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Gallbladder Large Cell Neuroendocrine Carcinoma

MedGen UID:
473514
Concept ID:
C2010353
Neoplastic Process
Synonym: Gallbladder Large Cell NEC

Definition

An aggressive, high-grade and poorly differentiated carcinoma with neuroendocrine differentiation that arises from the gallbladder. It is characterized by the presence of malignant large cells. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVGallbladder Large Cell Neuroendocrine Carcinoma

Professional guidelines

PubMed

Zhu J, Xiao W, Li Y
J Laparoendosc Adv Surg Tech A 2022 Jun;32(6):639-645. Epub 2021 Oct 11 doi: 10.1089/lap.2021.0482. PMID: 34637632
Kemeny N, Schneider A
Curr Probl Cancer 1989 Jul-Aug;13(4):197-283. doi: 10.1016/0147-0272(89)90007-x. PMID: 2548812

Recent clinical studies

Etiology

Zhu J, Xiao W, Li Y
J Laparoendosc Adv Surg Tech A 2022 Jun;32(6):639-645. Epub 2021 Oct 11 doi: 10.1089/lap.2021.0482. PMID: 34637632
Abutaka A, El-Matbouly M, Helmy I, Elmoghazy W, Sulieman I, Ben Gashir M, Soofi M, Khalaf H, Elaffandi A
World J Surg Oncol 2019 Jul 20;17(1):126. doi: 10.1186/s12957-019-1666-9. PMID: 31325969Free PMC Article
Ayabe RI, Wach M, Ruff S, Martin S, Diggs L, Wiemken T, Hinyard L, Davis JL, Luu C, Hernandez JM
Ann Surg Oncol 2019 Oct;26(11):3577-3585. Epub 2019 May 17 doi: 10.1245/s10434-019-07440-6. PMID: 31102094Free PMC Article
Soin S, Pannu BS, Myint PT, Dhillon AS
BMJ Case Rep 2018 Jun 28;2018 doi: 10.1136/bcr-2018-225141. PMID: 29954768Free PMC Article
Kamboj M, Gandhi JS, Gupta G, Sharma A, Pasricha S, Mehta A, Chandragouda D, Sinha R
J Gastrointest Cancer 2015 Dec;46(4):356-64. doi: 10.1007/s12029-015-9745-9. PMID: 26208508

Diagnosis

Jiang M, Zhang Y
J Cancer Res Ther 2023 Aug;19(4):910-916. doi: 10.4103/jcrt.jcrt_1959_21. PMID: 37675716
Ren X, Jiang H, Sun K, Qin X, Qu Y, Xia T, Chen Y
Diagn Pathol 2022 Jun 17;17(1):51. doi: 10.1186/s13000-022-01231-6. PMID: 35715834Free PMC Article
Zhu J, Xiao W, Li Y
J Laparoendosc Adv Surg Tech A 2022 Jun;32(6):639-645. Epub 2021 Oct 11 doi: 10.1089/lap.2021.0482. PMID: 34637632
Raiker R, Chauhan A, Hasanein H, Burkeen G, Horn M, Veedu J, Vela C, Arnold S, Kolesar J, Anthony L, Evers BM, Cavnar M
Orphanet J Rare Dis 2019 Nov 21;14(1):266. doi: 10.1186/s13023-019-1230-2. PMID: 31752927Free PMC Article
Sato K, Imai T, Shirota Y, Ueda Y, Katsuda S
Pathol Res Pract 2010 Jun 15;206(6):397-400. Epub 2009 Nov 27 doi: 10.1016/j.prp.2009.10.008. PMID: 19945229

Therapy

Giraldo NA, Drill E, Satravada BA, Dika IE, Brannon AR, Dermawan J, Mohanty A, Ozcan K, Chakravarty D, Benayed R, Vakiani E, Abou-Alfa GK, Kundra R, Schultz N, Li BT, Berger MF, Harding JJ, Ladanyi M, O'Reilly EM, Jarnagin W, Vanderbilt C, Basturk O, Arcila ME
Clin Cancer Res 2022 Dec 15;28(24):5359-5367. doi: 10.1158/1078-0432.CCR-22-1954. PMID: 36228155Free PMC Article
Han Y, Li L, Sun H
World Neurosurg 2020 Jun;138:723-731. Epub 2020 Jan 30 doi: 10.1016/j.wneu.2020.01.169. PMID: 32006738
Shimono C, Suwa K, Sato M, Shirai S, Yamada K, Nakamura Y, Makuuchi M
Int J Clin Oncol 2009 Aug;14(4):351-5. Epub 2009 Aug 25 doi: 10.1007/s10147-008-0843-6. PMID: 19705247
Iype S, Mirza TA, Propper DJ, Bhattacharya S, Feakins RM, Kocher HM
Postgrad Med J 2009 Apr;85(1002):213-8. doi: 10.1136/pgmj.2008.070649. PMID: 19417172
Kemeny N, Schneider A
Curr Probl Cancer 1989 Jul-Aug;13(4):197-283. doi: 10.1016/0147-0272(89)90007-x. PMID: 2548812

Prognosis

Sah DN, Shrestha O
JNMA J Nepal Med Assoc 2024 Feb 24;62(270):152-154. doi: 10.31729/jnma.8444. PMID: 38409975Free PMC Article
Jiang M, Zhang Y
J Cancer Res Ther 2023 Aug;19(4):910-916. doi: 10.4103/jcrt.jcrt_1959_21. PMID: 37675716
Giraldo NA, Drill E, Satravada BA, Dika IE, Brannon AR, Dermawan J, Mohanty A, Ozcan K, Chakravarty D, Benayed R, Vakiani E, Abou-Alfa GK, Kundra R, Schultz N, Li BT, Berger MF, Harding JJ, Ladanyi M, O'Reilly EM, Jarnagin W, Vanderbilt C, Basturk O, Arcila ME
Clin Cancer Res 2022 Dec 15;28(24):5359-5367. doi: 10.1158/1078-0432.CCR-22-1954. PMID: 36228155Free PMC Article
Zhu J, Xiao W, Li Y
J Laparoendosc Adv Surg Tech A 2022 Jun;32(6):639-645. Epub 2021 Oct 11 doi: 10.1089/lap.2021.0482. PMID: 34637632
Raiker R, Chauhan A, Hasanein H, Burkeen G, Horn M, Veedu J, Vela C, Arnold S, Kolesar J, Anthony L, Evers BM, Cavnar M
Orphanet J Rare Dis 2019 Nov 21;14(1):266. doi: 10.1186/s13023-019-1230-2. PMID: 31752927Free PMC Article

Clinical prediction guides

Liu F, Li Y, Ying D, Qiu S, He Y, Li M, Liu Y, Zhang Y, Zhu Q, Hu Y, Liu L, Li G, Pan W, Jin W, Mu J, Cao Y, Liu Y
Signal Transduct Target Ther 2021 Feb 10;6(1):55. doi: 10.1038/s41392-020-00412-3. PMID: 33563892Free PMC Article
Lee SM, Sung CO
Am J Surg Pathol 2020 Oct;44(10):1308-1321. doi: 10.1097/PAS.0000000000001536. PMID: 32739935
Sciarra A, Missiaglia E, Trimech M, Melloul E, Brouland JP, Sempoux C, La Rosa S
Endocr Pathol 2020 Mar;31(1):84-93. doi: 10.1007/s12022-020-09605-6. PMID: 31981075
Liu W, Wang L, He XD, Feng C, Chang XY, Lu ZH
World J Surg Oncol 2015 Mar 18;13:114. doi: 10.1186/s12957-015-0533-6. PMID: 25890047Free PMC Article
Sato K, Imai T, Shirota Y, Ueda Y, Katsuda S
Pathol Res Pract 2010 Jun 15;206(6):397-400. Epub 2009 Nov 27 doi: 10.1016/j.prp.2009.10.008. PMID: 19945229

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