U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Membranous Nephropathy - PLA2R Induced

MedGen UID:
882712
Concept ID:
C4054537
Disease or Syndrome

Definition

Membranous nephropathy due to phospholipase 2 receptor (PLA2R) antibodies. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVMembranous Nephropathy - PLA2R Induced

Professional guidelines

PubMed

Chen X, Jiao S, Li S, Li J, Li P, Song F, Yan Z
Balkan Med J 2023 Jul 12;40(4):287-293. Epub 2023 Jun 1 doi: 10.4274/balkanmedj.galenos.2023.2022-9-7. PMID: 37260416Free PMC Article

Recent clinical studies

Etiology

Ronco P, Beck L, Debiec H, Fervenza FC, Hou FF, Jha V, Sethi S, Tong A, Vivarelli M, Wetzels J
Nat Rev Dis Primers 2021 Sep 30;7(1):69. doi: 10.1038/s41572-021-00303-z. PMID: 34593809
Fernández-Juárez G, Rojas-Rivera J, Logt AV, Justino J, Sevillano A, Caravaca-Fontán F, Ávila A, Rabasco C, Cabello V, Varela A, Díez M, Martín-Reyes G, Diezhandino MG, Quintana LF, Agraz I, Gómez-Martino JR, Cao M, Rodríguez-Moreno A, Rivas B, Galeano C, Bonet J, Romera A, Shabaka A, Plaisier E, Espinosa M, Egido J, Segarra A, Lambeau G, Ronco P, Wetzels J, Praga M; STARMEN Investigators
Kidney Int 2021 Apr;99(4):986-998. Epub 2020 Nov 7 doi: 10.1016/j.kint.2020.10.014. PMID: 33166580
Ronco P, Debiec H
Annu Rev Pathol 2020 Jan 24;15:287-313. Epub 2019 Oct 17 doi: 10.1146/annurev-pathol-020117-043811. PMID: 31622560
Fervenza FC, Appel GB, Barbour SJ, Rovin BH, Lafayette RA, Aslam N, Jefferson JA, Gipson PE, Rizk DV, Sedor JR, Simon JF, McCarthy ET, Brenchley P, Sethi S, Avila-Casado C, Beanlands H, Lieske JC, Philibert D, Li T, Thomas LF, Green DF, Juncos LA, Beara-Lasic L, Blumenthal SS, Sussman AN, Erickson SB, Hladunewich M, Canetta PA, Hebert LA, Leung N, Radhakrishnan J, Reich HN, Parikh SV, Gipson DS, Lee DK, da Costa BR, Jüni P, Cattran DC; MENTOR Investigators
N Engl J Med 2019 Jul 4;381(1):36-46. doi: 10.1056/NEJMoa1814427. PMID: 31269364
Beck LH Jr
J Am Soc Nephrol 2017 Sep;28(9):2579-2589. Epub 2017 Jul 3 doi: 10.1681/ASN.2017020178. PMID: 28674044Free PMC Article

Diagnosis

Ronco P, Beck L, Debiec H, Fervenza FC, Hou FF, Jha V, Sethi S, Tong A, Vivarelli M, Wetzels J
Nat Rev Dis Primers 2021 Sep 30;7(1):69. doi: 10.1038/s41572-021-00303-z. PMID: 34593809
Zhang P, Huang W, Zheng Q, Tang J, Dong Z, Jiang Y, Liu Y, Liu W
J Immunol Res 2021;2021:8163298. Epub 2021 Jul 14 doi: 10.1155/2021/8163298. PMID: 34337081Free PMC Article
Dhaouadi T, Abdellatif J, Trabelsi R, Gaied H, Chamkhi S, Sfar I, Goucha R, Ben Hamida F, Ben Abdallah T, Gorgi Y
PLoS One 2020;15(10):e0240025. Epub 2020 Oct 1 doi: 10.1371/journal.pone.0240025. PMID: 33002091Free PMC Article
Ronco P, Debiec H
Annu Rev Pathol 2020 Jan 24;15:287-313. Epub 2019 Oct 17 doi: 10.1146/annurev-pathol-020117-043811. PMID: 31622560
Beck LH Jr
J Am Soc Nephrol 2017 Sep;28(9):2579-2589. Epub 2017 Jul 3 doi: 10.1681/ASN.2017020178. PMID: 28674044Free PMC Article

Therapy

Ma Q, Li X, Xu G
Viruses 2022 Sep 28;14(10) doi: 10.3390/v14102143. PMID: 36298697Free PMC Article
Ramachandran R, Prabakaran R, Priya G, Nayak S, Kumar P, Kumar A, Kumar V, Agrawal N, Rathi M, Kohli HS, Nada R
Nephron 2022;146(2):138-145. Epub 2021 Nov 3 doi: 10.1159/000518609. PMID: 34818240
Ronco P, Beck L, Debiec H, Fervenza FC, Hou FF, Jha V, Sethi S, Tong A, Vivarelli M, Wetzels J
Nat Rev Dis Primers 2021 Sep 30;7(1):69. doi: 10.1038/s41572-021-00303-z. PMID: 34593809
Fernández-Juárez G, Rojas-Rivera J, Logt AV, Justino J, Sevillano A, Caravaca-Fontán F, Ávila A, Rabasco C, Cabello V, Varela A, Díez M, Martín-Reyes G, Diezhandino MG, Quintana LF, Agraz I, Gómez-Martino JR, Cao M, Rodríguez-Moreno A, Rivas B, Galeano C, Bonet J, Romera A, Shabaka A, Plaisier E, Espinosa M, Egido J, Segarra A, Lambeau G, Ronco P, Wetzels J, Praga M; STARMEN Investigators
Kidney Int 2021 Apr;99(4):986-998. Epub 2020 Nov 7 doi: 10.1016/j.kint.2020.10.014. PMID: 33166580
Fervenza FC, Appel GB, Barbour SJ, Rovin BH, Lafayette RA, Aslam N, Jefferson JA, Gipson PE, Rizk DV, Sedor JR, Simon JF, McCarthy ET, Brenchley P, Sethi S, Avila-Casado C, Beanlands H, Lieske JC, Philibert D, Li T, Thomas LF, Green DF, Juncos LA, Beara-Lasic L, Blumenthal SS, Sussman AN, Erickson SB, Hladunewich M, Canetta PA, Hebert LA, Leung N, Radhakrishnan J, Reich HN, Parikh SV, Gipson DS, Lee DK, da Costa BR, Jüni P, Cattran DC; MENTOR Investigators
N Engl J Med 2019 Jul 4;381(1):36-46. doi: 10.1056/NEJMoa1814427. PMID: 31269364

Prognosis

Ma Q, Li X, Xu G
Viruses 2022 Sep 28;14(10) doi: 10.3390/v14102143. PMID: 36298697Free PMC Article
Ronco P, Beck L, Debiec H, Fervenza FC, Hou FF, Jha V, Sethi S, Tong A, Vivarelli M, Wetzels J
Nat Rev Dis Primers 2021 Sep 30;7(1):69. doi: 10.1038/s41572-021-00303-z. PMID: 34593809
Dhaouadi T, Abdellatif J, Trabelsi R, Gaied H, Chamkhi S, Sfar I, Goucha R, Ben Hamida F, Ben Abdallah T, Gorgi Y
PLoS One 2020;15(10):e0240025. Epub 2020 Oct 1 doi: 10.1371/journal.pone.0240025. PMID: 33002091Free PMC Article
Glassock RJ
Curr Opin Nephrol Hypertens 2012 May;21(3):235-42. doi: 10.1097/MNH.0b013e3283522ea8. PMID: 22388552
Beck LH Jr, Fervenza FC, Beck DM, Bonegio RG, Malik FA, Erickson SB, Cosio FG, Cattran DC, Salant DJ
J Am Soc Nephrol 2011 Aug;22(8):1543-50. Epub 2011 Jul 22 doi: 10.1681/ASN.2010111125. PMID: 21784898Free PMC Article

Clinical prediction guides

Zhang S, Huang J, Dong J, Li Z, Sun M, Sun Y, Chen B
Front Immunol 2023;14:1156470. Epub 2023 Apr 28 doi: 10.3389/fimmu.2023.1156470. PMID: 37187749Free PMC Article
Ronco P, Beck L, Debiec H, Fervenza FC, Hou FF, Jha V, Sethi S, Tong A, Vivarelli M, Wetzels J
Nat Rev Dis Primers 2021 Sep 30;7(1):69. doi: 10.1038/s41572-021-00303-z. PMID: 34593809
Fernández-Juárez G, Rojas-Rivera J, Logt AV, Justino J, Sevillano A, Caravaca-Fontán F, Ávila A, Rabasco C, Cabello V, Varela A, Díez M, Martín-Reyes G, Diezhandino MG, Quintana LF, Agraz I, Gómez-Martino JR, Cao M, Rodríguez-Moreno A, Rivas B, Galeano C, Bonet J, Romera A, Shabaka A, Plaisier E, Espinosa M, Egido J, Segarra A, Lambeau G, Ronco P, Wetzels J, Praga M; STARMEN Investigators
Kidney Int 2021 Apr;99(4):986-998. Epub 2020 Nov 7 doi: 10.1016/j.kint.2020.10.014. PMID: 33166580
Dhaouadi T, Abdellatif J, Trabelsi R, Gaied H, Chamkhi S, Sfar I, Goucha R, Ben Hamida F, Ben Abdallah T, Gorgi Y
PLoS One 2020;15(10):e0240025. Epub 2020 Oct 1 doi: 10.1371/journal.pone.0240025. PMID: 33002091Free PMC Article
Glassock RJ
Curr Opin Nephrol Hypertens 2012 May;21(3):235-42. doi: 10.1097/MNH.0b013e3283522ea8. PMID: 22388552

Recent systematic reviews

Xue C, Wang J, Pan J, Liang C, Zhou C, Wu J, Song S, Cui L, Zhang L, Liu Y, Dai B
BMC Nephrol 2023 Sep 22;24(1):280. doi: 10.1186/s12882-023-03307-x. PMID: 37740193Free PMC Article

Supplemental Content

Table of contents

    Practice guidelines

    • PubMed
      See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Recent activity

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...