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Pancreaticobiliary Malunion

MedGen UID:
887240
Concept ID:
C4054251
Disease or Syndrome

Definition

An abnormality of the pancreatic and biliary ducts in which their junction occurs above the duodenal wall. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVPancreaticobiliary Malunion

Recent clinical studies

Etiology

Cazares J, Koga H, Yamataka A
Pediatr Surg Int 2023 Jun 1;39(1):209. doi: 10.1007/s00383-023-05483-1. PMID: 37261604
Matsumura T, Komatsu S, Komaya K, Fukami Y, Arikawa T, Saito T, Osawa T, Kurahashi S, Uchino T, Kato S, Toda Y, Kaneko K, Sano T
Surg Endosc 2021 Jul;35(7):3379-3386. Epub 2020 Jul 9 doi: 10.1007/s00464-020-07779-y. PMID: 32648039
Diao M, Li L, Cheng W
J Pediatr Surg 2011 Aug;46(8):1503-9. doi: 10.1016/j.jpedsurg.2010.12.022. PMID: 21843715
Obara T, Tanno S, Fujii T, Izawa T, Mizukami Y, Yanagawa N, Ura H, Kohgo Y
J Hepatobiliary Pancreat Surg 1999;6(3):229-36. doi: 10.1007/s005340050112. PMID: 10526057
Watanabe Y, Toki A, Todani T
J Hepatobiliary Pancreat Surg 1999;6(3):207-12. doi: 10.1007/s005340050108. PMID: 10526053

Diagnosis

Cazares J, Koga H, Yamataka A
Pediatr Surg Int 2023 Jun 1;39(1):209. doi: 10.1007/s00383-023-05483-1. PMID: 37261604
Matsumura T, Komatsu S, Komaya K, Fukami Y, Arikawa T, Saito T, Osawa T, Kurahashi S, Uchino T, Kato S, Toda Y, Kaneko K, Sano T
Surg Endosc 2021 Jul;35(7):3379-3386. Epub 2020 Jul 9 doi: 10.1007/s00464-020-07779-y. PMID: 32648039
Saeed A, El Mouzan M, Assiri A, Alsarkhy A, Majeed K
J Coll Physicians Surg Pak 2014 Nov;24 Suppl 3:S250-2. PMID: 25518792
Ohtsuka T, Inoue K, Ohuchida J, Nabae T, Takahata S, Niiyama H, Yokohata K, Ogawa Y, Yamaguchi K, Chijiiwa K, Tanaka M
Endoscopy 2001 Jul;33(7):614-9. doi: 10.1055/s-2001-15324. PMID: 11473335
Miyano T, Yamataka A, Li L
Semin Pediatr Surg 2000 Nov;9(4):187-95. doi: 10.1053/spsu.2000.18843. PMID: 11112836

Therapy

Matsumura T, Komatsu S, Komaya K, Fukami Y, Arikawa T, Saito T, Osawa T, Kurahashi S, Uchino T, Kato S, Toda Y, Kaneko K, Sano T
Surg Endosc 2021 Jul;35(7):3379-3386. Epub 2020 Jul 9 doi: 10.1007/s00464-020-07779-y. PMID: 32648039

Prognosis

Saeed A, El Mouzan M, Assiri A, Alsarkhy A, Majeed K
J Coll Physicians Surg Pak 2014 Nov;24 Suppl 3:S250-2. PMID: 25518792
Lao OB, Stein S, Ely KA, Lovvorn HN 3rd
Pediatr Surg Int 2008 Jul;24(7):859-62. Epub 2008 Apr 26 doi: 10.1007/s00383-008-2162-4. PMID: 18438673
Miyano G, Yamataka A, Shimotakahara A, Kobayashi H, Lane GJ, Miyano T
Pediatr Surg Int 2005 Jan;21(1):61-3. doi: 10.1007/s00383-004-1266-8. PMID: 15316725
Shimotakahara A, Yamataka A, Kobayashi H, Okada Y, Yanai T, Lane GJ, Miyano T
J Pediatr Surg 2003 Dec;38(12):1833-6. doi: 10.1016/j.jpedsurg.2003.08.026. PMID: 14666480
Watanabe Y, Toki A, Todani T
J Hepatobiliary Pancreat Surg 1999;6(3):207-12. doi: 10.1007/s005340050108. PMID: 10526053

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