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Pauci-Immune Glomerulonephritis associated with Microscopic Polyangiitis

MedGen UID:
889022
Concept ID:
C4054224
Disease or Syndrome

Definition

Glomerulonephritis in the context of systemic, small vessel vasculitis in which anti neutrophil cytoplasm antibody (ANCA) is almost always present. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVPauci-Immune Glomerulonephritis associated with Microscopic Polyangiitis

Professional guidelines

PubMed

Suppiah R, Robson JC, Grayson PC, Ponte C, Craven A, Khalid S, Judge A, Hutchings A, Merkel PA, Luqmani RA, Watts RA; DCVAS INVESTIGATORS
Ann Rheum Dis 2022 Mar;81(3):321-326. Epub 2022 Feb 2 doi: 10.1136/annrheumdis-2021-221796. PMID: 35110332
Suppiah R, Robson JC, Grayson PC, Ponte C, Craven A, Khalid S, Judge A, Hutchings A, Merkel PA, Luqmani RA, Watts RA; DCVAS Study Group
Arthritis Rheumatol 2022 Mar;74(3):400-406. Epub 2022 Feb 2 doi: 10.1002/art.41983. PMID: 35106973
Haubitz M
Vasa 2007 May;36(2):81-9. doi: 10.1024/0301-1526.36.2.81. PMID: 17708098

Recent clinical studies

Etiology

Suppiah R, Robson JC, Grayson PC, Ponte C, Craven A, Khalid S, Judge A, Hutchings A, Merkel PA, Luqmani RA, Watts RA; DCVAS INVESTIGATORS
Ann Rheum Dis 2022 Mar;81(3):321-326. Epub 2022 Feb 2 doi: 10.1136/annrheumdis-2021-221796. PMID: 35110332
Suppiah R, Robson JC, Grayson PC, Ponte C, Craven A, Khalid S, Judge A, Hutchings A, Merkel PA, Luqmani RA, Watts RA; DCVAS Study Group
Arthritis Rheumatol 2022 Mar;74(3):400-406. Epub 2022 Feb 2 doi: 10.1002/art.41983. PMID: 35106973
Jennette JC, Nachman PH
Clin J Am Soc Nephrol 2017 Oct 6;12(10):1680-1691. Epub 2017 Aug 25 doi: 10.2215/CJN.02500317. PMID: 28842398Free PMC Article
Scaglioni V, Scolnik M, Catoggio LJ, Christiansen SB, Varela CF, Greloni G, Rosa-Diez G, Soriano ER
Clin Exp Rheumatol 2017 Mar-Apr;35 Suppl 103(1):55-58. Epub 2017 Jan 31 PMID: 28229825
Tervaert JW, Stegeman CA, Kallenberg CG
Curr Opin Rheumatol 1998 Jan;10(1):12-7. doi: 10.1097/00002281-199801000-00003. PMID: 9448985

Diagnosis

Suppiah R, Robson JC, Grayson PC, Ponte C, Craven A, Khalid S, Judge A, Hutchings A, Merkel PA, Luqmani RA, Watts RA; DCVAS INVESTIGATORS
Ann Rheum Dis 2022 Mar;81(3):321-326. Epub 2022 Feb 2 doi: 10.1136/annrheumdis-2021-221796. PMID: 35110332
Suppiah R, Robson JC, Grayson PC, Ponte C, Craven A, Khalid S, Judge A, Hutchings A, Merkel PA, Luqmani RA, Watts RA; DCVAS Study Group
Arthritis Rheumatol 2022 Mar;74(3):400-406. Epub 2022 Feb 2 doi: 10.1002/art.41983. PMID: 35106973
Tobiáš D, Brázdilová K, Killinger Z, Payer J
Vnitr Lek 2020 Summer;66(4):249-252. PMID: 32972189
Jennette JC, Nachman PH
Clin J Am Soc Nephrol 2017 Oct 6;12(10):1680-1691. Epub 2017 Aug 25 doi: 10.2215/CJN.02500317. PMID: 28842398Free PMC Article
Scaglioni V, Scolnik M, Catoggio LJ, Christiansen SB, Varela CF, Greloni G, Rosa-Diez G, Soriano ER
Clin Exp Rheumatol 2017 Mar-Apr;35 Suppl 103(1):55-58. Epub 2017 Jan 31 PMID: 28229825

Therapy

Jennette JC, Nachman PH
Clin J Am Soc Nephrol 2017 Oct 6;12(10):1680-1691. Epub 2017 Aug 25 doi: 10.2215/CJN.02500317. PMID: 28842398Free PMC Article
Kallenberg CG
J Autoimmun 2014 Feb-Mar;48-49:90-3. Epub 2014 Jan 22 doi: 10.1016/j.jaut.2014.01.023. PMID: 24461388
Rutgers A, Sanders JS, Stegeman CA, Kallenberg CG
Rheum Dis Clin North Am 2010 Aug;36(3):559-72. doi: 10.1016/j.rdc.2010.05.002. PMID: 20688250
Langford CA, Balow JE
Curr Opin Nephrol Hypertens 2003 May;12(3):267-72. doi: 10.1097/00041552-200305000-00007. PMID: 12698064
Tervaert JW, Stegeman CA, Kallenberg CG
Curr Opin Rheumatol 1998 Jan;10(1):12-7. doi: 10.1097/00002281-199801000-00003. PMID: 9448985

Prognosis

Zonozi R, Niles JL, Cortazar FB
Rheum Dis Clin North Am 2018 Nov;44(4):525-543. Epub 2018 Sep 7 doi: 10.1016/j.rdc.2018.06.001. PMID: 30274621
Naidu GS, Sharma A, Nada R, Kohli HS, Jha V, Gupta KL, Sakhuja V, Rathi M
Rheumatol Int 2014 Dec;34(12):1721-7. Epub 2014 May 18 doi: 10.1007/s00296-014-3041-z. PMID: 24838685
Kallenberg CG
J Autoimmun 2014 Feb-Mar;48-49:90-3. Epub 2014 Jan 22 doi: 10.1016/j.jaut.2014.01.023. PMID: 24461388
Rutgers A, Sanders JS, Stegeman CA, Kallenberg CG
Rheum Dis Clin North Am 2010 Aug;36(3):559-72. doi: 10.1016/j.rdc.2010.05.002. PMID: 20688250
Peco-Antic A, Bonaci-Nikolic B, Basta-Jovanovic G, Kostic M, Markovic-Lipkovski J, Nikolic M, Spasojevic B
Pediatr Nephrol 2006 Jan;21(1):46-53. Epub 2005 Oct 27 doi: 10.1007/s00467-005-2063-x. PMID: 16252100

Clinical prediction guides

Suppiah R, Robson JC, Grayson PC, Ponte C, Craven A, Khalid S, Judge A, Hutchings A, Merkel PA, Luqmani RA, Watts RA; DCVAS INVESTIGATORS
Ann Rheum Dis 2022 Mar;81(3):321-326. Epub 2022 Feb 2 doi: 10.1136/annrheumdis-2021-221796. PMID: 35110332
Suppiah R, Robson JC, Grayson PC, Ponte C, Craven A, Khalid S, Judge A, Hutchings A, Merkel PA, Luqmani RA, Watts RA; DCVAS Study Group
Arthritis Rheumatol 2022 Mar;74(3):400-406. Epub 2022 Feb 2 doi: 10.1002/art.41983. PMID: 35106973
Naidu GS, Sharma A, Nada R, Kohli HS, Jha V, Gupta KL, Sakhuja V, Rathi M
Rheumatol Int 2014 Dec;34(12):1721-7. Epub 2014 May 18 doi: 10.1007/s00296-014-3041-z. PMID: 24838685
Sinico RA, Di Toma L, Radice A
Autoimmun Rev 2013 Feb;12(4):477-82. Epub 2012 Aug 16 doi: 10.1016/j.autrev.2012.08.006. PMID: 22921791
Peco-Antic A, Bonaci-Nikolic B, Basta-Jovanovic G, Kostic M, Markovic-Lipkovski J, Nikolic M, Spasojevic B
Pediatr Nephrol 2006 Jan;21(1):46-53. Epub 2005 Oct 27 doi: 10.1007/s00467-005-2063-x. PMID: 16252100

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