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Darier sign

MedGen UID:
909963
Concept ID:
C0878658
Sign or Symptom
Synonym: Darier's sign
 
HPO: HP:0025081

Definition

A skin change elicited by briskly rubbing the skin lesion in urticaria pigmentosa (UP), whereby the area begins to itch and becomes raised and surrounded by erythema. Unlike other forms of dermatographism, Darier's sign refers to urtication that is limited to the UP involved areas and, as in this case, spares the skin unaffected by UP. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVDarier sign

Professional guidelines

PubMed

Leung AKC, Lam JM, Leong KF
Curr Pediatr Rev 2019;15(1):42-46. doi: 10.2174/1573396315666181120163952. PMID: 30465511Free PMC Article

Recent clinical studies

Etiology

Santosh T, Sharma T, Patra S, Asati DP, Chaurasia JK, Joshi D, Kapoor N
Indian J Pathol Microbiol 2021 Jul-Sep;64(3):587-590. doi: 10.4103/IJPM.IJPM_970_20. PMID: 34341280
Mashiah J, Harel A, Bodemer C, Hadj-Rabia S, Goldberg I, Sprecher E, Kutz A
Clin Exp Dermatol 2018 Jul;43(5):559-565. Epub 2018 Feb 20 doi: 10.1111/ced.13391. PMID: 29460435
Ray S, Mukherjee A, Chatterjee N, Alam MA
J Indian Med Assoc 2011 May;109(5):354-5. PMID: 22187777

Diagnosis

Marín-Hernández E, Ramírez-Rico A
Bol Med Hosp Infant Mex 2022;79(5):326-333. doi: 10.24875/BMHIM.21000177. PMID: 36264918
Tampouratzi L, Kanni T, Katsantonis J, Douvali T
Acta Dermatovenerol Croat 2021 Apr;291(1):60-61. PMID: 34477069
Der Sarkissian SA, Sebaratnam DF
Med J Aust 2021 Mar;214(5):206. doi: 10.5694/mja2.50947. PMID: 33715187
Leung AKC, Lam JM, Leong KF
Curr Pediatr Rev 2019;15(1):42-46. doi: 10.2174/1573396315666181120163952. PMID: 30465511Free PMC Article
Mashiah J, Harel A, Bodemer C, Hadj-Rabia S, Goldberg I, Sprecher E, Kutz A
Clin Exp Dermatol 2018 Jul;43(5):559-565. Epub 2018 Feb 20 doi: 10.1111/ced.13391. PMID: 29460435

Therapy

Tampouratzi L, Kanni T, Katsantonis J, Douvali T
Acta Dermatovenerol Croat 2021 Apr;291(1):60-61. PMID: 34477069
Leonard N, Lal K, Luffman C, O'Donnell P, Jolley L, Belazarian L
Pediatr Dermatol 2021 Mar;38(2):494-496. Epub 2020 Dec 18 doi: 10.1111/pde.14488. PMID: 33336458
Leung AKC, Lam JM, Leong KF
Curr Pediatr Rev 2019;15(1):42-46. doi: 10.2174/1573396315666181120163952. PMID: 30465511Free PMC Article
Mashiah J, Harel A, Bodemer C, Hadj-Rabia S, Goldberg I, Sprecher E, Kutz A
Clin Exp Dermatol 2018 Jul;43(5):559-565. Epub 2018 Feb 20 doi: 10.1111/ced.13391. PMID: 29460435
Correia O, Duarte AF, Quirino P, Azevedo R, Delgado L
Dermatol Online J 2010 May 15;16(5):8. PMID: 20492825

Prognosis

Santosh T, Sharma T, Patra S, Asati DP, Chaurasia JK, Joshi D, Kapoor N
Indian J Pathol Microbiol 2021 Jul-Sep;64(3):587-590. doi: 10.4103/IJPM.IJPM_970_20. PMID: 34341280

Clinical prediction guides

Marín-Hernández E, Ramírez-Rico A
Bol Med Hosp Infant Mex 2022;79(5):326-333. doi: 10.24875/BMHIM.21000177. PMID: 36264918
Leung AKC, Lam JM, Leong KF
Curr Pediatr Rev 2019;15(1):42-46. doi: 10.2174/1573396315666181120163952. PMID: 30465511Free PMC Article
Mashiah J, Harel A, Bodemer C, Hadj-Rabia S, Goldberg I, Sprecher E, Kutz A
Clin Exp Dermatol 2018 Jul;43(5):559-565. Epub 2018 Feb 20 doi: 10.1111/ced.13391. PMID: 29460435
Sharquie KE, Al-Dhalimi MA
Dermatol Surg 2003 Aug;29(8):847-51. doi: 10.1046/j.1524-4725.2003.29230.x. PMID: 12859386

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