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Pediatric myxoid chondrosarcoma

MedGen UID:
232065
Concept ID:
C1332984
Neoplastic Process
Synonyms: Childhood Extraskeletal Myxoid Chondrosarcoma; Childhood Myxoid Chondrosarcoma; childhood myxoid chondrosarcoma; myxoid chondrosarcoma of childhood; Pediatric Myxoid Chondrosarcoma; pediatric myxoid chondrosarcoma
 
Monarch Initiative: MONDO:0003898

Definition

A myxoid chondrosarcoma occurring in children. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVPediatric myxoid chondrosarcoma

Professional guidelines

PubMed

Agaimy A
Surg Pathol Clin 2019 Mar;12(1):149-163. doi: 10.1016/j.path.2018.10.006. PMID: 30709441

Recent clinical studies

Etiology

Martínez-Trufero J, Cruz Jurado J, Hernández-León CN, Correa R, Asencio JM, Bernabeu D, Alvarez R, Hindi N, Mata C, Marquina G, Martínez V, Redondo A, Floría LJ, Gómez-Mateo MC, Lavernia J, Sebio A, Garcia Del Muro X, Martin-Broto J, Valverde-Morales C
Cancer Treat Rev 2021 Sep;99:102260. Epub 2021 Jul 16 doi: 10.1016/j.ctrv.2021.102260. PMID: 34340159
Brčić I, Godschachner TM, Bergovec M, Igrec J, Till H, Lackner H, Scheipl S, Kashofer K, Brodowicz T, Leithner A, Szkandera J, Liegl-Atzwanger B
Mod Pathol 2021 Feb;34(2):396-407. Epub 2020 Aug 28 doi: 10.1038/s41379-020-00657-x. PMID: 32860002Free PMC Article
Hatina J, Kripnerova M, Houfkova K, Pesta M, Kuncova J, Sana J, Slaby O, Rodríguez R
Adv Exp Med Biol 2019;1123:95-118. doi: 10.1007/978-3-030-11096-3_7. PMID: 31016597
Koelsche C, Kriegsmann M, Kommoss FKF, Stichel D, Kriegsmann K, Vokuhl C, Grünewald TGP, Romero-Pérez L, Kirchner T, de Alava E, Diaz-Martin J, Hartmann W, Baumhoer D, Antonescu CR, Szuhai K, Flucke U, Dirksen U, Pfister SM, Jones DTW, Mechtersheimer G, von Deimling A
J Cancer Res Clin Oncol 2019 May;145(5):1273-1281. Epub 2019 Mar 20 doi: 10.1007/s00432-019-02895-2. PMID: 30895378Free PMC Article
Kohashi K, Nakatsura T, Kinoshita Y, Yamamoto H, Yamada Y, Tajiri T, Taguchi T, Iwamoto Y, Oda Y
Hum Pathol 2013 Apr;44(4):526-33. Epub 2012 Oct 16 doi: 10.1016/j.humpath.2012.06.014. PMID: 23084579

Diagnosis

Martínez-Trufero J, Cruz Jurado J, Hernández-León CN, Correa R, Asencio JM, Bernabeu D, Alvarez R, Hindi N, Mata C, Marquina G, Martínez V, Redondo A, Floría LJ, Gómez-Mateo MC, Lavernia J, Sebio A, Garcia Del Muro X, Martin-Broto J, Valverde-Morales C
Cancer Treat Rev 2021 Sep;99:102260. Epub 2021 Jul 16 doi: 10.1016/j.ctrv.2021.102260. PMID: 34340159
Al Khader A, Nsour E, Al-Zubi RB, Al Maadat HMD
Medicine (Baltimore) 2019 Apr;98(15):e15207. doi: 10.1097/MD.0000000000015207. PMID: 30985717Free PMC Article
Koelsche C, Kriegsmann M, Kommoss FKF, Stichel D, Kriegsmann K, Vokuhl C, Grünewald TGP, Romero-Pérez L, Kirchner T, de Alava E, Diaz-Martin J, Hartmann W, Baumhoer D, Antonescu CR, Szuhai K, Flucke U, Dirksen U, Pfister SM, Jones DTW, Mechtersheimer G, von Deimling A
J Cancer Res Clin Oncol 2019 May;145(5):1273-1281. Epub 2019 Mar 20 doi: 10.1007/s00432-019-02895-2. PMID: 30895378Free PMC Article
Agaimy A
Surg Pathol Clin 2019 Mar;12(1):149-163. doi: 10.1016/j.path.2018.10.006. PMID: 30709441
Kohashi K, Nakatsura T, Kinoshita Y, Yamamoto H, Yamada Y, Tajiri T, Taguchi T, Iwamoto Y, Oda Y
Hum Pathol 2013 Apr;44(4):526-33. Epub 2012 Oct 16 doi: 10.1016/j.humpath.2012.06.014. PMID: 23084579

Therapy

Ibrahim ZA, Chan WH, Wong SL, Ong EJ, Narihan MZ
J Orthop Surg (Hong Kong) 2014 Dec;22(3):423-6. doi: 10.1177/230949901402200331. PMID: 25550031
Kilpatrick SE, Cappellari JO, Bos GD, Gold SH, Ward WG
Am J Clin Pathol 2001 Jan;115(1):59-68. doi: 10.1309/YN14-K8U4-5FLJ-DGJE. PMID: 11190808

Prognosis

Almoiliqy M, Al-Danakh A, Safi M, Alradhi M, Al-Azab M, Adlat S, Zhou W, Mohammed ASA, Al-Maamari A
Oxid Med Cell Longev 2021;2021:9999529. Epub 2021 Apr 30 doi: 10.1155/2021/9999529. PMID: 34007412Free PMC Article
Agaimy A
Surg Pathol Clin 2019 Mar;12(1):149-163. doi: 10.1016/j.path.2018.10.006. PMID: 30709441
Ibrahim ZA, Chan WH, Wong SL, Ong EJ, Narihan MZ
J Orthop Surg (Hong Kong) 2014 Dec;22(3):423-6. doi: 10.1177/230949901402200331. PMID: 25550031
Kohashi K, Nakatsura T, Kinoshita Y, Yamamoto H, Yamada Y, Tajiri T, Taguchi T, Iwamoto Y, Oda Y
Hum Pathol 2013 Apr;44(4):526-33. Epub 2012 Oct 16 doi: 10.1016/j.humpath.2012.06.014. PMID: 23084579
Boyd AS
J Cutan Pathol 2012 Sep;39(9):872-6. Epub 2012 Jul 16 doi: 10.1111/j.1600-0560.2012.01943.x. PMID: 22804337

Clinical prediction guides

Brčić I, Godschachner TM, Bergovec M, Igrec J, Till H, Lackner H, Scheipl S, Kashofer K, Brodowicz T, Leithner A, Szkandera J, Liegl-Atzwanger B
Mod Pathol 2021 Feb;34(2):396-407. Epub 2020 Aug 28 doi: 10.1038/s41379-020-00657-x. PMID: 32860002Free PMC Article
Kilpatrick SE, Cappellari JO, Bos GD, Gold SH, Ward WG
Am J Clin Pathol 2001 Jan;115(1):59-68. doi: 10.1309/YN14-K8U4-5FLJ-DGJE. PMID: 11190808
Fletcher JA, Lipinski KK, Weidner N, Morton CC
Cancer Genet Cytogenet 1989 Aug;41(1):115-21. doi: 10.1016/0165-4608(89)90115-5. PMID: 2766246

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