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Sclerosing Epithelioid Fibrosarcoma

MedGen UID:
313689
Concept ID:
C1710026
Neoplastic Process
Synonym: Sclerosing epithelioid fibrosarcoma
SNOMED CT: Sclerosing epithelioid fibrosarcoma (703618009)

Definition

A well-circumscribed malignant fibroblastic neoplasm that usually arises from the soft tissue. It is characterized by the presence of nests of malignant epithelioid fibroblasts and sclerotic collagen stroma formation. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVSclerosing Epithelioid Fibrosarcoma

Professional guidelines

PubMed

Martínez-Trufero J, Cruz Jurado J, Gómez-Mateo MC, Bernabeu D, Floría LJ, Lavernia J, Sebio A, García Del Muro X, Álvarez R, Correa R, Hernández-León CN, Marquina G, Hindi N, Redondo A, Martínez V, Asencio JM, Mata C, Valverde Morales CM, Martin-Broto J
Cancer Treat Rev 2021 Sep;99:102259. Epub 2021 Jul 11 doi: 10.1016/j.ctrv.2021.102259. PMID: 34311246
Arbajian E, Puls F, Antonescu CR, Amary F, Sciot R, Debiec-Rychter M, Sumathi VP, Järås M, Magnusson L, Nilsson J, Hofvander J, Mertens F
Clin Cancer Res 2017 Dec 1;23(23):7426-7434. Epub 2017 Sep 22 doi: 10.1158/1078-0432.CCR-17-1856. PMID: 28939748
Eyden BP, Manson C, Banerjee SS, Roberts IS, Harris M
Histopathology 1998 Oct;33(4):354-60. doi: 10.1046/j.1365-2559.1998.00530.x. PMID: 9822926

Recent clinical studies

Etiology

Kosemehmetoglu K, Ardic F, Kilpatrick SE, Aydingoz U, Sumathi VP, Michal M
Virchows Arch 2021 Apr;478(4):767-777. Epub 2020 Oct 21 doi: 10.1007/s00428-020-02953-y. PMID: 33084978
Yahyaoui M, Benhammou M, Aharram S, Amghar J, Sadougui M, Agoumi O, Daoudi A
Pan Afr Med J 2020;36:131. Epub 2020 Jun 25 doi: 10.11604/pamj.2020.36.131.18668. PMID: 32849986Free PMC Article
Porteus C, Gan Q, Gong Y, Pantanowitz L, Henderson-Jackson E, Saeed-Vafa D, Mela N, Peterson D, Ahmad N, Ahmed A, Bui M
J Am Soc Cytopathol 2020 Nov-Dec;9(6):513-519. Epub 2020 Jun 5 doi: 10.1016/j.jasc.2020.05.005. PMID: 32624384
Agaimy A
Virchows Arch 2020 Jan;476(1):81-96. Epub 2019 Nov 4 doi: 10.1007/s00428-019-02677-8. PMID: 31686193
Chew W, Benson C, Thway K, Hayes A, Miah A, Zaidi S, Lee ATJ, Messiou C, Fisher C, van der Graaf WT, Jones RL
Med Oncol 2018 Sep 5;35(11):138. doi: 10.1007/s12032-018-1192-6. PMID: 30187231Free PMC Article

Diagnosis

Warmke LM, Yu W, Meis JM
Surg Pathol Clin 2024 Mar;17(1):119-139. Epub 2023 Aug 5 doi: 10.1016/j.path.2023.06.009. PMID: 38278601
Yahyaoui M, Benhammou M, Aharram S, Amghar J, Sadougui M, Agoumi O, Daoudi A
Pan Afr Med J 2020;36:131. Epub 2020 Jun 25 doi: 10.11604/pamj.2020.36.131.18668. PMID: 32849986Free PMC Article
Flaman AN, Wasserman JK, Gravel DH, Purgina BM
Head Neck Pathol 2018 Sep;12(3):392-406. Epub 2018 Aug 1 doi: 10.1007/s12105-018-0891-9. PMID: 30069839Free PMC Article
Patterson JW, Tchernev G, Chokoeva AA, Wick MR
Wien Med Wochenschr 2017 Apr;167(5-6):120-123. Epub 2016 Sep 15 doi: 10.1007/s10354-016-0509-3. PMID: 27631873
Folpe AL
Histopathology 2014 Jan;64(1):12-25. Epub 2013 Nov 22 doi: 10.1111/his.12282. PMID: 24266941

Therapy

Doshi SD, Oza J, Remotti H, Remotti F, Moy MP, Schwartz GK, Ingham M
JCO Precis Oncol 2021 Nov;5:1-5. doi: 10.1200/PO.20.00201. PMID: 34994591
Tariq MU, Umer M, Khan Z, Saeed J, Siddiqui MA, Din NU
Ann Diagn Pathol 2020 Apr;45:151479. Epub 2020 Feb 14 doi: 10.1016/j.anndiagpath.2020.151479. PMID: 32088577
Pipola V, Boriani S, Ghermandi R, Tedesco G, Evangelisti G, Girolami M, Ricci A, Gasbarrini A
J Clin Neurosci 2020 Feb;72:429-433. Epub 2019 Dec 27 doi: 10.1016/j.jocn.2019.12.035. PMID: 31889641
Chew W, Benson C, Thway K, Hayes A, Miah A, Zaidi S, Lee ATJ, Messiou C, Fisher C, van der Graaf WT, Jones RL
Med Oncol 2018 Sep 5;35(11):138. doi: 10.1007/s12032-018-1192-6. PMID: 30187231Free PMC Article
Massier A, Scheithauer BW, Taylor HC, Clark C, Llerena L
Endocr Pathol 2007 Winter;18(4):233-8. doi: 10.1007/s12022-007-9010-2. PMID: 18097772

Prognosis

Kosemehmetoglu K, Ardic F, Kilpatrick SE, Aydingoz U, Sumathi VP, Michal M
Virchows Arch 2021 Apr;478(4):767-777. Epub 2020 Oct 21 doi: 10.1007/s00428-020-02953-y. PMID: 33084978
Warmke LM, Meis JM
Am J Surg Pathol 2021 Mar 1;45(3):317-328. doi: 10.1097/PAS.0000000000001559. PMID: 32769431
Yahyaoui M, Benhammou M, Aharram S, Amghar J, Sadougui M, Agoumi O, Daoudi A
Pan Afr Med J 2020;36:131. Epub 2020 Jun 25 doi: 10.11604/pamj.2020.36.131.18668. PMID: 32849986Free PMC Article
Porteus C, Gan Q, Gong Y, Pantanowitz L, Henderson-Jackson E, Saeed-Vafa D, Mela N, Peterson D, Ahmad N, Ahmed A, Bui M
J Am Soc Cytopathol 2020 Nov-Dec;9(6):513-519. Epub 2020 Jun 5 doi: 10.1016/j.jasc.2020.05.005. PMID: 32624384
Chew W, Benson C, Thway K, Hayes A, Miah A, Zaidi S, Lee ATJ, Messiou C, Fisher C, van der Graaf WT, Jones RL
Med Oncol 2018 Sep 5;35(11):138. doi: 10.1007/s12032-018-1192-6. PMID: 30187231Free PMC Article

Clinical prediction guides

Blay JY, Tlemsani C, Toulmonde M, Italiano A, Rios M, Bompas E, Valentin T, Duffaud F, Le Nail LR, Watson S, Firmin N, Dubray-Longeras P, Ropars M, Perrin C, Hervieu A, Lebbe C, Saada-Bouzid E, Soibinet P, Fiorenza F, Bertucci F, Boudou P, Vaz G, Bonvalot S, Honoré C, Marec-Berard P, Minard V, Cleirec M, Biau D, Meeus P, Babinet A, Dumaine V, Carriere S, Fau M, Decanter G, Gouin F, Ngo C, Le Loarer F, Karanian M, Meurgey A, Dufresne A, Brahmi M, Chemin-Airiau C, Ducimetiere F, Penel N, Le Cesne A; NETSARC/REPPS/RESOS and French Sarcoma Group- Groupe d′Etude des Tumeurs Osseuses (GSF-GETO) networks
Eur J Cancer 2024 Jan;196:113454. Epub 2023 Nov 23 doi: 10.1016/j.ejca.2023.113454. PMID: 38008029
Peng Y, Zhang D, Lei T, Xie J, Wu C, Wang H, Shi Y, Li Q, Wang J
Pathology 2023 Apr;55(3):355-361. Epub 2022 Dec 21 doi: 10.1016/j.pathol.2022.10.005. PMID: 36690575
Woods AD, Purohit R, Mitchell LC, Collier JR, Collier KA, Lathara M, Learned K, Vaske O, Geiger H, Wrzeszczynski KO, Jobanputra V, Srinivasa G, Rudzinski ER, Whelan K, Beierle E, Spunt SL, Keller C, Wadhwa A
Cold Spring Harb Mol Case Stud 2021 Oct;7(5) Epub 2021 Oct 19 doi: 10.1101/mcs.a006093. PMID: 34362827Free PMC Article
Forgó E, Hornick JL, Charville GW
Histopathology 2021 May;78(6):905-908. Epub 2021 Mar 16 doi: 10.1111/his.14321. PMID: 33368602Free PMC Article
Kosemehmetoglu K, Ardic F, Kilpatrick SE, Aydingoz U, Sumathi VP, Michal M
Virchows Arch 2021 Apr;478(4):767-777. Epub 2020 Oct 21 doi: 10.1007/s00428-020-02953-y. PMID: 33084978

Recent systematic reviews

Ossendorf C, Studer GM, Bode B, Fuchs B
Clin Orthop Relat Res 2008 Jun;466(6):1485-91. Epub 2008 Mar 14 doi: 10.1007/s11999-008-0205-8. PMID: 18340502Free PMC Article

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