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Pediatric-Type Follicular Lymphoma

MedGen UID:
437600
Concept ID:
C2698750
Neoplastic Process
Synonym: Pediatric follicular lymphoma
SNOMED CT: Pediatric follicular lymphoma (733917002); Pediatric follicular lymphoma (736322001)

Definition

A nodal follicular lymphoma with favorable prognosis. It lacks BCL-2 rearrangement and 14;18 translocation. Nearly all cases are localized. It is usually seen in the pediatric population but similar lymphomas may occur in adults. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVPediatric-Type Follicular Lymphoma

Recent clinical studies

Etiology

Yerigeri K, Buhtoiarov I
World J Gastroenterol 2023 Nov 21;29(43):5865-5871. doi: 10.3748/wjg.v29.i43.5865. PMID: 38074918Free PMC Article
Lim S, Lim KY, Koh J, Bae JM, Yun H, Lee C, Kim YA, Paik JH, Jeon YK
Am J Surg Pathol 2022 Oct 1;46(10):1397-1406. Epub 2022 Jul 14 doi: 10.1097/PAS.0000000000001932. PMID: 35834399Free PMC Article
Schmidt J, Gong S, Marafioti T, Mankel B, Gonzalez-Farre B, Balagué O, Mozos A, Cabeçadas J, van der Walt J, Hoehn D, Rosenwald A, Ott G, Dojcinov S, Egan C, Nadeu F, Ramis-Zaldívar JE, Clot G, Bárcena C, Pérez-Alonso V, Endris V, Penzel R, Lome-Maldonado C, Bonzheim I, Fend F, Campo E, Jaffe ES, Salaverria I, Quintanilla-Martinez L
Blood 2016 Aug 25;128(8):1101-11. Epub 2016 Jun 2 doi: 10.1182/blood-2016-03-703819. PMID: 27257180Free PMC Article

Diagnosis

Laurent C, Cook JR, Yoshino T, Quintanilla-Martinez L, Jaffe ES
Virchows Arch 2023 Jan;482(1):149-162. Epub 2022 Nov 17 doi: 10.1007/s00428-022-03432-2. PMID: 36394631Free PMC Article
Lim S, Lim KY, Koh J, Bae JM, Yun H, Lee C, Kim YA, Paik JH, Jeon YK
Am J Surg Pathol 2022 Oct 1;46(10):1397-1406. Epub 2022 Jul 14 doi: 10.1097/PAS.0000000000001932. PMID: 35834399Free PMC Article
Auerbach A, Schmieg JJ, Aguilera NS
Head Neck Pathol 2021 Mar;15(1):41-58. Epub 2021 Mar 15 doi: 10.1007/s12105-020-01257-6. PMID: 33723759Free PMC Article
Okudolo JO, Bagg A, Meghpara BB, Sieber MR, Eagle RC Jr, Milman T
Ophthalmic Plast Reconstr Surg 2020 Mar/Apr;36(2):e46-e49. doi: 10.1097/IOP.0000000000001556. PMID: 31868792
Agostinelli C, Akarca AU, Ramsay A, Rizvi H, Rodriguez-Justo M, Pomplun S, Proctor I, Sabattini E, Linch D, Daw S, Pittaluga S, Pileri SA, Jaffe ES, Quintanilla-Martinez L, Marafioti T
Virchows Arch 2019 Dec;475(6):771-779. Epub 2019 Nov 4 doi: 10.1007/s00428-019-02681-y. PMID: 31686194Free PMC Article

Therapy

Yerigeri K, Buhtoiarov I
World J Gastroenterol 2023 Nov 21;29(43):5865-5871. doi: 10.3748/wjg.v29.i43.5865. PMID: 38074918Free PMC Article
Yamaguchi J, Kato S, Iwata E, Aoki K, Kabeya R, Natsume A, Wakabayashi T
World Neurosurg 2018 Jul;115:176-180. Epub 2018 Apr 17 doi: 10.1016/j.wneu.2018.04.053. PMID: 29678710

Prognosis

Barroca H, Marques C, Soares MJ, Carvalhais I
Diagn Cytopathol 2021 Dec;49(12):E453-E457. Epub 2021 Aug 18 doi: 10.1002/dc.24854. PMID: 34406712
Zhang H, Sun S, Zhang B, Yang H
Medicine (Baltimore) 2019 Oct;98(41):e17567. doi: 10.1097/MD.0000000000017567. PMID: 31593142Free PMC Article
Woessmann W, Quintanilla-Martinez L
Hematol Oncol 2019 Jun;37 Suppl 1:53-61. doi: 10.1002/hon.2585. PMID: 31187530
Kanaan C, Burroni B
Blood 2018 Oct 18;132(16):1725. doi: 10.1182/blood-2018-07-862524. PMID: 30337322
Koo M, Ohgami RS
Adv Anat Pathol 2017 May;24(3):128-135. doi: 10.1097/PAP.0000000000000144. PMID: 28277421

Clinical prediction guides

Kumar J, Alspach AE, Zucker JP, Gratzinger D
Am J Clin Pathol 2022 Nov 3;158(5):564-569. doi: 10.1093/ajcp/aqac104. PMID: 36048893
Lim S, Lim KY, Koh J, Bae JM, Yun H, Lee C, Kim YA, Paik JH, Jeon YK
Am J Surg Pathol 2022 Oct 1;46(10):1397-1406. Epub 2022 Jul 14 doi: 10.1097/PAS.0000000000001932. PMID: 35834399Free PMC Article
Agostinelli C, Akarca AU, Ramsay A, Rizvi H, Rodriguez-Justo M, Pomplun S, Proctor I, Sabattini E, Linch D, Daw S, Pittaluga S, Pileri SA, Jaffe ES, Quintanilla-Martinez L, Marafioti T
Virchows Arch 2019 Dec;475(6):771-779. Epub 2019 Nov 4 doi: 10.1007/s00428-019-02681-y. PMID: 31686194Free PMC Article
Ozawa MG, Bhaduri A, Chisholm KM, Baker SA, Ma L, Zehnder JL, Luna-Fineman S, Link MP, Merker JD, Arber DA, Ohgami RS
Mod Pathol 2016 Oct;29(10):1212-20. Epub 2016 Jun 24 doi: 10.1038/modpathol.2016.102. PMID: 27338637Free PMC Article
Schmidt J, Gong S, Marafioti T, Mankel B, Gonzalez-Farre B, Balagué O, Mozos A, Cabeçadas J, van der Walt J, Hoehn D, Rosenwald A, Ott G, Dojcinov S, Egan C, Nadeu F, Ramis-Zaldívar JE, Clot G, Bárcena C, Pérez-Alonso V, Endris V, Penzel R, Lome-Maldonado C, Bonzheim I, Fend F, Campo E, Jaffe ES, Salaverria I, Quintanilla-Martinez L
Blood 2016 Aug 25;128(8):1101-11. Epub 2016 Jun 2 doi: 10.1182/blood-2016-03-703819. PMID: 27257180Free PMC Article

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