U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Extrahepatic portal hypertension

MedGen UID:
870811
Concept ID:
C4025268
Disease or Syndrome
HPO: HP:0004941

Definition

Increased pressure in the pre-hepatic portal vein. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVExtrahepatic portal hypertension

Conditions with this feature

Portal vein, cavernous transformation of
MedGen UID:
331396
Concept ID:
C1832917
Disease or Syndrome

Professional guidelines

PubMed

Le Roy B, Gelli M, Serji B, Memeo R, Vibert E
J Visc Surg 2015 Jun;152(3):161-6. Epub 2015 May 27 doi: 10.1016/j.jviscsurg.2015.04.003. PMID: 26025414
Erkan T, Cullu F, Kutlu T, Emir H, Yeşildağ E, Sarimurat N, Senyüz OF, Erginöz E, Tümay GT
Acta Gastroenterol Belg 2003 Jul-Sep;66(3):213-7. PMID: 14618951
Pajor A, Lehoczky D
Gynecol Obstet Invest 1990;30(4):193-7. doi: 10.1159/000293268. PMID: 2289698

Recent clinical studies

Etiology

Alkhasov A, Komina E, Ratnikov S, Saveleva M, Romanova E, Gusev A, Lochmatov M, Yatsyk S, Dyakonova E
J Laparoendosc Adv Surg Tech A 2023 Dec;33(12):1231-1235. Epub 2023 Oct 16 doi: 10.1089/lap.2022.0404. PMID: 37844079
Zhang YQ, Wang Q, Wu M, Ruan Z-, Li Y, Wei X-, Zhang FX, Li Y, Shao GR, Xiao J
Pediatr Surg Int 2021 May;37(5):597-606. Epub 2021 Jan 10 doi: 10.1007/s00383-020-04847-1. PMID: 33423101
Islek A, Ilhan D, Ozturk N, Guven B, Sag E
J Pediatr Hematol Oncol 2021 Oct 1;43(7):e951-e956. doi: 10.1097/MPH.0000000000002038. PMID: 33369998
Rehman ZU, Nazir Z
J Coll Physicians Surg Pak 2019 Dec;29(12):1228-1229. doi: 10.29271/jcpsp.2019.12.1228. PMID: 31839103
Menon P, Rao KL, Bhattacharya A, Thapa BR, Chowdhary SK, Mahajan JK, Samujh R
Eur J Pediatr Surg 2005 Apr;15(2):82-7. doi: 10.1055/s-2004-830341. PMID: 15877255

Diagnosis

Brichard M, Iesari S, Lerut J, Reding R, Goffette P, Coubeau L
Hepatobiliary Pancreat Dis Int 2022 Feb;21(1):25-32. Epub 2021 Aug 14 doi: 10.1016/j.hbpd.2021.08.003. PMID: 34426078
El Kininy W, Kearney L, Hosam N, Broe P, Keeling A
Ir J Med Sci 2017 May;186(2):323-327. Epub 2016 Feb 25 doi: 10.1007/s11845-016-1420-z. PMID: 26911860
Le Roy B, Gelli M, Serji B, Memeo R, Vibert E
J Visc Surg 2015 Jun;152(3):161-6. Epub 2015 May 27 doi: 10.1016/j.jviscsurg.2015.04.003. PMID: 26025414
Herve P, Le Pavec J, Sztrymf B, Decante B, Savale L, Sitbon O
Best Pract Res Clin Gastroenterol 2007;21(1):141-59. doi: 10.1016/j.bpg.2006.07.011. PMID: 17223502
Madsen MS, Petersen TH, Sommer H
Ann Surg 1986 Jul;204(1):72-7. doi: 10.1097/00000658-198607000-00010. PMID: 3729585Free PMC Article

Therapy

Alkhasov A, Komina E, Ratnikov S, Saveleva M, Romanova E, Gusev A, Lochmatov M, Yatsyk S, Dyakonova E
J Laparoendosc Adv Surg Tech A 2023 Dec;33(12):1231-1235. Epub 2023 Oct 16 doi: 10.1089/lap.2022.0404. PMID: 37844079
Liu J, Wang Q, Ding X, Liu Q, Huang W, Gu J, Wang Z, Wu W, Wu Z
BMC Gastroenterol 2022 Mar 25;22(1):136. doi: 10.1186/s12876-022-02214-z. PMID: 35337294Free PMC Article
Yang AY, Slatnick BL, Durgin J, Truche P, Kim HB, Cuenca AG
Am J Surg 2022 Jul;224(1 Pt B):530-534. Epub 2022 Feb 9 doi: 10.1016/j.amjsurg.2022.01.031. PMID: 35164959
Zhang YQ, Wang Q, Wu M, Ruan Z-, Li Y, Wei X-, Zhang FX, Li Y, Shao GR, Xiao J
Pediatr Surg Int 2021 May;37(5):597-606. Epub 2021 Jan 10 doi: 10.1007/s00383-020-04847-1. PMID: 33423101
Gulati MS, Paul SB, Arora NK, Berry M
Clin Imaging 1999 Nov-Dec;23(6):377-85. doi: 10.1016/s0899-7071(00)00170-4. PMID: 10899422

Prognosis

Islek A, Ilhan D, Ozturk N, Guven B, Sag E
J Pediatr Hematol Oncol 2021 Oct 1;43(7):e951-e956. doi: 10.1097/MPH.0000000000002038. PMID: 33369998
Rehman ZU, Nazir Z
J Coll Physicians Surg Pak 2019 Dec;29(12):1228-1229. doi: 10.29271/jcpsp.2019.12.1228. PMID: 31839103
El Kininy W, Kearney L, Hosam N, Broe P, Keeling A
Ir J Med Sci 2017 May;186(2):323-327. Epub 2016 Feb 25 doi: 10.1007/s11845-016-1420-z. PMID: 26911860
Bertocchini A, Falappa P, Grimaldi C, Bolla G, Monti L, de Ville de Goyet J
J Pediatr Surg 2014 Aug;49(8):1268-75. Epub 2013 Nov 15 doi: 10.1016/j.jpedsurg.2013.10.029. PMID: 25092088
Menon P, Rao KL, Bhattacharya A, Thapa BR, Chowdhary SK, Mahajan JK, Samujh R
Eur J Pediatr Surg 2005 Apr;15(2):82-7. doi: 10.1055/s-2004-830341. PMID: 15877255

Clinical prediction guides

Yuldashev RZ, Aliev MM, Maksudov MF, Khaydarov UO, Shokhaydarov S
Pediatr Surg Int 2023 Feb 1;39(1):97. doi: 10.1007/s00383-023-05384-3. PMID: 36723662
Brichard M, Iesari S, Lerut J, Reding R, Goffette P, Coubeau L
Hepatobiliary Pancreat Dis Int 2022 Feb;21(1):25-32. Epub 2021 Aug 14 doi: 10.1016/j.hbpd.2021.08.003. PMID: 34426078
Le Roy B, Gelli M, Serji B, Memeo R, Vibert E
J Visc Surg 2015 Jun;152(3):161-6. Epub 2015 May 27 doi: 10.1016/j.jviscsurg.2015.04.003. PMID: 26025414
Menon P, Rao KL, Bhattacharya A, Thapa BR, Chowdhary SK, Mahajan JK, Samujh R
Eur J Pediatr Surg 2005 Apr;15(2):82-7. doi: 10.1055/s-2004-830341. PMID: 15877255
Edwards BS, Weir EK, Edwards WD, Ludwig J, Dykoski RK, Edwards JE
J Am Coll Cardiol 1987 Dec;10(6):1233-8. doi: 10.1016/s0735-1097(87)80123-7. PMID: 3680790

Recent systematic reviews

Latorre Fragua RA, Manuel Vázquez A, López Marcano AJ, Gijón De La Santa L, de la Plaza Llamas R, Ramia Ángel JM
Scand J Surg 2020 Sep;109(3):177-186. Epub 2019 Jun 23 doi: 10.1177/1457496919857260. PMID: 31232190

Supplemental Content

Table of contents

    Clinical resources

    Practice guidelines

    • PubMed
      See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Consumer resources

    Recent activity

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...