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Renal lymphangiectasia

MedGen UID:
344661
Concept ID:
C1856132
Finding
Synonyms: Hygroma renale; Peripelvic lymphangiectasia; Renal lymphangiomatosis
 
HPO: HP:6000073

Definition

A developmental anomaly of renal lymphatics that results from a failure of the lymphatics to make communication with the rest of the lymph trunks. The abnormal lymphatics thus dilate and form cystic spaces at the renal sinus and in the perinephric space. [from HPO]

Term Hierarchy

Recent clinical studies

Etiology

Ueda S, Yanagida H, Sugimoto K, Fujita S, Yagi K, Okada M, Takemura T
Clin Nephrol 2007 Dec;68(6):416-21. doi: 10.5414/cnp68416. PMID: 18184526
Simonton SC, Saltzman DA, Brennom W, Pergament M, Drake G, Sinaiko A, Priest JR
Pediatr Pathol Lab Med 1997 Mar-Apr;17(2):293-301. PMID: 9086536

Diagnosis

Alshanafey S, Alkhani A, Alkibsib A
Ann Saudi Med 2022 Mar-Apr;42(2):139-144. Epub 2022 Apr 7 doi: 10.5144/0256-4947.2022.139. PMID: 35380057Free PMC Article
Desai SB, Sun RC, Johnson BL, Rialon KL, Iacobas I, Kukreja KU, Schady DA, Phung T, Sanvitha S, Naik-Mathuria BJ
Lymphat Res Biol 2020 Dec;18(6):572-578. Epub 2020 Jun 24 doi: 10.1089/lrb.2020.0004. PMID: 32589505
Pandya VK, Sutariya HC, Gandhi SP, Khemchandani SI, Patel HV, Shah MK
Ren Fail 2017 Nov;39(1):533-539. doi: 10.1080/0886022X.2017.1337584. PMID: 28639460Free PMC Article
Chen Z, Qi L, Tang Z, Hu Z, Fan B
Scand J Urol Nephrol 2009;43(5):428-30. doi: 10.3109/00365590902930857. PMID: 19921991
Ashraf K, Raza SS, Ashraf O, Memon W, Memon A, Zubairi TA
Br J Radiol 2007 Jun;80(954):e117-8. doi: 10.1259/bjr/16931054. PMID: 17684071

Therapy

Dawidek MT, Aquil S, Alogaili R, Gabril M, Moussa M, Sener A, Luke PP
Transplantation 2020 Jan;104(1):172-175. doi: 10.1097/TP.0000000000002745. PMID: 30964839
Pandya VK, Sutariya HC, Gandhi SP, Khemchandani SI, Patel HV, Shah MK
Ren Fail 2017 Nov;39(1):533-539. doi: 10.1080/0886022X.2017.1337584. PMID: 28639460Free PMC Article
Ashraf K, Raza SS, Ashraf O, Memon W, Memon A, Zubairi TA
Br J Radiol 2007 Jun;80(954):e117-8. doi: 10.1259/bjr/16931054. PMID: 17684071

Prognosis

Alzahrani AM, Khamis AA, Barakat AE, Alotaibi K
Am J Case Rep 2021 Nov 8;22:e933934. doi: 10.12659/AJCR.933934. PMID: 34748529Free PMC Article
Desai SB, Sun RC, Johnson BL, Rialon KL, Iacobas I, Kukreja KU, Schady DA, Phung T, Sanvitha S, Naik-Mathuria BJ
Lymphat Res Biol 2020 Dec;18(6):572-578. Epub 2020 Jun 24 doi: 10.1089/lrb.2020.0004. PMID: 32589505
Ueda S, Yanagida H, Sugimoto K, Fujita S, Yagi K, Okada M, Takemura T
Clin Nephrol 2007 Dec;68(6):416-21. doi: 10.5414/cnp68416. PMID: 18184526
Ashraf K, Raza SS, Ashraf O, Memon W, Memon A, Zubairi TA
Br J Radiol 2007 Jun;80(954):e117-8. doi: 10.1259/bjr/16931054. PMID: 17684071

Clinical prediction guides

Ueda S, Yanagida H, Sugimoto K, Fujita S, Yagi K, Okada M, Takemura T
Clin Nephrol 2007 Dec;68(6):416-21. doi: 10.5414/cnp68416. PMID: 18184526
Ashraf K, Raza SS, Ashraf O, Memon W, Memon A, Zubairi TA
Br J Radiol 2007 Jun;80(954):e117-8. doi: 10.1259/bjr/16931054. PMID: 17684071

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