U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Hyperostosis, Sternocostoclavicular

MedGen UID:
5696
Concept ID:
C0020499
Disease or Syndrome
Synonyms: Hyperostoses, Sternocostoclavicular; Sternocostoclavicular Hyperostoses; Sternocostoclavicular Hyperostosis

Definition

A rare, benign rheumatologic disorder or syndrome characterized by hyperostosis and soft tissue ossification between the clavicles and the anterior part of the upper ribs. It is often associated with the dermatologic disorder palmoplantar pustulosis, particularly in Japan. Careful diagnosis is required to distinguish it from psoriatic arthritis, OSTEITIS DEFORMANS, and other diseases. Spondylitis of pustulosis palmaris et plantaris is one of the possible causes; also, evidence suggests one origin may be bone infection. Bone imaging is especially useful for diagnosis. It was originally described by Sonozaki in 1974. [from MeSH]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVHyperostosis, Sternocostoclavicular

Recent clinical studies

Etiology

Suzuki M, Kanazawa H, Shinozaki T, Sugimoto H
Eur Radiol 2017 Nov;27(11):4532-4537. Epub 2017 May 12 doi: 10.1007/s00330-017-4861-5. PMID: 28500364
Valkema PA, Luymes CH, Witteveen JE, le Cessie S, Appelman-Dijkstra NM, Hogendoorn PC, Hamdy NA
Orphanet J Rare Dis 2017 Jan 25;12(1):20. doi: 10.1186/s13023-017-0573-9. PMID: 28122596Free PMC Article
Freyschmidt J, Sternberg A
Eur Radiol 1998;8(5):807-12. doi: 10.1007/s003300050476. PMID: 9601969
Watts RA, Crisp AJ, Hazleman BL, Daunt SO, Jenner JR
Br J Rheumatol 1993 May;32(5):403-7. doi: 10.1093/rheumatology/32.5.403. PMID: 8495262
Fritz P, Baldauf G, Wilke HJ, Reitter I
Ann Rheum Dis 1992 May;51(5):658-64. doi: 10.1136/ard.51.5.658. PMID: 1616334Free PMC Article

Diagnosis

Leerling AT, Cañete AN, Ramautar AIE, Appelman-Dijkstra NM, Winter EM
Front Endocrinol (Lausanne) 2021;12:621604. Epub 2021 Feb 18 doi: 10.3389/fendo.2021.621604. PMID: 33679619Free PMC Article
Yachoui R, Kreidy M, Parker BJ
Clin Med Res 2017 Jun;15(1-2):37-40. doi: 10.3121/cmr.2017.1352. PMID: 28751466Free PMC Article
Azouz EM, Jurik AG, Bernard C
AJR Am J Roentgenol 1998 Aug;171(2):461-6. doi: 10.2214/ajr.171.2.9694476. PMID: 9694476
Brandsen RE, Dekel S, Yaron M, Caspi D, Ophir J, Brenner S
Dermatology 1993;186(3):176-80. doi: 10.1159/000247340. PMID: 8453142
Suh JS, Chung JJ, Park BM, Kim KR
Yonsei Med J 1988;29(4):388-92. doi: 10.3349/ymj.1988.29.4.388. PMID: 3266697

Therapy

Leerling AT, Cañete AN, Ramautar AIE, Appelman-Dijkstra NM, Winter EM
Front Endocrinol (Lausanne) 2021;12:621604. Epub 2021 Feb 18 doi: 10.3389/fendo.2021.621604. PMID: 33679619Free PMC Article
Yachoui R, Kreidy M, Parker BJ
Clin Med Res 2017 Jun;15(1-2):37-40. doi: 10.3121/cmr.2017.1352. PMID: 28751466Free PMC Article
Noda K, Kodama S, Suenaga S, Suzuki M
Clin Exp Nephrol 2007 Mar;11(1):97-101. Epub 2007 Mar 28 doi: 10.1007/s10157-006-0450-7. PMID: 17385006
Ringe JD, Faber H, Farahmand P
J Bone Miner Metab 2006;24(1):87-93. doi: 10.1007/s00774-005-0651-2. PMID: 16369904
Nungu S, Olerud C, Rehnberg L
Ups J Med Sci 1992;97(2):177-82. doi: 10.3109/03009739209179294. PMID: 1471317

Prognosis

Leerling AT, Cañete AN, Ramautar AIE, Appelman-Dijkstra NM, Winter EM
Front Endocrinol (Lausanne) 2021;12:621604. Epub 2021 Feb 18 doi: 10.3389/fendo.2021.621604. PMID: 33679619Free PMC Article
Colina M, Govoni M, Orzincolo C, Trotta F
Arthritis Rheum 2009 Jun 15;61(6):813-21. doi: 10.1002/art.24540. PMID: 19479702
Massara A, Cavazzini PL, Trotta F
Rheumatology (Oxford) 2006 Jun;45(6):730-3. Epub 2006 Jan 10 doi: 10.1093/rheumatology/kei221. PMID: 16403830
Dihlmann W, Dihlmann SW, Hering L
Clin Rheumatol 1997 Jan;16(1):13-24. doi: 10.1007/BF02238758. PMID: 9132321
Fritz P, Baldauf G, Wilke HJ, Reitter I
Ann Rheum Dis 1992 May;51(5):658-64. doi: 10.1136/ard.51.5.658. PMID: 1616334Free PMC Article

Clinical prediction guides

Leerling AT, Cañete AN, Ramautar AIE, Appelman-Dijkstra NM, Winter EM
Front Endocrinol (Lausanne) 2021;12:621604. Epub 2021 Feb 18 doi: 10.3389/fendo.2021.621604. PMID: 33679619Free PMC Article
Valkema PA, Luymes CH, Witteveen JE, le Cessie S, Appelman-Dijkstra NM, Hogendoorn PC, Hamdy NA
Orphanet J Rare Dis 2017 Jan 25;12(1):20. doi: 10.1186/s13023-017-0573-9. PMID: 28122596Free PMC Article
Furukawa M, Miwa T, Kamide M, Sakumoto M, Umeda R
J Laryngol Otol 1989 Aug;103(8):783-6. doi: 10.1017/s0022215100110072. PMID: 2788688

Supplemental Content

Table of contents

    Recent activity

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...