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Extragastrointestinal Gastrointestinal Stromal Tumor

MedGen UID:
234242
Concept ID:
C1333500
Neoplastic Process
Synonym: Extragastrointestinal Stromal Tumor

Definition

A rare gastrointestinal stromal tumor that presents as a solitary mass outside the gastrointestinal tract. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVExtragastrointestinal Gastrointestinal Stromal Tumor

Professional guidelines

PubMed

Priya V, Kumari N, Krishnani N
Turk Patoloji Derg 2020;36(2):116-125. doi: 10.5146/tjpath.2019.01470. PMID: 31538651Free PMC Article
Patnayak R, Jena A, Parthasarathy S, Prasad PD, Reddy MK, Chowhan AK, Rukamangadha N, Phaneendra BV
Indian J Cancer 2013 Jan-Mar;50(1):41-5. doi: 10.4103/0019-509X.112298. PMID: 23713043
Calabuig-Farinas S, Lopez-Guerrero JA, Llombart-Bosch A
Arkh Patol 2011 Jul-Aug;73(4):13-21. PMID: 22164425

Recent clinical studies

Etiology

Liu L, Feng Y, Ye Y, Wang Z, Xu X
Surg Endosc 2023 Nov;37(11):8498-8510. Epub 2023 Sep 28 doi: 10.1007/s00464-023-10433-y. PMID: 37770606
Etit D, Kar H, Ekinci N, Yenipazar AE, Çakalağaoğlu F
Balkan Med J 2017 Apr 5;34(2):168-171. doi: 10.4274/balkanmedj.2015.1331. PMID: 28418346Free PMC Article
AbdullGaffar B
South Med J 2010 Oct;103(10):1004-8. doi: 10.1097/SMJ.0b013e3181ef2f41. PMID: 20818304
Miettinen M, Lasota J
Semin Diagn Pathol 2006 May;23(2):70-83. doi: 10.1053/j.semdp.2006.09.001. PMID: 17193820
Miettinen M, Sarlomo-Rikala M, Lasota J
Ann Chir Gynaecol 1998;87(4):278-81. PMID: 9891765

Diagnosis

Mohamed N, Khan M, Hosler G, Tumminello K
J Cutan Pathol 2023 Aug;50(8):723-729. Epub 2023 May 1 doi: 10.1111/cup.14432. PMID: 37127848
Moldovan VT, Pătraşcu OM, Ali L, Costache M, Sajin M
Rom J Morphol Embryol 2021 Oct-Dec;62(4):1011-1016. doi: 10.47162/RJME.62.4.13. PMID: 35673820Free PMC Article
You YH, Zhang Y
J Int Med Res 2018 Oct;46(10):4343-4349. Epub 2018 Aug 28 doi: 10.1177/0300060518791677. PMID: 30152251Free PMC Article
Etit D, Kar H, Ekinci N, Yenipazar AE, Çakalağaoğlu F
Balkan Med J 2017 Apr 5;34(2):168-171. doi: 10.4274/balkanmedj.2015.1331. PMID: 28418346Free PMC Article
Padhi S, Sarangi R, Mallick S
JOP 2013 Jan 10;14(1):1-14. doi: 10.6092/1590-8577/1293. PMID: 23306329

Therapy

Lu LJ, Xu XP, Dong F, Min J
Medicine (Baltimore) 2020 Oct 2;99(40):e22493. doi: 10.1097/MD.0000000000022493. PMID: 33019445Free PMC Article
Padhi S, Nayak HK
Adv Exp Med Biol 2016;913:207-228. doi: 10.1007/978-981-10-1061-3_14. PMID: 27796890
Yüksel ÖH, Akan S, Yildirim Ç, Ürkmez A, Verit A
Arch Ital Urol Androl 2015 Jul 7;87(2):177-8. doi: 10.4081/aiua.2015.2.177. PMID: 26150044
Li H, Li J, Li X, Kang Y, Wei Q
World J Surg Oncol 2013 Aug 5;11(1):174. doi: 10.1186/1477-7819-11-174. PMID: 23915013Free PMC Article
Frilling A, Malago M, Testa G, Schleyer E, Grabellus F, Kronenberger R, Li J, Broelsch CE
Transplant Proc 2010 Nov;42(9):3843-8. doi: 10.1016/j.transproceed.2010.06.016. PMID: 21094867

Prognosis

Beltrame V, Gruppo M, Pastorelli D, Pizzi S, Merigliano S, Sperti C
World J Surg Oncol 2014 Apr 23;12:105. doi: 10.1186/1477-7819-12-105. PMID: 24755359Free PMC Article
Yi JH, Sim J, Park BB, Lee YY, Jung WS, Jang HJ, Ha TK, Paik SS
Jpn J Clin Oncol 2013 Dec;43(12):1269-72. Epub 2013 Oct 29 doi: 10.1093/jjco/hyt158. PMID: 24168806
Nakajima T, Saito S, Sugiyama T, Murata K, Fukushima J, Horiuchi H
Pathol Int 2011 Nov;61(11):677-80. Epub 2011 Aug 30 doi: 10.1111/j.1440-1827.2011.02719.x. PMID: 22029680
Miettinen M, Lasota J
Semin Diagn Pathol 2006 May;23(2):70-83. doi: 10.1053/j.semdp.2006.09.001. PMID: 17193820
Yamamoto H, Oda Y, Kawaguchi K, Nakamura N, Takahira T, Tamiya S, Saito T, Oshiro Y, Ohta M, Yao T, Tsuneyoshi M
Am J Surg Pathol 2004 Apr;28(4):479-88. doi: 10.1097/00000478-200404000-00007. PMID: 15087667

Clinical prediction guides

Shabunin A, Bagatelia Z, Tavobilov M, Dolidze D, Andreytsev I, Sheviakova T, Ivanova N, Foshina A, Chibukhchyan Z, Covantsev S
Folia Med (Plovdiv) 2024 Apr 30;66(2):291-297. doi: 10.3897/folmed.66.e113215. PMID: 38690828
Etit D, Kar H, Ekinci N, Yenipazar AE, Çakalağaoğlu F
Balkan Med J 2017 Apr 5;34(2):168-171. doi: 10.4274/balkanmedj.2015.1331. PMID: 28418346Free PMC Article
Qi Y, Zhao W, Wang Z, Li T, Meng X
Tohoku J Exp Med 2014 May;233(1):65-72. doi: 10.1620/tjem.233.65. PMID: 24827382
Lopes LF, Bacchi CE
Appl Immunohistochem Mol Morphol 2009 Mar;17(2):146-50. doi: 10.1097/PAI.0b013e31818fcfde. PMID: 19077908
Yamamoto H, Oda Y, Kawaguchi K, Nakamura N, Takahira T, Tamiya S, Saito T, Oshiro Y, Ohta M, Yao T, Tsuneyoshi M
Am J Surg Pathol 2004 Apr;28(4):479-88. doi: 10.1097/00000478-200404000-00007. PMID: 15087667

Recent systematic reviews

Xu L, Zhang M, Xu M
Medicine (Baltimore) 2019 May;98(20):e15482. doi: 10.1097/MD.0000000000015482. PMID: 31096446Free PMC Article
Padhi S, Sarangi R, Mallick S
JOP 2013 Jan 10;14(1):1-14. doi: 10.6092/1590-8577/1293. PMID: 23306329

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