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Vulvar keratinizing squamous cell carcinoma

MedGen UID:
378346
Concept ID:
C2109334
Neoplastic Process
Synonyms: Vulvar Keratinizing Squamous Cell Carcinoma; vulvar keratinizing squamous cell carcinoma
 
Monarch Initiative: MONDO:0004199

Definition

A squamous cell carcinoma that arises from the vulva and is characterized by the presence of keratin pearls. [from NCI]

Professional guidelines

PubMed

Heller DS, Day T, Allbritton JI, Scurry J, Radici G, Welch K, Preti M; ISSVD Difficult Pathologic Diagnoses Committee
J Low Genit Tract Dis 2021 Jan 1;25(1):57-70. doi: 10.1097/LGT.0000000000000572. PMID: 33105449Free PMC Article
Charkviani LI, Chkuaseli GT
Eur J Gynaecol Oncol 1988;9(1):5-9. PMID: 3345785
Krupp PJ, Lee FY, Bohm JW, Batson HW, Diem JE, Lemire JE
Obstet Gynecol 1975 Jul;46(1):84-8. doi: 10.1097/00006250-197507000-00016. PMID: 1153141

Recent clinical studies

Etiology

Nguyen TQ, Hamada A, Yamada K, Higaki M, Shintani T, Yoshioka Y, Toratani S, Okamoto T
In Vitro Cell Dev Biol Anim 2021 Mar;57(3):300-314. Epub 2021 Feb 3 doi: 10.1007/s11626-020-00542-6. PMID: 33537930
Milliken S, May J, Sanderson PA, Congiu MA, D'Oria O, Golia D'Augè T, Caruso G, DI Donato V, Benedetti Panici P, Giannini A
Minerva Obstet Gynecol 2021 Apr;73(2):160-165. Epub 2020 Dec 11 doi: 10.23736/S2724-606X.20.04743-7. PMID: 33306289
Heller DS, Day T, Allbritton JI, Scurry J, Radici G, Welch K, Preti M; ISSVD Difficult Pathologic Diagnoses Committee
J Low Genit Tract Dis 2021 Jan 1;25(1):57-70. doi: 10.1097/LGT.0000000000000572. PMID: 33105449Free PMC Article
Jenkins TM, Mills AM
Semin Diagn Pathol 2021 Jan;38(1):27-36. Epub 2020 Sep 6 doi: 10.1053/j.semdp.2020.09.006. PMID: 32948383
Day T, Marzol A, Pagano R, Jaaback K, Scurry J
J Low Genit Tract Dis 2020 Oct;24(4):392-398. doi: 10.1097/LGT.0000000000000569. PMID: 32976294Free PMC Article

Diagnosis

Heller DS, Day T, Allbritton JI, Scurry J, Radici G, Welch K, Preti M; ISSVD Difficult Pathologic Diagnoses Committee
J Low Genit Tract Dis 2021 Jan 1;25(1):57-70. doi: 10.1097/LGT.0000000000000572. PMID: 33105449Free PMC Article
Jenkins TM, Mills AM
Semin Diagn Pathol 2021 Jan;38(1):27-36. Epub 2020 Sep 6 doi: 10.1053/j.semdp.2020.09.006. PMID: 32948383
Day T, Marzol A, Pagano R, Jaaback K, Scurry J
J Low Genit Tract Dis 2020 Oct;24(4):392-398. doi: 10.1097/LGT.0000000000000569. PMID: 32976294Free PMC Article
Rakislova N, Saco A, Sierra A, Del Pino M, Ordi J
Adv Anat Pathol 2017 Jul;24(4):201-214. doi: 10.1097/PAP.0000000000000155. PMID: 28590952
Ozkan F, Bilgiç R, Cesur S
APMIS 2006 Jul-Aug;114(7-8):562-5. doi: 10.1111/j.1600-0463.2006.apm_326.x. PMID: 16907863

Therapy

Kortekaas KE, Santegoets SJ, Abdulrahman Z, van Ham VJ, van der Tol M, Ehsan I, van Doorn HC, Bosse T, van Poelgeest MIE, van der Burg SH
J Immunother Cancer 2019 Sep 3;7(1):236. doi: 10.1186/s40425-019-0712-z. PMID: 31481117Free PMC Article
Fiset PO, Wou K, Arseneau J, Gilbert L
J Low Genit Tract Dis 2014 Jul;18(3):e74-9. doi: 10.1097/LGT.0b013e3182a82115. PMID: 24556613
Sun Y, Hildesheim A, Brinton LA, Nasca PC, Trimble CL, Kurman RJ, Viscidi RP, Shah KV
Gynecol Oncol 1996 Nov;63(2):200-3. doi: 10.1006/gyno.1996.0306. PMID: 8910627
Dixon RS, Mikhail GR
J Am Acad Dermatol 1981 Feb;4(2):160-5. doi: 10.1016/s0190-9622(81)70019-7. PMID: 7217386
Choo YC, Morley GW
Gynecol Oncol 1980 Jun;9(3):324-33. doi: 10.1016/0090-8258(80)90044-x. PMID: 6991376

Prognosis

Stolnicu S, Allison D, Praiss AM, Tessier-Cloutier B, Momeni Boroujeni A, Flynn J, Iasonos A, Serrette R, Hoang L, Patrichi A, Terinte C, Pesci A, Mateoiu C, Lastra RR, Kiyokawa T, Ali-Fehmi R, Kheil M, Oliva E, Devins KM, Abu-Rustum NR, Soslow RA
Am J Surg Pathol 2023 Dec 1;47(12):1376-1389. Epub 2023 Sep 13 doi: 10.1097/PAS.0000000000002122. PMID: 37702216Free PMC Article
Milliken S, May J, Sanderson PA, Congiu MA, D'Oria O, Golia D'Augè T, Caruso G, DI Donato V, Benedetti Panici P, Giannini A
Minerva Obstet Gynecol 2021 Apr;73(2):160-165. Epub 2020 Dec 11 doi: 10.23736/S2724-606X.20.04743-7. PMID: 33306289
Jenkins TM, Mills AM
Semin Diagn Pathol 2021 Jan;38(1):27-36. Epub 2020 Sep 6 doi: 10.1053/j.semdp.2020.09.006. PMID: 32948383
Rakislova N, Saco A, Sierra A, Del Pino M, Ordi J
Adv Anat Pathol 2017 Jul;24(4):201-214. doi: 10.1097/PAP.0000000000000155. PMID: 28590952
Del Pino M, Rodriguez-Carunchio L, Ordi J
Histopathology 2013 Jan;62(1):161-75. Epub 2012 Nov 27 doi: 10.1111/his.12034. PMID: 23190170

Clinical prediction guides

Stolnicu S, Allison D, Praiss AM, Tessier-Cloutier B, Momeni Boroujeni A, Flynn J, Iasonos A, Serrette R, Hoang L, Patrichi A, Terinte C, Pesci A, Mateoiu C, Lastra RR, Kiyokawa T, Ali-Fehmi R, Kheil M, Oliva E, Devins KM, Abu-Rustum NR, Soslow RA
Am J Surg Pathol 2023 Dec 1;47(12):1376-1389. Epub 2023 Sep 13 doi: 10.1097/PAS.0000000000002122. PMID: 37702216Free PMC Article
Wanka G, Jueckstock J, Wild CM, Vattai A, Fürst S, Heidegger HH, Kuhn C, Schmoeckel E, Jeschke U, Dannecker C
J Cancer Res Clin Oncol 2023 Aug;149(9):6191-6201. Epub 2023 Jan 23 doi: 10.1007/s00432-023-04579-4. PMID: 36689059Free PMC Article
Kim E, Chung M, Jeong HS, Baek CH, Cho J
Hum Pathol 2022 Aug;126:45-54. Epub 2022 May 18 doi: 10.1016/j.humpath.2022.05.010. PMID: 35597368
Milliken S, May J, Sanderson PA, Congiu MA, D'Oria O, Golia D'Augè T, Caruso G, DI Donato V, Benedetti Panici P, Giannini A
Minerva Obstet Gynecol 2021 Apr;73(2):160-165. Epub 2020 Dec 11 doi: 10.23736/S2724-606X.20.04743-7. PMID: 33306289
Day T, Marzol A, Pagano R, Jaaback K, Scurry J
J Low Genit Tract Dis 2020 Oct;24(4):392-398. doi: 10.1097/LGT.0000000000000569. PMID: 32976294Free PMC Article

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