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Meningothelial meningioma

MedGen UID:
90814
Concept ID:
C0334605
Neoplastic Process
Synonyms: Meningioma, Meningotheliomatous; Meningiomas, Meningotheliomatous; Meningotheliomatous Meningioma; Meningotheliomatous Meningiomas
SNOMED CT: Endotheliomatous meningioma (68944005); Syncytial meningioma (68944005); Meningothelial meningioma (68944005)
 
Monarch Initiative: MONDO:0004145

Definition

A WHO grade I meningioma characterized by the presence of tumor cells that form lobules. The tumor cells are generally uniform. Whorls and psammoma bodies are usually not present. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVMeningothelial meningioma

Professional guidelines

PubMed

Marc JA, Takei Y, Schechter MM, Hoffman JC
Am J Roentgenol Radium Ther Nucl Med 1975 Dec;125(4):823-32. doi: 10.2214/ajr.125.4.823. PMID: 1211512

Recent clinical studies

Etiology

Chew SJY, Rajesvaran C, Woo X, Goh CH
Malays J Pathol 2021 Dec;43(3):453-456. PMID: 34958067
Aoyama T, Ogiwara T, Ito K, Miyaoka Y, Fujii Y, Hanaoka Y, Hasegawa T, Watanabe G, Seguchi T, Hongo K
Acta Med Okayama 2021 Dec;75(6):713-718. doi: 10.18926/AMO/62811. PMID: 34955539
Takamura T, Motosugi U, Ogiwara M, Sasaki Y, Glaser KJ, Ehman RL, Kinouchi H, Onishi H
AJNR Am J Neuroradiol 2021 Jul;42(7):1216-1222. Epub 2021 May 13 doi: 10.3174/ajnr.A7117. PMID: 33985944Free PMC Article
Altunrende ME, Göker B, Dolgun M, Akçakaya MO, Kasımcan MÖ, Şencan F, Hamamcıoğlu MK, Kırış T
Neurocirugia (Astur : Engl Ed) 2019 Jul-Aug;30(4):159-166. Epub 2019 Feb 18 doi: 10.1016/j.neucir.2019.01.003. PMID: 30792109
Elbabaa SK, Gokden M, Crawford JR, Kesari S, Saad AG
J Neurosurg Pediatr 2012 Oct;10(4):281-90. Epub 2012 Aug 17 doi: 10.3171/2012.7.PEDS1251. PMID: 22900483

Diagnosis

Zheng X, Guo S, Liu D, Chu J, Li Y, Wang X, Zhang X, Song C, Huang Q
BMC Pediatr 2022 Dec 3;22(1):694. doi: 10.1186/s12887-022-03747-8. PMID: 36463108Free PMC Article
Wen D, Xu D, Wang L, Chen Y, Ou C
J Craniofac Surg 2022 Nov-Dec 01;33(8):e837-e840. Epub 2022 Jul 26 doi: 10.1097/SCS.0000000000008766. PMID: 35882350
Ersoz S, Yilmaz ZS, Eyuboglu I, Yazar U
Turk Neurosurg 2019;29(1):141-144. doi: 10.5137/1019-5149.JTN.19561-16.1. PMID: 28191624
Ishida M, Fukami T, Nitta N, Iwai M, Yoshida K, Kagotani A, Nozaki K, Okabe H
Int J Clin Exp Pathol 2013;6(10):2242-6. Epub 2013 Sep 15 PMID: 24133605Free PMC Article
Inoue T, Kuromatsu C, Sawada K, Matsushima T
Surg Neurol 1986 Oct;26(4):399-404. doi: 10.1016/0090-3019(86)90145-x. PMID: 3750200

Therapy

Niu L, Zhou X, Duan C, Zhao J, Sui Q, Liu X, Zhang X
World Neurosurg 2019 Jun;126:e646-e652. Epub 2019 Mar 1 doi: 10.1016/j.wneu.2019.02.109. PMID: 30831287
Celtikci E, Kaymaz AM, Akgul G, Karaaslan B, Emmez OH, Borcek A
Turk Neurosurg 2018;28(1):1-6. doi: 10.5137/1019-5149.JTN.17866-16.1. PMID: 27593846
Weller M, Roth P, Sahm F, Burghardt I, Schuknecht B, Rushing EJ, Regli L, Lindemann JP, von Deimling A
J Natl Cancer Inst 2017 Mar 1;109(3):1-4. doi: 10.1093/jnci/djw320. PMID: 28376212
Balik V, Sarissky M, Lohmann D, Sulla I
Zentralbl Neurochir 2008 Nov;69(4):194-9. Epub 2008 Jul 29 doi: 10.1055/s-2008-1077079. PMID: 18666063
Batay F, Al-Mefty O
Acta Neurochir (Wien) 2002 Apr;144(4):365-8. doi: 10.1007/s007010200050. PMID: 12021883

Prognosis

Chew SJY, Rajesvaran C, Woo X, Goh CH
Malays J Pathol 2021 Dec;43(3):453-456. PMID: 34958067
Takamura T, Motosugi U, Ogiwara M, Sasaki Y, Glaser KJ, Ehman RL, Kinouchi H, Onishi H
AJNR Am J Neuroradiol 2021 Jul;42(7):1216-1222. Epub 2021 May 13 doi: 10.3174/ajnr.A7117. PMID: 33985944Free PMC Article
Berghoff AS, Kresl P, Rajky O, Widhalm G, Ricken G, Hainfellner JA, Marosi C, Birner P, Preusser M
Clin Neuropathol 2020 Nov/Dec;39(6):256-262. doi: 10.5414/NP301156. PMID: 32831157
Smith MJ, Ahn S, Lee JI, Bulman M, Plessis DD, Suh YL
Histopathology 2017 Apr;70(5):814-820. Epub 2017 Feb 2 doi: 10.1111/his.13135. PMID: 27891692
Righi V, Tugnoli V, Mucci A, Bacci A, Bonora S, Schenetti L
Oncol Rep 2012 Oct;28(4):1461-7. Epub 2012 Jul 19 doi: 10.3892/or.2012.1919. PMID: 22824994

Clinical prediction guides

Chew SJY, Rajesvaran C, Woo X, Goh CH
Malays J Pathol 2021 Dec;43(3):453-456. PMID: 34958067
Lee I, Kong JS, Youn SM, Lim I, Ha JH
Clin Nucl Med 2021 Aug 1;46(8):e431-e432. doi: 10.1097/RLU.0000000000003565. PMID: 33661207
Berghoff AS, Kresl P, Rajky O, Widhalm G, Ricken G, Hainfellner JA, Marosi C, Birner P, Preusser M
Clin Neuropathol 2020 Nov/Dec;39(6):256-262. doi: 10.5414/NP301156. PMID: 32831157
Ersoz S, Yilmaz ZS, Eyuboglu I, Yazar U
Turk Neurosurg 2019;29(1):141-144. doi: 10.5137/1019-5149.JTN.19561-16.1. PMID: 28191624
Righi V, Tugnoli V, Mucci A, Bacci A, Bonora S, Schenetti L
Oncol Rep 2012 Oct;28(4):1461-7. Epub 2012 Jul 19 doi: 10.3892/or.2012.1919. PMID: 22824994

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