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Severe hearing impairment

MedGen UID:
846511
Concept ID:
C3874334
Finding
Synonym: Severe hearing loss
SNOMED CT: Severe hearing loss (3561000119106)
 
HPO: HP:0012714

Definition

A severe form of hearing impairment. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • Severe hearing impairment

Professional guidelines

PubMed

Saki N, Bayat A, Hoseinabadi R, Nikakhlagh S, Karimi M, Dashti R
Int J Pediatr Otorhinolaryngol 2017 Jun;97:89-92. Epub 2017 Mar 31 doi: 10.1016/j.ijporl.2017.03.038. PMID: 28483258
Braun T, Hempel JM, Berghaus A
Dtsch Arztebl Int 2014 Feb 7;111(6):92-8. doi: 10.3238/arztebl.2014.0092. PMID: 24622605Free PMC Article
Oudesluys-Murphy AM, van Straaten HL, Bholasingh R, van Zanten GA
Eur J Pediatr 1996 Jun;155(6):429-35. doi: 10.1007/BF01955176. PMID: 8789756

Recent clinical studies

Etiology

Shen X, Yu H, Chen K, Xue Q, Lu J, Xie Z
J Clin Anesth 2023 Dec;91:111254. Epub 2023 Sep 8 doi: 10.1016/j.jclinane.2023.111254. PMID: 37689025
Foster JI, Williams KL, Timmer BHB, Brauer SG
Trends Hear 2022 Jan-Dec;26:23312165221144155. doi: 10.1177/23312165221144155. PMID: 36524292Free PMC Article
Alattar AA, Bergstrom J, Laughlin GA, Kritz-Silverstein D, Richard EL, Reas ET, Harris JP, Barrett-Connor E, McEvoy LK
J Gerontol A Biol Sci Med Sci 2020 Feb 14;75(3):567-573. doi: 10.1093/gerona/glz035. PMID: 30753308Free PMC Article
Kim SY, Kim HJ, Park EK, Joe J, Sim S, Choi HG
PLoS One 2017;12(6):e0179973. Epub 2017 Jun 22 doi: 10.1371/journal.pone.0179973. PMID: 28640916Free PMC Article
Oudesluys-Murphy AM, van Straaten HL, Bholasingh R, van Zanten GA
Eur J Pediatr 1996 Jun;155(6):429-35. doi: 10.1007/BF01955176. PMID: 8789756

Diagnosis

Foster JI, Williams KL, Timmer BHB, Brauer SG
Trends Hear 2022 Jan-Dec;26:23312165221144155. doi: 10.1177/23312165221144155. PMID: 36524292Free PMC Article
Kim SY, Lee CH, Min C, Yoo DM, Choi HG
Curr Issues Mol Biol 2021 May 18;43(1):142-152. doi: 10.3390/cimb43010012. PMID: 34070082Free PMC Article
Meyer C, Hickson L
Int J Audiol 2012 Feb;51(2):66-74. doi: 10.3109/14992027.2011.611178. PMID: 22256793
Keats BJ, Corey DP
Am J Med Genet 1999 Sep 24;89(3):158-66. PMID: 10704190
Oudesluys-Murphy AM, van Straaten HL, Bholasingh R, van Zanten GA
Eur J Pediatr 1996 Jun;155(6):429-35. doi: 10.1007/BF01955176. PMID: 8789756

Therapy

Kim SY, Lee CH, Min C, Yoo DM, Choi HG
Curr Issues Mol Biol 2021 May 18;43(1):142-152. doi: 10.3390/cimb43010012. PMID: 34070082Free PMC Article
Solheim J, Hickson L
Int J Audiol 2017 Jul;56(7):472-479. Epub 2017 Mar 23 doi: 10.1080/14992027.2017.1303201. PMID: 28332420
Braun T, Hempel JM, Berghaus A
Dtsch Arztebl Int 2014 Feb 7;111(6):92-8. doi: 10.3238/arztebl.2014.0092. PMID: 24622605Free PMC Article
Rawlani S, Patil CY, Bhowte R, Degwekar S, Rawlani S, Chandak R, Rawlani S
Indian J Lepr 2013 Oct-Dec;85(4):171-6. PMID: 24834638
Centers for Disease Control and Prevention (CDC)
MMWR Morb Mortal Wkly Rep 2011 Jul 22;60(28):955-8. PMID: 21775950

Prognosis

Shen X, Yu H, Chen K, Xue Q, Lu J, Xie Z
J Clin Anesth 2023 Dec;91:111254. Epub 2023 Sep 8 doi: 10.1016/j.jclinane.2023.111254. PMID: 37689025
Kim SY, Lim JS, Kong IG, Choi HG
Sci Rep 2018 Oct 15;8(1):15266. doi: 10.1038/s41598-018-33325-x. PMID: 30323320Free PMC Article
Saki N, Bayat A, Hoseinabadi R, Nikakhlagh S, Karimi M, Dashti R
Int J Pediatr Otorhinolaryngol 2017 Jun;97:89-92. Epub 2017 Mar 31 doi: 10.1016/j.ijporl.2017.03.038. PMID: 28483258
Kemperman MH, Koch SM, Kumar S, Huygen PL, Joosten FB, Cremers CW
Int J Audiol 2004 Oct;43(9):523-32. doi: 10.1080/14992020400050067. PMID: 15726843
Oudesluys-Murphy AM, van Straaten HL, Bholasingh R, van Zanten GA
Eur J Pediatr 1996 Jun;155(6):429-35. doi: 10.1007/BF01955176. PMID: 8789756

Clinical prediction guides

Shen X, Yu H, Chen K, Xue Q, Lu J, Xie Z
J Clin Anesth 2023 Dec;91:111254. Epub 2023 Sep 8 doi: 10.1016/j.jclinane.2023.111254. PMID: 37689025
Foster JI, Williams KL, Timmer BHB, Brauer SG
Trends Hear 2022 Jan-Dec;26:23312165221144155. doi: 10.1177/23312165221144155. PMID: 36524292Free PMC Article
Stropahl M, Besser J, Launer S
Ear Hear 2020 Jul/Aug;41(4):697-704. doi: 10.1097/AUD.0000000000000806. PMID: 31613823
Dufresne D, Dagenais L, Shevell MI; REPACQ Consortium
Pediatr Neurol 2014 Nov;51(5):641-4. Epub 2014 Jul 19 doi: 10.1016/j.pediatrneurol.2014.07.005. PMID: 25194720
Eisenberg LS
Ear Hear 2007 Dec;28(6):766-72. doi: 10.1097/AUD.0b013e318157f01f. PMID: 17982364

Recent systematic reviews

Foster JI, Williams KL, Timmer BHB, Brauer SG
Trends Hear 2022 Jan-Dec;26:23312165221144155. doi: 10.1177/23312165221144155. PMID: 36524292Free PMC Article
de Kleijn JL, van Kalmthout LWM, van der Vossen MJB, Vonck BMD, Topsakal V, Bruijnzeel H
JAMA Otolaryngol Head Neck Surg 2018 Jul 1;144(7):630-638. doi: 10.1001/jamaoto.2018.0652. PMID: 29800000

Supplemental Content

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    Clinical resources

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