Etiology
Jaïs X,
Brenot P,
Bouvaist H,
Jevnikar M,
Canuet M,
Chabanne C,
Chaouat A,
Cottin V,
De Groote P,
Favrolt N,
Horeau-Langlard D,
Magro P,
Savale L,
Prévot G,
Renard S,
Sitbon O,
Parent F,
Trésorier R,
Tromeur C,
Piedvache C,
Grimaldi L,
Fadel E,
Montani D,
Humbert M,
Simonneau G
Lancet Respir Med
2022 Oct;10(10):961-971.
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Obokata M,
Reddy YNV,
Verbrugge FH,
Omar M,
DuBrock HM,
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Eur Heart J
2022 Sep 21;43(36):3417-3431.
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Luna-López R,
Ruiz Martín A,
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Med Clin (Barc)
2022 Jun 24;158(12):622-629.
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Anjum H,
Surani S
Medicina (Kaunas)
2021 Mar 11;57(3)
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Hoeper MM,
Bogaard HJ,
Condliffe R,
Frantz R,
Khanna D,
Kurzyna M,
Langleben D,
Manes A,
Satoh T,
Torres F,
Wilkins MR,
Badesch DB
J Am Coll Cardiol
2013 Dec 24;62(25 Suppl):D42-50.
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PMID: 24355641
Diagnosis
Luna-López R,
Ruiz Martín A,
Escribano Subías P
Med Clin (Barc)
2022 Jun 24;158(12):622-629.
Epub 2022 Mar 9
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PMID: 35279313
Beshay S,
Sahay S,
Humbert M
Respir Med
2020 Sep;171:106099.
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Pascall E,
Tulloh RM
Future Cardiol
2018 Jul;14(4):343-353.
Epub 2018 May 24
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PMID: 29792339Free PMC Article
Hoeper MM,
Bogaard HJ,
Condliffe R,
Frantz R,
Khanna D,
Kurzyna M,
Langleben D,
Manes A,
Satoh T,
Torres F,
Wilkins MR,
Badesch DB
J Am Coll Cardiol
2013 Dec 24;62(25 Suppl):D42-50.
doi: 10.1016/j.jacc.2013.10.032.
PMID: 24355641
Duggan M,
Kavanagh BP
Anesthesiology
2005 Apr;102(4):838-54.
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PMID: 15791115
Therapy
Hoeper MM,
Badesch DB,
Ghofrani HA,
Gibbs JSR,
Gomberg-Maitland M,
McLaughlin VV,
Preston IR,
Souza R,
Waxman AB,
Grünig E,
Kopeć G,
Meyer G,
Olsson KM,
Rosenkranz S,
Xu Y,
Miller B,
Fowler M,
Butler J,
Koglin J,
de Oliveira Pena J,
Humbert M;
STELLAR Trial Investigators
N Engl J Med
2023 Apr 20;388(16):1478-1490.
Epub 2023 Mar 6
doi: 10.1056/NEJMoa2213558.
PMID: 36877098
Zhang H,
Wei Y,
Zhang C,
Yang Z,
Kan J,
Gu H,
Fan F,
Gu H,
Wang Q,
Xie D,
Zhang G,
Guo X,
Yin Y,
Jin B,
Zhou H,
Yang Z,
Wang Z,
Xin Y,
Zhang C,
Meng L,
Wang X,
Sun J,
Zhao C,
Zhang J,
Yan X,
Chen F,
Yao C,
Stone GW,
Chen SL
JACC Cardiovasc Interv
2022 Dec 12;15(23):2412-2423.
Epub 2022 Sep 18
doi: 10.1016/j.jcin.2022.09.013.
PMID: 36121246
Jaïs X,
Brenot P,
Bouvaist H,
Jevnikar M,
Canuet M,
Chabanne C,
Chaouat A,
Cottin V,
De Groote P,
Favrolt N,
Horeau-Langlard D,
Magro P,
Savale L,
Prévot G,
Renard S,
Sitbon O,
Parent F,
Trésorier R,
Tromeur C,
Piedvache C,
Grimaldi L,
Fadel E,
Montani D,
Humbert M,
Simonneau G
Lancet Respir Med
2022 Oct;10(10):961-971.
Epub 2022 Aug 1
doi: 10.1016/S2213-2600(22)00214-4.
PMID: 35926542
Humbert M,
McLaughlin V,
Gibbs JSR,
Gomberg-Maitland M,
Hoeper MM,
Preston IR,
Souza R,
Waxman A,
Escribano Subias P,
Feldman J,
Meyer G,
Montani D,
Olsson KM,
Manimaran S,
Barnes J,
Linde PG,
de Oliveira Pena J,
Badesch DB;
PULSAR Trial Investigators
N Engl J Med
2021 Apr 1;384(13):1204-1215.
doi: 10.1056/NEJMoa2024277.
PMID: 33789009
Ghofrani HA,
Galiè N,
Grimminger F,
Grünig E,
Humbert M,
Jing ZC,
Keogh AM,
Langleben D,
Kilama MO,
Fritsch A,
Neuser D,
Rubin LJ;
PATENT-1 Study Group
N Engl J Med
2013 Jul 25;369(4):330-40.
doi: 10.1056/NEJMoa1209655.
PMID: 23883378
Prognosis
Jaïs X,
Brenot P,
Bouvaist H,
Jevnikar M,
Canuet M,
Chabanne C,
Chaouat A,
Cottin V,
De Groote P,
Favrolt N,
Horeau-Langlard D,
Magro P,
Savale L,
Prévot G,
Renard S,
Sitbon O,
Parent F,
Trésorier R,
Tromeur C,
Piedvache C,
Grimaldi L,
Fadel E,
Montani D,
Humbert M,
Simonneau G
Lancet Respir Med
2022 Oct;10(10):961-971.
Epub 2022 Aug 1
doi: 10.1016/S2213-2600(22)00214-4.
PMID: 35926542
Suzuki S,
Asano R,
Aoki T,
Nakayama S,
Ueda J,
Tsuji A,
Noguchi T,
Ogo T
Open Heart
2022 Jun;9(1)
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PMID: 35675988Free PMC Article
Beshay S,
Sahay S,
Humbert M
Respir Med
2020 Sep;171:106099.
Epub 2020 Aug 19
doi: 10.1016/j.rmed.2020.106099.
PMID: 32829182
Ivy DD,
Abman SH,
Barst RJ,
Berger RM,
Bonnet D,
Fleming TR,
Haworth SG,
Raj JU,
Rosenzweig EB,
Schulze Neick I,
Steinhorn RH,
Beghetti M
J Am Coll Cardiol
2013 Dec 24;62(25 Suppl):D117-26.
doi: 10.1016/j.jacc.2013.10.028.
PMID: 24355636
Razuin R,
Effat O,
Shahidan MN,
Shama DV,
Miswan MF
Malays J Pathol
2013 Jun;35(1):87-90.
PMID: 23817399
Clinical prediction guides
Jaïs X,
Brenot P,
Bouvaist H,
Jevnikar M,
Canuet M,
Chabanne C,
Chaouat A,
Cottin V,
De Groote P,
Favrolt N,
Horeau-Langlard D,
Magro P,
Savale L,
Prévot G,
Renard S,
Sitbon O,
Parent F,
Trésorier R,
Tromeur C,
Piedvache C,
Grimaldi L,
Fadel E,
Montani D,
Humbert M,
Simonneau G
Lancet Respir Med
2022 Oct;10(10):961-971.
Epub 2022 Aug 1
doi: 10.1016/S2213-2600(22)00214-4.
PMID: 35926542
DuBrock HM,
Cartin-Ceba R,
Channick RN,
Kawut SM,
Krowka MJ
Chest
2021 Jan;159(1):328-336.
Epub 2020 Aug 13
doi: 10.1016/j.chest.2020.07.081.
PMID: 32798521Free PMC Article
Kwan WC,
Shavelle DM,
Laughrun DR
Clin Cardiol
2019 Mar;42(3):334-338.
Epub 2019 Feb 27
doi: 10.1002/clc.23151.
PMID: 30614019Free PMC Article
Wright LM,
Dwyer N,
Celermajer D,
Kritharides L,
Marwick TH
JACC Cardiovasc Imaging
2016 Jun;9(6):733-46.
doi: 10.1016/j.jcmg.2016.02.022.
PMID: 27282440
Naeije R,
D'Alto M,
Forfia PR
Prog Cardiovasc Dis
2015 Mar-Apr;57(5):463-72.
Epub 2014 Dec 19
doi: 10.1016/j.pcad.2014.12.003.
PMID: 25534670