U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Polyembryoma

MedGen UID:
83160
Concept ID:
C0334518
Neoplastic Process
Synonyms: Embryonal carcinoma - polyembryonal type; Embryonal carcinoma, polyembryonal type; Gonadal Polyembryoma; gonadal polyembryoma; polyembryoma
SNOMED CT: Embryonal carcinoma - polyembryonal type (28325008); Polyembryoma (1156404008); Polyembryoma (28325008); Embryonal carcinoma, polyembryonal type (28325008)
Modes of inheritance:
Not genetically inherited
MedGen UID:
988794
Concept ID:
CN307044
Finding
Source: Orphanet
clinical entity without genetic inheritance.
 
Monarch Initiative: MONDO:0015863
Orphanet: ORPHA180229

Definition

A rare malignant germ cell tumor characterized by predominant composition of embryoid bodies consisting of a central core of embryonal carcinoma cells, an amnion-like cavity, and a yolk sac tumor component. The tumor usually occurs as the dominant component of a mixed germ cell tumor, with teratoma being the most common associated element. It may manifest as an abdominal mass or with abdominal pain, menstrual irregularities, or precocious puberty in women, while men typically present with testicular enlargement. Serum alpha-fetoprotein and/or beta-human chorionic gonadotropin can be elevated. [from ORDO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVPolyembryoma
Follow this link to review classifications for Polyembryoma in Orphanet.

Professional guidelines

PubMed

Ulbright TM
Mod Pathol 2005 Feb;18 Suppl 2:S61-79. doi: 10.1038/modpathol.3800310. PMID: 15761467
Aziz MF
Gan To Kagaku Ryoho 1995 Aug;22 Suppl 3:262-76. PMID: 7661594

Recent clinical studies

Etiology

Ulbright TM
Mod Pathol 2005 Feb;18 Suppl 2:S61-79. doi: 10.1038/modpathol.3800310. PMID: 15761467
Ulbright TM
Am J Surg Pathol 1993 Nov;17(11):1075-91. doi: 10.1097/00000478-199311000-00001. PMID: 8214253
Kawai M, Kano T, Furuhashi Y, Mizuno K, Nakashima N, Hattori SE, Kazeto S, Iida S, Ohta M, Arii Y
Cancer 1991 Jan 1;67(1):184-92. doi: 10.1002/1097-0142(19910101)67:1<184::aid-cncr2820670131>3.0.co;2-c. PMID: 1845936
Kawai M, Furuhashi Y, Kano T, Misawa T, Nakashima N, Hattori S, Okamoto Y, Kobayashi I, Ohta M, Arii Y
Gynecol Oncol 1990 Nov;39(2):160-6. doi: 10.1016/0090-8258(90)90425-k. PMID: 1699854

Diagnosis

Ricci C, Ambrosi F, Franceschini T, Giunchi F, Di Filippo G, Franchini E, Massari F, Mollica V, Tateo V, Bianchi FM, Colecchia M, Acosta AM, Fiorentino M
Histopathology 2023 Sep;83(3):465-476. Epub 2023 Jun 14 doi: 10.1111/his.14968. PMID: 37317674
Stall JN, Young RH
Mod Pathol 2017 Jul;30(7):908-918. Epub 2017 Apr 21 doi: 10.1038/modpathol.2017.25. PMID: 28429716
Young RH
Arch Pathol Lab Med 2008 Apr;132(4):548-64. doi: 10.5858/2008-132-548-TTNAAF. PMID: 18384207
Corakçi A, Ozeren S, Ozkan S, Gürbüz Y, Ustün H, Yücesoy I
Arch Gynecol Obstet 2005 Feb;271(2):176-7. Epub 2004 Feb 28 doi: 10.1007/s00404-004-0604-3. PMID: 14991382
Aziz MF
Gan To Kagaku Ryoho 1995 Aug;22 Suppl 3:262-76. PMID: 7661594

Therapy

Song SY, Ko YH, Ahn G
Int J Surg Pathol 2005 Jul;13(3):299-303. doi: 10.1177/106689690501300314. PMID: 16086090
Bakaris S, Resim S, Tunali N
Pediatr Dev Pathol 2005 Jan-Feb;8(1):92-7. Epub 2004 Dec 6 doi: 10.1007/s10024-004-2123-4. PMID: 15803215
Nishida T, Oda T, Sugiyama T, Kataoka A, Honda S, Yakushiji M
Eur J Obstet Gynecol Reprod Biol 1998 May;78(1):95-7. doi: 10.1016/s0301-2115(98)00013-x. PMID: 9605457
Aziz MF
Gan To Kagaku Ryoho 1995 Aug;22 Suppl 3:262-76. PMID: 7661594
de Peralta-Venturina MN, Ro JY, Ordónez NG, Ayala AG
Am J Clin Pathol 1994 Oct;102(4):402-5. doi: 10.1093/ajcp/102.4.402. PMID: 7524298

Prognosis

Cheng L, Zhang S, Talerman A, Roth LM
Hum Pathol 2010 May;41(5):716-23. Epub 2010 Jan 21 doi: 10.1016/j.humpath.2009.10.016. PMID: 20096442
Ulbright TM
Mod Pathol 2005 Feb;18 Suppl 2:S61-79. doi: 10.1038/modpathol.3800310. PMID: 15761467
Aziz MF
Gan To Kagaku Ryoho 1995 Aug;22 Suppl 3:262-76. PMID: 7661594
Kawai M, Kano T, Furuhashi Y, Mizuno K, Nakashima N, Hattori SE, Kazeto S, Iida S, Ohta M, Arii Y
Cancer 1991 Jan 1;67(1):184-92. doi: 10.1002/1097-0142(19910101)67:1<184::aid-cncr2820670131>3.0.co;2-c. PMID: 1845936
Kawai M, Furuhashi Y, Kano T, Misawa T, Nakashima N, Hattori S, Okamoto Y, Kobayashi I, Ohta M, Arii Y
Gynecol Oncol 1990 Nov;39(2):160-6. doi: 10.1016/0090-8258(90)90425-k. PMID: 1699854

Clinical prediction guides

Kawai M, Furuhashi Y, Kano T, Misawa T, Nakashima N, Hattori S, Okamoto Y, Kobayashi I, Ohta M, Arii Y
Gynecol Oncol 1990 Nov;39(2):160-6. doi: 10.1016/0090-8258(90)90425-k. PMID: 1699854
Nakashima N, Fukatsu T, Nagasaka T, Sobue M, Takeuchi J
Am J Surg Pathol 1987 Sep;11(9):682-92. doi: 10.1097/00000478-198709000-00004. PMID: 2443027

Supplemental Content

Table of contents

    Clinical resources

    Practice guidelines

    • PubMed
      See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.
    • Bookshelf
      See practice and clinical guidelines in NCBI Bookshelf. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Recent activity

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...