U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Fibromatosis

MedGen UID:
8836
Concept ID:
C0016048
Neoplastic Process
Synonym: Fibromatoses
SNOMED CT: Fibromatosis (19928005); Fibromatosis (723976005)
 
Monarch Initiative: MONDO:0005031

Definition

A poorly circumscribed neoplasm arising from the soft tissues. It is characterized by the presence of spindle-shaped fibroblasts and an infiltrative growth pattern. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVFibromatosis

Professional guidelines

PubMed

Riedel RF, Agulnik M
Cancer 2022 Aug 15;128(16):3027-3040. Epub 2022 Jun 7 doi: 10.1002/cncr.34332. PMID: 35670122Free PMC Article
Desmoid Tumor Working Group
Eur J Cancer 2020 Mar;127:96-107. Epub 2020 Jan 28 doi: 10.1016/j.ejca.2019.11.013. PMID: 32004793
Kasper B, Baumgarten C, Garcia J, Bonvalot S, Haas R, Haller F, Hohenberger P, Penel N, Messiou C, van der Graaf WT, Gronchi A; Desmoid Working Group
Ann Oncol 2017 Oct 1;28(10):2399-2408. doi: 10.1093/annonc/mdx323. PMID: 28961825Free PMC Article

Recent clinical studies

Etiology

Bektas M, Bell T, Khan S, Tumminello B, Fernandez MM, Heyes C, Oton AB
Adv Ther 2023 Sep;40(9):3697-3722. Epub 2023 Jul 12 doi: 10.1007/s12325-023-02592-0. PMID: 37436594Free PMC Article
Prendergast K, Kryeziu S, Crago AM
Surg Clin North Am 2022 Aug;102(4):667-677. doi: 10.1016/j.suc.2022.05.005. PMID: 35952695
Riedel RF, Agulnik M
Cancer 2022 Aug 15;128(16):3027-3040. Epub 2022 Jun 7 doi: 10.1002/cncr.34332. PMID: 35670122Free PMC Article
Desmoid Tumor Working Group
Eur J Cancer 2020 Mar;127:96-107. Epub 2020 Jan 28 doi: 10.1016/j.ejca.2019.11.013. PMID: 32004793
Kasper B, Baumgarten C, Garcia J, Bonvalot S, Haas R, Haller F, Hohenberger P, Penel N, Messiou C, van der Graaf WT, Gronchi A; Desmoid Working Group
Ann Oncol 2017 Oct 1;28(10):2399-2408. doi: 10.1093/annonc/mdx323. PMID: 28961825Free PMC Article

Diagnosis

Bektas M, Bell T, Khan S, Tumminello B, Fernandez MM, Heyes C, Oton AB
Adv Ther 2023 Sep;40(9):3697-3722. Epub 2023 Jul 12 doi: 10.1007/s12325-023-02592-0. PMID: 37436594Free PMC Article
Brownstein JM, DeLaney TF
Hematol Oncol Clin North Am 2020 Feb;34(1):177-188. Epub 2019 Oct 28 doi: 10.1016/j.hoc.2019.09.002. PMID: 31739943
Kasper B, Baumgarten C, Garcia J, Bonvalot S, Haas R, Haller F, Hohenberger P, Penel N, Messiou C, van der Graaf WT, Gronchi A; Desmoid Working Group
Ann Oncol 2017 Oct 1;28(10):2399-2408. doi: 10.1093/annonc/mdx323. PMID: 28961825Free PMC Article
Otero S, Moskovic EC, Strauss DC, Benson C, Miah AB, Thway K, Messiou C
Clin Radiol 2015 Sep;70(9):1038-45. Epub 2015 Jul 7 doi: 10.1016/j.crad.2015.04.015. PMID: 26162574
Chaudhary P
Int J Colorectal Dis 2014 Dec;29(12):1445-51. Epub 2014 Aug 21 doi: 10.1007/s00384-014-1995-7. PMID: 25139370

Therapy

Gounder M, Ratan R, Alcindor T, Schöffski P, van der Graaf WT, Wilky BA, Riedel RF, Lim A, Smith LM, Moody S, Attia S, Chawla S, D'Amato G, Federman N, Merriam P, Van Tine BA, Vincenzi B, Benson C, Bui NQ, Chugh R, Tinoco G, Charlson J, Dileo P, Hartner L, Lapeire L, Mazzeo F, Palmerini E, Reichardt P, Stacchiotti S, Bailey HH, Burgess MA, Cote GM, Davis LE, Deshpande H, Gelderblom H, Grignani G, Loggers E, Philip T, Pressey JG, Kummar S, Kasper B
N Engl J Med 2023 Mar 9;388(10):898-912. doi: 10.1056/NEJMoa2210140. PMID: 36884323
Gounder MM, Mahoney MR, Van Tine BA, Ravi V, Attia S, Deshpande HA, Gupta AA, Milhem MM, Conry RM, Movva S, Pishvaian MJ, Riedel RF, Sabagh T, Tap WD, Horvat N, Basch E, Schwartz LH, Maki RG, Agaram NP, Lefkowitz RA, Mazaheri Y, Yamashita R, Wright JJ, Dueck AC, Schwartz GK
N Engl J Med 2018 Dec 20;379(25):2417-2428. doi: 10.1056/NEJMoa1805052. PMID: 30575484Free PMC Article
Kasper B, Baumgarten C, Garcia J, Bonvalot S, Haas R, Haller F, Hohenberger P, Penel N, Messiou C, van der Graaf WT, Gronchi A; Desmoid Working Group
Ann Oncol 2017 Oct 1;28(10):2399-2408. doi: 10.1093/annonc/mdx323. PMID: 28961825Free PMC Article
Veith NT, Tschernig T, Histing T, Madry H
Foot Ankle Int 2013 Dec;34(12):1742-6. Epub 2013 Sep 16 doi: 10.1177/1071100713505535. PMID: 24043350
Skubitz KM, D'Adamo DR
Mayo Clin Proc 2007 Nov;82(11):1409-32. doi: 10.4065/82.11.1409. PMID: 17976362

Prognosis

Riedel RF, Agulnik M
Cancer 2022 Aug 15;128(16):3027-3040. Epub 2022 Jun 7 doi: 10.1002/cncr.34332. PMID: 35670122Free PMC Article
Fiore M, Crago A, Gladdy R, Kasper B
Ann Surg Oncol 2021 Mar;28(3):1682-1689. Epub 2021 Jan 1 doi: 10.1245/s10434-020-09395-5. PMID: 33386543
Liu H, Zeng H, Zhang H, Wang H, Cheng Z, Hu Y, Wu Z
Breast J 2020 Nov;26(11):2217-2222. Epub 2020 Aug 4 doi: 10.1111/tbj.14008. PMID: 32754995
Gounder MM, Mahoney MR, Van Tine BA, Ravi V, Attia S, Deshpande HA, Gupta AA, Milhem MM, Conry RM, Movva S, Pishvaian MJ, Riedel RF, Sabagh T, Tap WD, Horvat N, Basch E, Schwartz LH, Maki RG, Agaram NP, Lefkowitz RA, Mazaheri Y, Yamashita R, Wright JJ, Dueck AC, Schwartz GK
N Engl J Med 2018 Dec 20;379(25):2417-2428. doi: 10.1056/NEJMoa1805052. PMID: 30575484Free PMC Article
Kasper B, Baumgarten C, Garcia J, Bonvalot S, Haas R, Haller F, Hohenberger P, Penel N, Messiou C, van der Graaf WT, Gronchi A; Desmoid Working Group
Ann Oncol 2017 Oct 1;28(10):2399-2408. doi: 10.1093/annonc/mdx323. PMID: 28961825Free PMC Article

Clinical prediction guides

Mangla A, Agarwal N, Schwartz G
Curr Treat Options Oncol 2024 Feb;25(2):161-175. Epub 2024 Jan 25 doi: 10.1007/s11864-024-01177-5. PMID: 38270798Free PMC Article
Prendergast K, Kryeziu S, Crago AM
Surg Clin North Am 2022 Aug;102(4):667-677. doi: 10.1016/j.suc.2022.05.005. PMID: 35952695
Fiore M, Crago A, Gladdy R, Kasper B
Ann Surg Oncol 2021 Mar;28(3):1682-1689. Epub 2021 Jan 1 doi: 10.1245/s10434-020-09395-5. PMID: 33386543
Gounder MM, Thomas DM, Tap WD
J Clin Oncol 2018 Jan 10;36(2):202-209. Epub 2017 Dec 8 doi: 10.1200/JCO.2017.75.8482. PMID: 29220303Free PMC Article
Biermann JS
Curr Treat Options Oncol 2000 Aug;1(3):262-6. doi: 10.1007/s11864-000-0038-5. PMID: 12057169

Recent systematic reviews

van Maren SA, van Noesel MM, Husson O, van der Graaf WTA
Pediatr Blood Cancer 2022 Sep;69(9):e29831. Epub 2022 Jul 9 doi: 10.1002/pbc.29831. PMID: 35714333
Aelvoet AS, Struik D, Bastiaansen BAJ, Bemelman WA, Hompes R, Bossuyt PMM, Dekker E
Fam Cancer 2022 Oct;21(4):429-439. Epub 2022 Jan 13 doi: 10.1007/s10689-022-00288-y. PMID: 35022961Free PMC Article
Vázquez Fernández R, Maneiro Fernández JR, Cervantes Pérez EC, Mera Varela A
Ir J Med Sci 2021 Aug;190(3):1005-1014. Epub 2020 Oct 1 doi: 10.1007/s11845-020-02378-1. PMID: 33006046
Costa CRR, Braz SV, de Toledo IP, Martelli-Júnior H, Mazzeu JF, Guerra ENS, Coletta RD, Acevedo AC
Oral Dis 2021 May;27(4):881-893. Epub 2020 May 25 doi: 10.1111/odi.13369. PMID: 32335995
Coletta RD, Graner E
J Periodontol 2006 May;77(5):753-64. doi: 10.1902/jop.2006.050379. PMID: 16671866

Supplemental Content

Table of contents

    Clinical resources

    Practice guidelines

    • PubMed
      See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.
    • Bookshelf
      See practice and clinical guidelines in NCBI Bookshelf. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Recent activity

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...