U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Congenital stenosis of pulmonary artery

MedGen UID:
472996
•Concept ID:
C0265911
•
Congenital Abnormality
Synonym: Congenital Pulmonary Artery Stenosis
SNOMED CT: Congenital stenosis of pulmonary artery (449125001)

Definition

A congenital cardiovascular abnormality characterized by the narrowing of the lumen of the main pulmonary artery or its branches. It may be associated with other congenital heart malformations. Signs and symptoms include dyspnea, tachypnea, tachycardia, fatigue, and edema. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVCongenital stenosis of pulmonary artery

Professional guidelines

PubMed

Treatment approach to unilateral branch pulmonary artery stenosis.
Hiremath G, Qureshi AM, Meadows J, Aggarwal V
Trends Cardiovasc Med 2021 Apr;31(3):179-184. Epub 2020 Feb 10 doi: 10.1016/j.tcm.2020.02.001. PMID: 32081565
Treatment of Peripheral Pulmonary Artery Stenosis.
Kim CW, Aronow WS, Dutta T, Spevack DM, Frishman WH
Cardiol Rev 2021 May-Jun 01;29(3):115-119. doi: 10.1097/CRD.0000000000000300. PMID: 32053544
Management of the adult Fontan patient.
Rodriguez FH, Book WM
Heart 2020 Jan;106(2):105-110. Epub 2019 Oct 29 doi: 10.1136/heartjnl-2019-314937. PMID: 31662332

Supplemental Content

Table of contents

    Practice guidelines

    • PubMed
      See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Related information

    • PMC Articles
      Related information in PubMed Central Links
    • PubMed
      Related literature resources in PubMed

    Recent activity

    Clear Turn Off Turn On

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...