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Natal teeth-intestinal pseudoobstruction-patent ductus syndrome

MedGen UID:
340945
Concept ID:
C1855732
Disease or Syndrome
Synonyms: Intestinal Pseudoobstruction with Patent Ductus Arteriosus and Natal Teeth; Natal teeth, intestinal pseudoobstruction and patent ductus
 
Monarch Initiative: MONDO:0009467
OMIM®: 243185

Clinical features

From HPO
Natal tooth
MedGen UID:
10268
Concept ID:
C0027443
Finding
A tooth present at birth or erupting within the first month of life.

Professional guidelines

PubMed

Lee WY, Yum SK, Seo YM, Kim S, Shin JA, Lee C
Eur J Cardiothorac Surg 2024 May 3;65(5) doi: 10.1093/ejcts/ezae175. PMID: 38724226

Recent clinical studies

Etiology

Lee WY, Yum SK, Seo YM, Kim S, Shin JA, Lee C
Eur J Cardiothorac Surg 2024 May 3;65(5) doi: 10.1093/ejcts/ezae175. PMID: 38724226
Faria RM, Pacheco JT, Oliveira IR, Vidal JM, Rodrigues AB Junior, Costa ALL, Nina VJDS, Cascudo MM
Braz J Cardiovasc Surg 2017 May-Jun;32(3):210-214. doi: 10.21470/1678-9741-2017-0058. PMID: 28832800Free PMC Article
van den Boom J, Battin M, Hornung T
J Paediatr Child Health 2010 Mar;46(3):76-9. Epub 2010 Jan 26 doi: 10.1111/j.1440-1754.2009.01641.x. PMID: 20105260
Dufourq N, Thomson M, Adhikari M, Moodley J
S Afr Med J 2004 Apr;94(4):299-302. PMID: 15150947

Diagnosis

Ferreira de Souza LM, Galvão E Brito Medeiros A, Júnior JPR, de Melo AN, Dias SAMM
Medicina (Kaunas) 2019 Jul 8;55(7) doi: 10.3390/medicina55070352. PMID: 31288482Free PMC Article
Bellettini CV, Wagner R, Sette Balzanelo A, de Souza Andretta AL, Nascimento de Moura A, Fabris CC, Maranhão Gubert E
Rev Paul Pediatr 2016 Sep;34(3):384-7. Epub 2016 Apr 8 doi: 10.1016/j.rpped.2016.03.003. PMID: 27133713Free PMC Article
Dufourq N, Thomson M, Adhikari M, Moodley J
S Afr Med J 2004 Apr;94(4):299-302. PMID: 15150947

Therapy

Lee WY, Yum SK, Seo YM, Kim S, Shin JA, Lee C
Eur J Cardiothorac Surg 2024 May 3;65(5) doi: 10.1093/ejcts/ezae175. PMID: 38724226

Prognosis

Ferreira de Souza LM, Galvão E Brito Medeiros A, Júnior JPR, de Melo AN, Dias SAMM
Medicina (Kaunas) 2019 Jul 8;55(7) doi: 10.3390/medicina55070352. PMID: 31288482Free PMC Article
Dufourq N, Thomson M, Adhikari M, Moodley J
S Afr Med J 2004 Apr;94(4):299-302. PMID: 15150947

Clinical prediction guides

Lee WY, Yum SK, Seo YM, Kim S, Shin JA, Lee C
Eur J Cardiothorac Surg 2024 May 3;65(5) doi: 10.1093/ejcts/ezae175. PMID: 38724226
Sevely A, Fries F, Regnier C, Manelfe C
J Neuroradiol 1991;18(4):340-50. PMID: 1804937

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