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Straddling atrioventricular valve

MedGen UID:
868886
Concept ID:
C4023297
Anatomical Abnormality
HPO: HP:0011562

Definition

Anomalous insertion of the chordae tendinae or papillary muscles into the contralateral ventricle in the presence of a ventricular septum defect. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVStraddling atrioventricular valve

Recent clinical studies

Etiology

Tam VKH, Erez E, Roten L, Muyskens S, Sebastian V, Tsao C, Nikaidoh H
Ann Thorac Surg 2021 May;111(5):1607-1612. Epub 2020 Oct 10 doi: 10.1016/j.athoracsur.2020.07.056. PMID: 33045205
Morell VO, Jacobs JP, Quintessenza JA
Ann Thorac Surg 2005 Jun;79(6):2089-92; discussion 2092-3. doi: 10.1016/j.athoracsur.2004.11.059. PMID: 15919315
Delius RE, Rademecker MA, de Leval MR, Elliott MJ, Stark J
J Thorac Cardiovasc Surg 1996 Dec;112(6):1561-8; discussion 1568-9. doi: 10.1016/S0022-5223(96)70015-6. PMID: 8975848
Barlow A, Pawade A, Wilkinson JL, Anderson RH
Ann Thorac Surg 1995 Nov;60(5):1324-30. doi: 10.1016/0003-4975(95)00646-3. PMID: 8526621
Smallhorn JF, Sutherland GR, Anderson RH, Macartney FJ
Br Heart J 1982 Oct;48(4):331-41. doi: 10.1136/hrt.48.4.331. PMID: 7126385Free PMC Article

Diagnosis

Aiello V, Ho SY, Anderson RH
Am J Cardiovasc Pathol 1990;3(2):107-13. PMID: 2264983
Rice MJ, Seward JB, Edwards WD, Hagler DJ, Danielson GK, Puga FJ, Tajik AJ
Am J Cardiol 1985 Feb 15;55(5):505-13. doi: 10.1016/0002-9149(85)90236-x. PMID: 3969890
Smallhorn JF, Sutherland GR, Anderson RH, Macartney FJ
Br Heart J 1982 Oct;48(4):331-41. doi: 10.1136/hrt.48.4.331. PMID: 7126385Free PMC Article
Tabry IF, McGoon DC, Danielson GK, Wallace RB, Tajik AJ, Seward JB
J Thorac Cardiovasc Surg 1979 Feb;77(2):191-201. PMID: 762959
Sieg K, Hagler DJ, Ritter DG, McGoon DC, Maloney JD, Seward JB, Davis GD
Mayo Clin Proc 1977 Sep;52(9):561-68. PMID: 895198

Prognosis

Nakamura Y, Hagino I, Nakajima H, Aoki M
Pediatr Cardiol 2015 Dec;36(8):1712-21. Epub 2015 Jun 24 doi: 10.1007/s00246-015-1221-6. PMID: 26099174
Hsieh MJ, Lin PJ, Chang CH, Chang JP, Chu JJ, Su WJ
Cardiovasc Surg 1993 Apr;1(2):172-5. PMID: 7521266
Danielson GK, Tabry IF, Ritter DG, Fulton RE
J Thorac Cardiovasc Surg 1979 Jun;77(6):847-51. PMID: 374883

Clinical prediction guides

Rice MJ, Seward JB, Edwards WD, Hagler DJ, Danielson GK, Puga FJ, Tajik AJ
Am J Cardiol 1985 Feb 15;55(5):505-13. doi: 10.1016/0002-9149(85)90236-x. PMID: 3969890
Ostermeyer J, Körfer R, Frenzel H, Bircks W
Thorac Cardiovasc Surg 1980 Aug;28(4):233-8. doi: 10.1055/s-2007-1022085. PMID: 6158123

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