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Scleroderma Renal Crisis

MedGen UID:
853197
Concept ID:
C1262147
Disease or Syndrome

Definition

The onset of acute renal failure, normally coupled with marked hypertension in a patient with scleroderma. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVScleroderma Renal Crisis

Professional guidelines

PubMed

Zhao M, Wu J, Wu H, Sawalha AH, Lu Q
Clin Rev Allergy Immunol 2022 Apr;62(2):273-291. Epub 2021 Jan 15 doi: 10.1007/s12016-020-08831-4. PMID: 33449302
Fernández-Codina A, Walker KM, Pope JE; Scleroderma Algorithm Group
Arthritis Rheumatol 2018 Nov;70(11):1820-1828. Epub 2018 Sep 17 doi: 10.1002/art.40560. PMID: 29781586
Kowal-Bielecka O, Fransen J, Avouac J, Becker M, Kulak A, Allanore Y, Distler O, Clements P, Cutolo M, Czirjak L, Damjanov N, Del Galdo F, Denton CP, Distler JHW, Foeldvari I, Figelstone K, Frerix M, Furst DE, Guiducci S, Hunzelmann N, Khanna D, Matucci-Cerinic M, Herrick AL, van den Hoogen F, van Laar JM, Riemekasten G, Silver R, Smith V, Sulli A, Tarner I, Tyndall A, Welling J, Wigley F, Valentini G, Walker UA, Zulian F, Müller-Ladner U; EUSTAR Coauthors
Ann Rheum Dis 2017 Aug;76(8):1327-1339. Epub 2016 Nov 9 doi: 10.1136/annrheumdis-2016-209909. PMID: 27941129

Recent clinical studies

Etiology

Cole A, Ong VH, Denton CP
Clin Rev Allergy Immunol 2023 Jun;64(3):378-391. Epub 2022 Jun 1 doi: 10.1007/s12016-022-08945-x. PMID: 35648373Free PMC Article
Fernández-Codina A, Walker KM, Pope JE; Scleroderma Algorithm Group
Arthritis Rheumatol 2018 Nov;70(11):1820-1828. Epub 2018 Sep 17 doi: 10.1002/art.40560. PMID: 29781586
Kowal-Bielecka O, Fransen J, Avouac J, Becker M, Kulak A, Allanore Y, Distler O, Clements P, Cutolo M, Czirjak L, Damjanov N, Del Galdo F, Denton CP, Distler JHW, Foeldvari I, Figelstone K, Frerix M, Furst DE, Guiducci S, Hunzelmann N, Khanna D, Matucci-Cerinic M, Herrick AL, van den Hoogen F, van Laar JM, Riemekasten G, Silver R, Smith V, Sulli A, Tarner I, Tyndall A, Welling J, Wigley F, Valentini G, Walker UA, Zulian F, Müller-Ladner U; EUSTAR Coauthors
Ann Rheum Dis 2017 Aug;76(8):1327-1339. Epub 2016 Nov 9 doi: 10.1136/annrheumdis-2016-209909. PMID: 27941129
Hudson M
Curr Opin Rheumatol 2015 Nov;27(6):549-54. doi: 10.1097/BOR.0000000000000221. PMID: 26352732
Mouthon L, Bussone G, Berezné A, Noël LH, Guillevin L
J Rheumatol 2014 Jun;41(6):1040-8. Epub 2014 May 15 doi: 10.3899/jrheum.131210. PMID: 24833760

Diagnosis

Scheen M, Dominati A, Olivier V, Nasr S, De Seigneux S, Mekinian A, Issa N, Haidar F
Autoimmun Rev 2023 Jun;22(6):103330. Epub 2023 Apr 7 doi: 10.1016/j.autrev.2023.103330. PMID: 37031831
Cole A, Ong VH, Denton CP
Clin Rev Allergy Immunol 2023 Jun;64(3):378-391. Epub 2022 Jun 1 doi: 10.1007/s12016-022-08945-x. PMID: 35648373Free PMC Article
Hudson M, Ghossein C, Steen V
Presse Med 2021 Apr;50(1):104063. Epub 2021 Feb 3 doi: 10.1016/j.lpm.2021.104063. PMID: 33548376
Denton CP, Khanna D
Lancet 2017 Oct 7;390(10103):1685-1699. Epub 2017 Apr 13 doi: 10.1016/S0140-6736(17)30933-9. PMID: 28413064
Hudson M
Curr Opin Rheumatol 2015 Nov;27(6):549-54. doi: 10.1097/BOR.0000000000000221. PMID: 26352732

Therapy

Cole A, Ong VH, Denton CP
Clin Rev Allergy Immunol 2023 Jun;64(3):378-391. Epub 2022 Jun 1 doi: 10.1007/s12016-022-08945-x. PMID: 35648373Free PMC Article
Zhao M, Wu J, Wu H, Sawalha AH, Lu Q
Clin Rev Allergy Immunol 2022 Apr;62(2):273-291. Epub 2021 Jan 15 doi: 10.1007/s12016-020-08831-4. PMID: 33449302
Hudson M, Ghossein C, Steen V
Presse Med 2021 Apr;50(1):104063. Epub 2021 Feb 3 doi: 10.1016/j.lpm.2021.104063. PMID: 33548376
Fernández-Codina A, Walker KM, Pope JE; Scleroderma Algorithm Group
Arthritis Rheumatol 2018 Nov;70(11):1820-1828. Epub 2018 Sep 17 doi: 10.1002/art.40560. PMID: 29781586
Kowal-Bielecka O, Fransen J, Avouac J, Becker M, Kulak A, Allanore Y, Distler O, Clements P, Cutolo M, Czirjak L, Damjanov N, Del Galdo F, Denton CP, Distler JHW, Foeldvari I, Figelstone K, Frerix M, Furst DE, Guiducci S, Hunzelmann N, Khanna D, Matucci-Cerinic M, Herrick AL, van den Hoogen F, van Laar JM, Riemekasten G, Silver R, Smith V, Sulli A, Tarner I, Tyndall A, Welling J, Wigley F, Valentini G, Walker UA, Zulian F, Müller-Ladner U; EUSTAR Coauthors
Ann Rheum Dis 2017 Aug;76(8):1327-1339. Epub 2016 Nov 9 doi: 10.1136/annrheumdis-2016-209909. PMID: 27941129

Prognosis

Khadra Y, Walker JG, Hakendorf P, Proudman S, Rischmueller M, Hill CL, Whittle S, Pontifex E, Roberts-Thomson PJ
Intern Med J 2021 Feb;51(2):235-242. doi: 10.1111/imj.14772. PMID: 32043674
Nagaraja V
Curr Opin Rheumatol 2019 May;31(3):223-230. doi: 10.1097/BOR.0000000000000604. PMID: 30870219
Woodworth TG, Suliman YA, Li W, Furst DE, Clements P
Nat Rev Nephrol 2016 Nov;12(11):678-691. Epub 2016 Sep 19 doi: 10.1038/nrneph.2016.124. PMID: 27641135
Bose N, Chiesa-Vottero A, Chatterjee S
Semin Arthritis Rheum 2015 Jun;44(6):687-94. Epub 2014 Dec 11 doi: 10.1016/j.semarthrit.2014.12.001. PMID: 25613774
Mouthon L, Bussone G, Berezné A, Noël LH, Guillevin L
J Rheumatol 2014 Jun;41(6):1040-8. Epub 2014 May 15 doi: 10.3899/jrheum.131210. PMID: 24833760

Clinical prediction guides

Scheen M, Dominati A, Olivier V, Nasr S, De Seigneux S, Mekinian A, Issa N, Haidar F
Autoimmun Rev 2023 Jun;22(6):103330. Epub 2023 Apr 7 doi: 10.1016/j.autrev.2023.103330. PMID: 37031831
Khadra Y, Walker JG, Hakendorf P, Proudman S, Rischmueller M, Hill CL, Whittle S, Pontifex E, Roberts-Thomson PJ
Intern Med J 2021 Feb;51(2):235-242. doi: 10.1111/imj.14772. PMID: 32043674
Gallan AJ, Chang A
Semin Diagn Pathol 2020 May;37(3):121-126. Epub 2020 Feb 6 doi: 10.1053/j.semdp.2020.01.002. PMID: 32085935
Yamashita H, Kamei R, Kaneko H
Rheumatology (Oxford) 2019 Dec 1;58(12):2099-2106. doi: 10.1093/rheumatology/kez435. PMID: 31566243
Fernández-Codina A, Walker KM, Pope JE; Scleroderma Algorithm Group
Arthritis Rheumatol 2018 Nov;70(11):1820-1828. Epub 2018 Sep 17 doi: 10.1002/art.40560. PMID: 29781586

Recent systematic reviews

Farrukh L, Steen VD, Shapiro L, Mehta S
Semin Arthritis Rheum 2023 Dec;63:152256. Epub 2023 Aug 22 doi: 10.1016/j.semarthrit.2023.152256. PMID: 37689027
Xiong A, Cao Y, Xiang Q, Song Z, Zhang Y, Zhou S, Qiang Y, Chen H, Hu Z, Cui H, Luo J, Wang Y, Yang Y, Yang M, Shuai S
J Clin Pharm Ther 2022 Jun;47(6):722-731. Epub 2022 Mar 1 doi: 10.1111/jcpt.13621. PMID: 35233779
Kowal-Bielecka O, Fransen J, Avouac J, Becker M, Kulak A, Allanore Y, Distler O, Clements P, Cutolo M, Czirjak L, Damjanov N, Del Galdo F, Denton CP, Distler JHW, Foeldvari I, Figelstone K, Frerix M, Furst DE, Guiducci S, Hunzelmann N, Khanna D, Matucci-Cerinic M, Herrick AL, van den Hoogen F, van Laar JM, Riemekasten G, Silver R, Smith V, Sulli A, Tarner I, Tyndall A, Welling J, Wigley F, Valentini G, Walker UA, Zulian F, Müller-Ladner U; EUSTAR Coauthors
Ann Rheum Dis 2017 Aug;76(8):1327-1339. Epub 2016 Nov 9 doi: 10.1136/annrheumdis-2016-209909. PMID: 27941129
Khan IY, Singer LG, de Perrot M, Granton JT, Keshavjee S, Chau C, Kron A, Johnson SR
Respir Med 2013 Dec;107(12):2081-7. Epub 2013 Sep 26 doi: 10.1016/j.rmed.2013.09.015. PMID: 24113572
Trang G, Steele R, Baron M, Hudson M
Rheumatol Int 2012 Mar;32(3):645-53. Epub 2010 Dec 4 doi: 10.1007/s00296-010-1697-6. PMID: 21132302

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