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Advanced sclerotic lupus nephritis

MedGen UID:
885820
Concept ID:
C4053953
Disease or Syndrome
Synonyms: Class VI lupus nephritis; Systemic Lupus Erythematosus Nephritis Class VI
 
HPO: HP:0033732

Definition

A subclass of lupus nephritis with at least 90% of glomeruli globally sclerosed without residual activity. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVAdvanced sclerotic lupus nephritis

Professional guidelines

PubMed

Schena FP, Sallustio F, Serino G
Clin Sci (Lond) 2015 Jun;128(11):775-88. doi: 10.1042/CS20140733. PMID: 25881669

Recent clinical studies

Etiology

Li YJ, Wu HH, Liu SH, Tu KH, Lee CC, Hsu HH, Chang MY, Yu KH, Chen W, Tian YC
PLoS One 2019;14(1):e0210633. Epub 2019 Jan 14 doi: 10.1371/journal.pone.0210633. PMID: 30640964Free PMC Article
Wada Y, Matsumoto K, Suzuki T, Saito T, Kanazawa N, Tachibana S, Iseri K, Sugiyama M, Iyoda M, Shibata T
PLoS One 2018;13(11):e0206865. Epub 2018 Nov 2 doi: 10.1371/journal.pone.0206865. PMID: 30388165Free PMC Article
Weening JJ, D'Agati VD, Schwartz MM, Seshan SV, Alpers CE, Appel GB, Balow JE, Bruijn JA, Cook T, Ferrario F, Fogo AB, Ginzler EM, Hebert L, Hill G, Hill P, Jennette JC, Kong NC, Lesavre P, Lockshin M, Looi LM, Makino H, Moura LA, Nagata M; International Society of Nephrology Working Group on the Classification of Lupus Nephritis; Renal Pathology Society Working Group on the Classification of Lupus Nephritis
Kidney Int 2004 Feb;65(2):521-30. doi: 10.1111/j.1523-1755.2004.00443.x. PMID: 14717922

Diagnosis

Li YJ, Wu HH, Liu SH, Tu KH, Lee CC, Hsu HH, Chang MY, Yu KH, Chen W, Tian YC
PLoS One 2019;14(1):e0210633. Epub 2019 Jan 14 doi: 10.1371/journal.pone.0210633. PMID: 30640964Free PMC Article
Wada Y, Matsumoto K, Suzuki T, Saito T, Kanazawa N, Tachibana S, Iseri K, Sugiyama M, Iyoda M, Shibata T
PLoS One 2018;13(11):e0206865. Epub 2018 Nov 2 doi: 10.1371/journal.pone.0206865. PMID: 30388165Free PMC Article
Shariati-Sarabi Z, Ranjbar A, Monzavi SM, Esmaily H, Farzadnia M, Zeraati AA
Int J Rheum Dis 2013 Dec;16(6):731-8. Epub 2013 May 28 doi: 10.1111/1756-185X.12059. PMID: 24382282
Tervaert TW, Mooyaart AL, Amann K, Cohen AH, Cook HT, Drachenberg CB, Ferrario F, Fogo AB, Haas M, de Heer E, Joh K, Noël LH, Radhakrishnan J, Seshan SV, Bajema IM, Bruijn JA; Renal Pathology Society
J Am Soc Nephrol 2010 Apr;21(4):556-63. Epub 2010 Feb 18 doi: 10.1681/ASN.2010010010. PMID: 20167701
Weening JJ, D'Agati VD, Schwartz MM, Seshan SV, Alpers CE, Appel GB, Balow JE, Bruijn JA, Cook T, Ferrario F, Fogo AB, Ginzler EM, Hebert L, Hill G, Hill P, Jennette JC, Kong NC, Lesavre P, Lockshin M, Looi LM, Makino H, Moura LA, Nagata M; International Society of Nephrology Working Group on the Classification of Lupus Nephritis; Renal Pathology Society Working Group on the Classification of Lupus Nephritis
Kidney Int 2004 Feb;65(2):521-30. doi: 10.1111/j.1523-1755.2004.00443.x. PMID: 14717922

Therapy

Li D, Guo B, Wu H, Tan L, Chang C, Lu Q
Autoimmunity 2015;48(6):353-61. Epub 2015 Apr 20 doi: 10.3109/08916934.2015.1037441. PMID: 25894789
Schena FP, Sallustio F, Serino G
Clin Sci (Lond) 2015 Jun;128(11):775-88. doi: 10.1042/CS20140733. PMID: 25881669

Prognosis

Li YJ, Wu HH, Liu SH, Tu KH, Lee CC, Hsu HH, Chang MY, Yu KH, Chen W, Tian YC
PLoS One 2019;14(1):e0210633. Epub 2019 Jan 14 doi: 10.1371/journal.pone.0210633. PMID: 30640964Free PMC Article
Wada Y, Matsumoto K, Suzuki T, Saito T, Kanazawa N, Tachibana S, Iseri K, Sugiyama M, Iyoda M, Shibata T
PLoS One 2018;13(11):e0206865. Epub 2018 Nov 2 doi: 10.1371/journal.pone.0206865. PMID: 30388165Free PMC Article
Schena FP, Sallustio F, Serino G
Clin Sci (Lond) 2015 Jun;128(11):775-88. doi: 10.1042/CS20140733. PMID: 25881669
Shariati-Sarabi Z, Ranjbar A, Monzavi SM, Esmaily H, Farzadnia M, Zeraati AA
Int J Rheum Dis 2013 Dec;16(6):731-8. Epub 2013 May 28 doi: 10.1111/1756-185X.12059. PMID: 24382282
Grishman E, Gerber MA, Churg J
Am J Kidney Dis 1982 Jul;2(1 Suppl 1):135-41. PMID: 6213149

Clinical prediction guides

Li YJ, Wu HH, Liu SH, Tu KH, Lee CC, Hsu HH, Chang MY, Yu KH, Chen W, Tian YC
PLoS One 2019;14(1):e0210633. Epub 2019 Jan 14 doi: 10.1371/journal.pone.0210633. PMID: 30640964Free PMC Article
Wada Y, Matsumoto K, Suzuki T, Saito T, Kanazawa N, Tachibana S, Iseri K, Sugiyama M, Iyoda M, Shibata T
PLoS One 2018;13(11):e0206865. Epub 2018 Nov 2 doi: 10.1371/journal.pone.0206865. PMID: 30388165Free PMC Article
Shariati-Sarabi Z, Ranjbar A, Monzavi SM, Esmaily H, Farzadnia M, Zeraati AA
Int J Rheum Dis 2013 Dec;16(6):731-8. Epub 2013 May 28 doi: 10.1111/1756-185X.12059. PMID: 24382282
Tanji N, Markowitz GS, Fu C, Kislinger T, Taguchi A, Pischetsrieder M, Stern D, Schmidt AM, D'Agati VD
J Am Soc Nephrol 2000 Sep;11(9):1656-1666. doi: 10.1681/ASN.V1191656. PMID: 10966490
Lhotta K, Würzner R, König P
Nephrol Dial Transplant 1999 Apr;14(4):881-6. doi: 10.1093/ndt/14.4.881. PMID: 10328463

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