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Adrenal gland ganglioneuroblastoma

MedGen UID:
231355
•Concept ID:
C1332176
•
Neoplastic Process
Synonyms: Adrenal Ganglioneuroblastoma; adrenal ganglioneuroblastoma; Adrenal Gland Ganglioneuroblastoma; adrenal gland ganglioneuroblastoma; adrenal gland ganglioneuroblastoma (disease); ganglioneuroblastoma (disease) of adrenal gland
 
Monarch Initiative: MONDO:0004477

Definition

A ganglioneuroblastoma arising from the adrenal gland. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVAdrenal gland ganglioneuroblastoma

Professional guidelines

PubMed

Clinical features and treatment options for pediatric adrenal incidentalomas: a retrospective single center study.
Zhu X, Liu S, Yuan Y, Gu N, Sha J, Guo Y, Deng Y
BMC Pediatr 2024 Mar 16;24(1):186. doi: 10.1186/s12887-024-04673-7. PMID: 38491421Free PMC Article
Early Detection and Treatment of Neuroblastic Tumor with Opsoclonus-Myoclonus Syndrome Improve Neurological Outcome: A Review of Five Cases at a Single Institution in Japan.
Takama Y, Yoneda A, Nakamura T, Nakaoka T, Higashio A, Santo K, Kuki I, Kawawaki H, Tomiwa K, Hara J
Eur J Pediatr Surg 2016 Feb;26(1):54-9. Epub 2015 Sep 26 doi: 10.1055/s-0035-1564714. PMID: 26409265
DNA-topoisomerase I, a new target for the treatment of neuroblastoma.
Vassal G, Pondarré C, Cappelli C, Terrier-Lacombe MJ, Boland I, Morizet J, Bénard J, Vénuat AM, Ardouin P, Hartmann O, Gouyette A
Eur J Cancer 1997 Oct;33(12):2011-5. doi: 10.1016/s0959-8049(97)00296-7. PMID: 9516844

Recent clinical studies

Etiology

ROHHAD(NET) Syndrome: Systematic Review of the Clinical Timeline and Recommendations for Diagnosis and Prognosis.
Harvengt J, Gernay C, Mastouri M, Farhat N, Lebrethon MC, Seghaye MC, Bours V
J Clin Endocrinol Metab 2020 Jul 1;105(7) doi: 10.1210/clinem/dgaa247. PMID: 32407531
Adrenal masses in children: Imaging, surgical treatment and outcome.
Emre Ş, Özcan R, Bakır AC, Kuruğoğlu S, Çomunoğlu N, Şen HS, Celkan T, Tekant GT
Asian J Surg 2020 Jan;43(1):207-212. Epub 2019 Apr 6 doi: 10.1016/j.asjsur.2019.03.012. PMID: 30962018
Update on Adrenal Tumours in 2017 World Health Organization (WHO) of Endocrine Tumours.
Lam AK
Endocr Pathol 2017 Sep;28(3):213-227. doi: 10.1007/s12022-017-9484-5. PMID: 28477311
HMGA molecules in neuroblastic tumors.
Cerignoli F, Ambrosi C, Mellone M, Assimi I, di Marcotullio L, Gulino A, Giannini G
Ann N Y Acad Sci 2004 Dec;1028:122-32. doi: 10.1196/annals.1322.013. PMID: 15650238
Neuroblastoma, ganglioneuroblastoma, and ganglioneuroma: radiologic-pathologic correlation.
Lonergan GJ, Schwab CM, Suarez ES, Carlson CL
Radiographics 2002 Jul-Aug;22(4):911-34. doi: 10.1148/radiographics.22.4.g02jl15911. PMID: 12110723

Diagnosis

Benign Neurogenic Tumors.
Farma JM, Porpiglia AS, Vo ET
Surg Clin North Am 2022 Aug;102(4):679-693. doi: 10.1016/j.suc.2022.04.007. PMID: 35952696
ROHHAD(NET) Syndrome: Systematic Review of the Clinical Timeline and Recommendations for Diagnosis and Prognosis.
Harvengt J, Gernay C, Mastouri M, Farhat N, Lebrethon MC, Seghaye MC, Bours V
J Clin Endocrinol Metab 2020 Jul 1;105(7) doi: 10.1210/clinem/dgaa247. PMID: 32407531
Uncommon adrenal masses: CT and MRI features with histopathologic correlation.
Guo YK, Yang ZG, Li Y, Deng YP, Ma ES, Min PQ, Zhang XC
Eur J Radiol 2007 Jun;62(3):359-70. doi: 10.1016/j.ejrad.2006.12.011. PMID: 17532488
Renal and adrenal tumours in children.
McHugh K
Cancer Imaging 2007 Mar 5;7(1):41-51. doi: 10.1102/1470-7330.2007.0007. PMID: 17339140Free PMC Article
HMGA molecules in neuroblastic tumors.
Cerignoli F, Ambrosi C, Mellone M, Assimi I, di Marcotullio L, Gulino A, Giannini G
Ann N Y Acad Sci 2004 Dec;1028:122-32. doi: 10.1196/annals.1322.013. PMID: 15650238

Therapy

Prolonged Isotretinoin in Ultra High-Risk Neuroblastoma.
Cash T, Alazraki A, Qayed M, Katzenstein HM
J Pediatr Hematol Oncol 2017 Jan;39(1):e33-e35. doi: 10.1097/MPH.0000000000000695. PMID: 27820130
Cerebral ganglioneuroblastoma of adult onset: two patients and a review of the literature.
Schipper MH, van Duinen SG, Taphoorn MJ, Kloet A, Walchenbach R, Wiggenraad RG, Vecht CJ
Clin Neurol Neurosurg 2012 Jul;114(6):529-34. Epub 2012 Apr 15 doi: 10.1016/j.clineuro.2012.03.015. PMID: 22510501
Laparoscopic adrenalectomy in children.
Lopes RI, Dénes FT, Bissoli J, Mendonca BB, Srougi M
J Pediatr Urol 2012 Aug;8(4):379-85. Epub 2011 Sep 29 doi: 10.1016/j.jpurol.2011.07.012. PMID: 21955529
Differentiation between tuberculosis and primary tumors in the adrenal gland: evaluation with contrast-enhanced CT.
Yang ZG, Guo YK, Li Y, Min PQ, Yu JQ, Ma ES
Eur Radiol 2006 Sep;16(9):2031-6. Epub 2006 Jan 25 doi: 10.1007/s00330-005-0096-y. PMID: 16435135
Ganglioneuroblastoma and persistent ataxia.
Griffin GC, Hensley MF
Clin Pediatr (Phila) 1982 Aug;21(8):457. PMID: 7083718

Prognosis

ROHHAD(NET) Syndrome: Systematic Review of the Clinical Timeline and Recommendations for Diagnosis and Prognosis.
Harvengt J, Gernay C, Mastouri M, Farhat N, Lebrethon MC, Seghaye MC, Bours V
J Clin Endocrinol Metab 2020 Jul 1;105(7) doi: 10.1210/clinem/dgaa247. PMID: 32407531
Update on Adrenal Tumours in 2017 World Health Organization (WHO) of Endocrine Tumours.
Lam AK
Endocr Pathol 2017 Sep;28(3):213-227. doi: 10.1007/s12022-017-9484-5. PMID: 28477311
Laparoscopic adrenalectomy in children.
Lopes RI, Dénes FT, Bissoli J, Mendonca BB, Srougi M
J Pediatr Urol 2012 Aug;8(4):379-85. Epub 2011 Sep 29 doi: 10.1016/j.jpurol.2011.07.012. PMID: 21955529
Renal and adrenal tumours in children.
McHugh K
Cancer Imaging 2007 Mar 5;7(1):41-51. doi: 10.1102/1470-7330.2007.0007. PMID: 17339140Free PMC Article
Neuroblastoma, ganglioneuroblastoma, and ganglioneuroma: radiologic-pathologic correlation.
Lonergan GJ, Schwab CM, Suarez ES, Carlson CL
Radiographics 2002 Jul-Aug;22(4):911-34. doi: 10.1148/radiographics.22.4.g02jl15911. PMID: 12110723

Clinical prediction guides

Clinical features and treatment options for pediatric adrenal incidentalomas: a retrospective single center study.
Zhu X, Liu S, Yuan Y, Gu N, Sha J, Guo Y, Deng Y
BMC Pediatr 2024 Mar 16;24(1):186. doi: 10.1186/s12887-024-04673-7. PMID: 38491421Free PMC Article
Primary cervical ganglioneuroblastoma: A case report.
Lu D, Liu J, Chen Y, Chen F, Yang H
Medicine (Baltimore) 2018 Mar;97(12):e0090. doi: 10.1097/MD.0000000000010090. PMID: 29561407Free PMC Article
Update on Adrenal Tumours in 2017 World Health Organization (WHO) of Endocrine Tumours.
Lam AK
Endocr Pathol 2017 Sep;28(3):213-227. doi: 10.1007/s12022-017-9484-5. PMID: 28477311
Costello syndrome: a cancer predisposing syndrome?
Moroni I, Bedeschi F, Luksch R, Casanova M, D'Incerti L, Uziel G, Selicorni A
Clin Dysmorphol 2000 Oct;9(4):265-8. doi: 10.1097/00019605-200009040-00006. PMID: 11045582
Bilateral adrenal ganglioneuroblastoma with neuromelanin. Clinical and pathologic observations.
Gonzalez-Crussi F, Hsueh W
Cancer 1988 Mar 15;61(6):1159-66. doi: 10.1002/1097-0142(19880315)61:6<1159::aid-cncr2820610617>3.0.co;2-s. PMID: 3277701

Recent systematic reviews

Composite phaeochromocytomas-a systematic review of published literature.
Dhanasekar K, Visakan V, Tahir F, Balasubramanian SP
Langenbecks Arch Surg 2022 Mar;407(2):517-527. Epub 2021 Mar 2 doi: 10.1007/s00423-021-02129-5. PMID: 33651160Free PMC Article
ROHHAD(NET) Syndrome: Systematic Review of the Clinical Timeline and Recommendations for Diagnosis and Prognosis.
Harvengt J, Gernay C, Mastouri M, Farhat N, Lebrethon MC, Seghaye MC, Bours V
J Clin Endocrinol Metab 2020 Jul 1;105(7) doi: 10.1210/clinem/dgaa247. PMID: 32407531

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