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Ovarian Low Grade Endometrioid Stromal Sarcoma

MedGen UID:
276498
Concept ID:
C1518022
Neoplastic Process
Synonyms: Endometrioid Stromal Sarcoma of the Ovary; Low Grade Endometrioid Stromal Sarcoma of the Ovary; Ovarian Endometrioid Stromal Sarcoma

Definition

A rare invasive mesenchymal tumor that arises from the ovary. It is characterized by the absence of marked pleomorphism and nuclear atypia in the neoplastic mesenchymal cells. It may have a favorable clinical outcome. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVOvarian Low Grade Endometrioid Stromal Sarcoma

Professional guidelines

PubMed

Gadducci A, Multinu F, De Vitis LA, Cosio S, Carinelli S, Aletti GD
Gynecol Oncol 2023 Apr;171:95-105. Epub 2023 Feb 24 doi: 10.1016/j.ygyno.2023.02.009. PMID: 36842409
Nagase S, Ohta T, Takahashi F, Yaegashi N; Board members of the 2020 Committee on Gynecologic Oncology of the Japan Society of Obstetrics and Gynecology
J Obstet Gynaecol Res 2021 May;47(5):1631-1642. Epub 2021 Feb 25 doi: 10.1111/jog.14724. PMID: 33631867
Kesic V
Recent Results Cancer Res 2008;178:79-95. doi: 10.1007/978-3-540-71274-9_9. PMID: 18080446

Recent clinical studies

Etiology

Moral AIB, Jiménez JCV, Bañón CM, Díaz Huesca MJ, González MV, López JSJ
BMC Womens Health 2022 Dec 3;22(1):491. doi: 10.1186/s12905-022-02046-9. PMID: 36463169Free PMC Article
Ricotta G, Maulard A, Candiani M, Scherrier S, Genestie C, Pautier P, Leary A, Chargari C, Mangili G, Morice P, Gouy S
Ann Surg Oncol 2022 Sep;29(9):5894-5903. Epub 2022 May 19 doi: 10.1245/s10434-022-11893-7. PMID: 35590116
Dundr P, Cibula D, Foretová L, Macek M Jr, Kopečková K, Petruželka L, Němejcová K, Bártů M, Hojný J, Hájková N, Jakša R, Janega P, Stružinská I
Cesk Patol 2021 Summer;57(2):96-104. PMID: 34275319
Dai Q, Xu B, Wu H, You Y, Wu M, Li L
Orphanet J Rare Dis 2021 Apr 7;16(1):160. doi: 10.1186/s13023-021-01802-8. PMID: 33827628Free PMC Article
Behtash N, Akhavan S, Gilani MM, Mousavi A, Ghaemmaghami F, Mazhari MM
Acta Med Iran 2011;49(9):619-24. PMID: 22052146

Diagnosis

Gadducci A, Multinu F, De Vitis LA, Cosio S, Carinelli S, Aletti GD
Gynecol Oncol 2023 Apr;171:95-105. Epub 2023 Feb 24 doi: 10.1016/j.ygyno.2023.02.009. PMID: 36842409
Moral AIB, Jiménez JCV, Bañón CM, Díaz Huesca MJ, González MV, López JSJ
BMC Womens Health 2022 Dec 3;22(1):491. doi: 10.1186/s12905-022-02046-9. PMID: 36463169Free PMC Article
Kertowidjojo EC, Bennett JA
Surg Pathol Clin 2022 Jun;15(2):315-340. Epub 2022 May 20 doi: 10.1016/j.path.2022.02.008. PMID: 35715164
Jamshidi F, Nielsen TO, Huntsman DG
J Mol Med (Berl) 2015 Apr;93(4):369-81. Epub 2015 Feb 14 doi: 10.1007/s00109-015-1260-8. PMID: 25676695Free PMC Article
Behtash N, Akhavan S, Gilani MM, Mousavi A, Ghaemmaghami F, Mazhari MM
Acta Med Iran 2011;49(9):619-24. PMID: 22052146

Therapy

Kujawa KA, Zembala-Nożyńska E, Cortez AJ, Kujawa T, Kupryjańczyk J, Lisowska KM
Cells 2020 Jan 8;9(1) doi: 10.3390/cells9010149. PMID: 31936272Free PMC Article
Nasioudis D, Ko EM, Kolovos G, Vagios S, Kalliouris D, Giuntoli RL
Int J Gynecol Cancer 2019 Jan;29(1):126-132. doi: 10.1136/ijgc-2018-000063. PMID: 30640694
Guidozzi F
Climacteric 2013 Dec;16(6):611-7. Epub 2013 Aug 16 doi: 10.3109/13697137.2013.806471. PMID: 23952524
Hinds L, Price J
Menopause Int 2010 Jun;16(2):89-93. doi: 10.1258/mi.2010.010018. PMID: 20729501
Gershenson DM
J Natl Cancer Inst Monogr 2005;(34):43-7. doi: 10.1093/jncimonographs/lgi011. PMID: 15784822

Prognosis

Gadducci A, Multinu F, De Vitis LA, Cosio S, Carinelli S, Aletti GD
Gynecol Oncol 2023 Apr;171:95-105. Epub 2023 Feb 24 doi: 10.1016/j.ygyno.2023.02.009. PMID: 36842409
Ricotta G, Maulard A, Candiani M, Scherrier S, Genestie C, Pautier P, Leary A, Chargari C, Mangili G, Morice P, Gouy S
Ann Surg Oncol 2022 Sep;29(9):5894-5903. Epub 2022 May 19 doi: 10.1245/s10434-022-11893-7. PMID: 35590116
Lee JS, Lee D, Lee J, Han MH, Hong DG, Lee HJ
J Med Case Rep 2021 Aug 3;15(1):387. doi: 10.1186/s13256-021-02986-0. PMID: 34340706Free PMC Article
Dai Q, Xu B, Wu H, You Y, Wu M, Li L
Orphanet J Rare Dis 2021 Apr 7;16(1):160. doi: 10.1186/s13023-021-01802-8. PMID: 33827628Free PMC Article
Nasioudis D, Ko EM, Kolovos G, Vagios S, Kalliouris D, Giuntoli RL
Int J Gynecol Cancer 2019 Jan;29(1):126-132. doi: 10.1136/ijgc-2018-000063. PMID: 30640694

Clinical prediction guides

Dai Q, Xu B, Wu H, You Y, Li L
Int J Surg 2024 Apr 1;110(4):1919-1928. doi: 10.1097/JS9.0000000000001146. PMID: 38329091Free PMC Article
Moral AIB, Jiménez JCV, Bañón CM, Díaz Huesca MJ, González MV, López JSJ
BMC Womens Health 2022 Dec 3;22(1):491. doi: 10.1186/s12905-022-02046-9. PMID: 36463169Free PMC Article
Ricotta G, Maulard A, Candiani M, Scherrier S, Genestie C, Pautier P, Leary A, Chargari C, Mangili G, Morice P, Gouy S
Ann Surg Oncol 2022 Sep;29(9):5894-5903. Epub 2022 May 19 doi: 10.1245/s10434-022-11893-7. PMID: 35590116
Nasioudis D, Ko EM, Kolovos G, Vagios S, Kalliouris D, Giuntoli RL
Int J Gynecol Cancer 2019 Jan;29(1):126-132. doi: 10.1136/ijgc-2018-000063. PMID: 30640694
Yoneoka Y, Yoshida H, Ishikawa M, Shimizu H, Uehara T, Murakami T, Kato T
J Gynecol Oncol 2019 Jan;30(1):e7. Epub 2018 Sep 17 doi: 10.3802/jgo.2019.30.e7. PMID: 30479091Free PMC Article

Recent systematic reviews

Jia M, Sun PL, Gao H
Diagn Pathol 2019 Nov 18;14(1):129. doi: 10.1186/s13000-019-0909-y. PMID: 31739799Free PMC Article
Nasioudis D, Ko EM, Kolovos G, Vagios S, Kalliouris D, Giuntoli RL
Int J Gynecol Cancer 2019 Jan;29(1):126-132. doi: 10.1136/ijgc-2018-000063. PMID: 30640694
Blake EA, Sheridan TB, Wang KL, Takiuchi T, Kodama M, Sawada K, Matsuo K
Eur J Obstet Gynecol Reprod Biol 2014 Oct;181:163-70. Epub 2014 Aug 8 doi: 10.1016/j.ejogrb.2014.07.050. PMID: 25150955

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