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Intermediate (Locally Aggressive) Blood Vessel Neoplasm

MedGen UID:
313314
Concept ID:
C1708537
Neoplastic Process

Definition

A borderline blood vessel neoplasm that has locally aggressive behavior. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVIntermediate (Locally Aggressive) Blood Vessel Neoplasm

Professional guidelines

PubMed

Mottet N, van den Bergh RCN, Briers E, Van den Broeck T, Cumberbatch MG, De Santis M, Fanti S, Fossati N, Gandaglia G, Gillessen S, Grivas N, Grummet J, Henry AM, van der Kwast TH, Lam TB, Lardas M, Liew M, Mason MD, Moris L, Oprea-Lager DE, van der Poel HG, Rouvière O, Schoots IG, Tilki D, Wiegel T, Willemse PM, Cornford P
Eur Urol 2021 Feb;79(2):243-262. Epub 2020 Nov 7 doi: 10.1016/j.eururo.2020.09.042. PMID: 33172724
Fahrtash F, McCahon E, Arbuckle S
J Pediatr Hematol Oncol 2010 Aug;32(6):506-10. doi: 10.1097/MPH.0b013e3181e001a9. PMID: 20523249
Abraham JA, Hornicek FJ, Kaufman AM, Harmon DC, Springfield DS, Raskin KA, Mankin HJ, Kirsch DG, Rosenberg AE, Nielsen GP, Desphpande V, Suit HD, DeLaney TF, Yoon SS
Ann Surg Oncol 2007 Jun;14(6):1953-67. Epub 2007 Mar 14 doi: 10.1245/s10434-006-9335-y. PMID: 17356953

Recent clinical studies

Etiology

Mezzacappa FM, Smith FK, Zhang W, Gard A, Cabuk FK, Gonzalez-Gomez I, Monforte HL, Liang J, Singh O, Quezado MM, Aldape KD, Gokden M, Bridge JA, Chen J
Acta Neuropathol Commun 2024 Jan 30;12(1):17. doi: 10.1186/s40478-024-01721-2. PMID: 38291529Free PMC Article
Vagnoni L, Aburas S, Giraffa M, Russo I, Chiarella V, Paolini S, Tini P, Minniti G
Neurosurg Rev 2022 Oct;45(5):3019-3033. Epub 2022 Jun 4 doi: 10.1007/s10143-022-01806-3. PMID: 35665867Free PMC Article
Mottet N, van den Bergh RCN, Briers E, Van den Broeck T, Cumberbatch MG, De Santis M, Fanti S, Fossati N, Gandaglia G, Gillessen S, Grivas N, Grummet J, Henry AM, van der Kwast TH, Lam TB, Lardas M, Liew M, Mason MD, Moris L, Oprea-Lager DE, van der Poel HG, Rouvière O, Schoots IG, Tilki D, Wiegel T, Willemse PM, Cornford P
Eur Urol 2021 Feb;79(2):243-262. Epub 2020 Nov 7 doi: 10.1016/j.eururo.2020.09.042. PMID: 33172724
Pichi F, Neri P, Agarwal A, Invernizzi A, Choudhry N, Amer R, Lembo A, Nucci P, Thompson I, Sen HN, Shields CL
Retina 2020 Sep;40(9):1765-1773. doi: 10.1097/IAE.0000000000002656. PMID: 31584561Free PMC Article
Ferrari A, Orbach D, Sultan I, Casanova M, Bisogno G
Semin Fetal Neonatal Med 2012 Aug;17(4):231-238. Epub 2012 May 25 doi: 10.1016/j.siny.2012.05.003. PMID: 22633289

Diagnosis

Hung YP
Surg Pathol Clin 2021 Dec;14(4):645-663. Epub 2021 Oct 7 doi: 10.1016/j.path.2021.06.007. PMID: 34742485
Mottet N, van den Bergh RCN, Briers E, Van den Broeck T, Cumberbatch MG, De Santis M, Fanti S, Fossati N, Gandaglia G, Gillessen S, Grivas N, Grummet J, Henry AM, van der Kwast TH, Lam TB, Lardas M, Liew M, Mason MD, Moris L, Oprea-Lager DE, van der Poel HG, Rouvière O, Schoots IG, Tilki D, Wiegel T, Willemse PM, Cornford P
Eur Urol 2021 Feb;79(2):243-262. Epub 2020 Nov 7 doi: 10.1016/j.eururo.2020.09.042. PMID: 33172724
Pichi F, Neri P, Agarwal A, Invernizzi A, Choudhry N, Amer R, Lembo A, Nucci P, Thompson I, Sen HN, Shields CL
Retina 2020 Sep;40(9):1765-1773. doi: 10.1097/IAE.0000000000002656. PMID: 31584561Free PMC Article
Ferrari A, Orbach D, Sultan I, Casanova M, Bisogno G
Semin Fetal Neonatal Med 2012 Aug;17(4):231-238. Epub 2012 May 25 doi: 10.1016/j.siny.2012.05.003. PMID: 22633289
Bruder E, Alaggio R, Kozakewich HP, Jundt G, Dehner LP, Coffin CM
Pediatr Dev Pathol 2012;15(1 Suppl):26-61. doi: 10.2350/11-11-1119-PB.1. PMID: 22420724

Therapy

Vagnoni L, Aburas S, Giraffa M, Russo I, Chiarella V, Paolini S, Tini P, Minniti G
Neurosurg Rev 2022 Oct;45(5):3019-3033. Epub 2022 Jun 4 doi: 10.1007/s10143-022-01806-3. PMID: 35665867Free PMC Article
Tang L, Chen G, Wang Q, John J, Lu C
Medicine (Baltimore) 2019 Nov;98(48):e18161. doi: 10.1097/MD.0000000000018161. PMID: 31770261Free PMC Article
Lai Q, Feys E, Karam V, Adam R, Klempnauer J, Oliverius M, Mazzaferro V, Pascher A, Remiszewski P, Isoniemi H, Pirenne J, Foss A, Ericzon BG, Markovic S, Lerut JP; European Liver Intestine Transplant Association (ELITA)
Transplantation 2017 Mar;101(3):555-564. doi: 10.1097/TP.0000000000001603. PMID: 28212256
Ravi V, Patel S
Curr Oncol Rep 2013 Aug;15(4):347-55. doi: 10.1007/s11912-013-0328-2. PMID: 23852636
Carew JF, Singh B, Kraus DH
Laryngoscope 1999 Sep;109(9):1409-11. doi: 10.1097/00005537-199909000-00009. PMID: 10499045

Prognosis

Mezzacappa FM, Smith FK, Zhang W, Gard A, Cabuk FK, Gonzalez-Gomez I, Monforte HL, Liang J, Singh O, Quezado MM, Aldape KD, Gokden M, Bridge JA, Chen J
Acta Neuropathol Commun 2024 Jan 30;12(1):17. doi: 10.1186/s40478-024-01721-2. PMID: 38291529Free PMC Article
Youngblood MW, Miyagishima DF, Jin L, Gupte T, Li C, Duran D, Montejo JD, Zhao A, Sheth A, Tyrtova E, Özduman K, Iacoangeli F, Peyre M, Boetto J, Pease M, Avşar T, Huttner A, Bilguvar K, Kilic T, Pamir MN, Amankulor N, Kalamarides M, Erson-Omay EZ, Günel M, Moliterno J
Neuro Oncol 2021 May 5;23(5):783-794. doi: 10.1093/neuonc/noaa226. PMID: 33068421Free PMC Article
Colmenero I, Hoeger PH
Br J Dermatol 2014 Sep;171(3):474-84. Epub 2014 Jun 25 doi: 10.1111/bjd.12835. PMID: 24965196
Ravi V, Patel S
Curr Oncol Rep 2013 Aug;15(4):347-55. doi: 10.1007/s11912-013-0328-2. PMID: 23852636
Ferrari A, Orbach D, Sultan I, Casanova M, Bisogno G
Semin Fetal Neonatal Med 2012 Aug;17(4):231-238. Epub 2012 May 25 doi: 10.1016/j.siny.2012.05.003. PMID: 22633289

Clinical prediction guides

Vagnoni L, Aburas S, Giraffa M, Russo I, Chiarella V, Paolini S, Tini P, Minniti G
Neurosurg Rev 2022 Oct;45(5):3019-3033. Epub 2022 Jun 4 doi: 10.1007/s10143-022-01806-3. PMID: 35665867Free PMC Article
Hassani M, Jung S, Garzia L, Ghodsi E, Alcindor T, Turcotte RE
Ann Surg Oncol 2021 Oct;28(11):6861-6867. Epub 2021 Jan 29 doi: 10.1245/s10434-021-09592-w. PMID: 33512676
Youngblood MW, Miyagishima DF, Jin L, Gupte T, Li C, Duran D, Montejo JD, Zhao A, Sheth A, Tyrtova E, Özduman K, Iacoangeli F, Peyre M, Boetto J, Pease M, Avşar T, Huttner A, Bilguvar K, Kilic T, Pamir MN, Amankulor N, Kalamarides M, Erson-Omay EZ, Günel M, Moliterno J
Neuro Oncol 2021 May 5;23(5):783-794. doi: 10.1093/neuonc/noaa226. PMID: 33068421Free PMC Article
Ravi V, Patel S
Curr Oncol Rep 2013 Aug;15(4):347-55. doi: 10.1007/s11912-013-0328-2. PMID: 23852636
Abraham JA, Hornicek FJ, Kaufman AM, Harmon DC, Springfield DS, Raskin KA, Mankin HJ, Kirsch DG, Rosenberg AE, Nielsen GP, Desphpande V, Suit HD, DeLaney TF, Yoon SS
Ann Surg Oncol 2007 Jun;14(6):1953-67. Epub 2007 Mar 14 doi: 10.1245/s10434-006-9335-y. PMID: 17356953

Recent systematic reviews

Mottet N, van den Bergh RCN, Briers E, Van den Broeck T, Cumberbatch MG, De Santis M, Fanti S, Fossati N, Gandaglia G, Gillessen S, Grivas N, Grummet J, Henry AM, van der Kwast TH, Lam TB, Lardas M, Liew M, Mason MD, Moris L, Oprea-Lager DE, van der Poel HG, Rouvière O, Schoots IG, Tilki D, Wiegel T, Willemse PM, Cornford P
Eur Urol 2021 Feb;79(2):243-262. Epub 2020 Nov 7 doi: 10.1016/j.eururo.2020.09.042. PMID: 33172724

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