Diencephalic astrocytomas

MedGen UID:: 272542
•Concept ID:: C1333284
•: Neoplastic Process

Synonyms:	astrocytoma (excluding glioblastoma) of diencephalon; Astrocytoma of Diencephalon; astrocytoma of diencephalon; Astrocytoma of the Diencephalon; astrocytoma of the diencephalon; Diencephalic Astrocytoma; diencephalic astrocytoma; Diencephalic Astrocytomas; diencephalic astrocytomas; diencephalon astrocytoma; diencephalon astrocytoma (excluding glioblastoma)

Monarch Initiative:	MONDO:0003169

Definition

A astrocytoma that involves the diencephalon. [from MONDO]

Term Hierarchy

GTR
MeSH

CClinical test, RResearch test, OOMIM, GGeneReviews, VClinVar

CROGVDiencephalic astrocytomas

Abnormality of the nervous system
- Abnormal nervous system morphology
  - Abnormal glial cell morphology
    - Abnormal astrocyte morphology
      - Astrocytoma
        Brain astrocytoma
        Diencephalic astrocytomas
        Anaplastic Diencephalic Astrocytoma

Professional guidelines

PubMed

Long-term follow-up of the multicenter, multidisciplinary treatment study HIT-LGG-1996 for low-grade glioma in children and adolescents of the German Speaking Society of Pediatric Oncology and Hematology.

Gnekow AK, Falkenstein F, von Hornstein S, Zwiener I, Berkefeld S, Bison B, Warmuth-Metz M, Driever PH, Soerensen N, Kortmann RD, Pietsch T, Faldum A
Neuro Oncol 2012 Oct;14(10):1265-84. Epub 2012 Aug 31 doi: 10.1093/neuonc/nos202. PMID: 22942186 Free PMC Article

Successful treatment with a low-dose cisplatin--etoposide regimen for patients with diencephalic syndrome.

Sardi I, Bresci C, Schiavello E, Biassoni V, Fratoni V, Cardellicchio S, Genitori L, Aricò M, Massimino M
J Neurooncol 2012 Sep;109(2):375-83. Epub 2012 Jun 21 doi: 10.1007/s11060-012-0903-7. PMID: 22717669

Initial management of children with hypothalamic and thalamic tumors and the modifying role of neurofibromatosis-1.

Allen JC
Pediatr Neurosurg 2000 Mar;32(3):154-62. doi: 10.1159/000028922. PMID: 10867564

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