2000 Feb;15(2):412-8. doi: 10.1034/j.1399-3003.2000.15b31.x. PMID: 10706513

Clinical prediction guides

Shepherd HM, Terada Y, Takahashi T, Pasque MK, Kulkarni HS, Guillamet RV, Witt CA, Nava RG, Puri V, Kreisel D, Patterson GA, Hachem RR
Transplant Proc 2022 Oct;54(8):2313-2316. Epub 2022 Sep 6 doi: 10.1016/j.transproceed.2022.07.010. PMID: 36075742
Cheng F, Lu T, Wang Y, Yuan D, Wei Z, Li Y, Li J, Tang R
Int J Exp Pathol 2022 Oct;103(5):190-197. Epub 2022 May 8 doi: 10.1111/iep.12443. PMID: 35527237Free PMC Article
Kalisz KR, Ramaiya NH, Laukamp KR, Gupta A
Radiographics 2019 Nov-Dec;39(7):1923-1937. Epub 2019 Oct 4 doi: 10.1148/rg.2019190036. PMID: 31584861
Mochimaru H, Fukuda Y, Azuma A, Osanai K, Saito Y, Mochimaru T, Gemma A
Sarcoidosis Vasc Diffuse Lung Dis 2015 Jan 5;31(4):325-35. PMID: 25591144
Ichikado K
Semin Ultrasound CT MR 2014 Feb;35(1):39-46. Epub 2013 Oct 22 doi: 10.1053/j.sult.2013.10.007. PMID: 24480142

Recent systematic reviews

Agarwal R, Jindal SK
Eur J Intern Med 2008 Jun;19(4):227-35. Epub 2008 Jan 16 doi: 10.1016/j.ejim.2007.04.024. PMID: 18471669

Supplemental Content

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