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Conventional Extraskeletal Myxoid Chondrosarcoma

MedGen UID:
234486
Concept ID:
C1337010
Neoplastic Process
Synonyms: Extraskeletal Well Differentiated Myxoid Chondrosarcoma; Well Differentiated Extraosseous Myxoid Chondrosarcoma; Well Differentiated Extraskeletal Myxoid Chondrosarcoma

Definition

A well differentiated extraskeletal myxoid chondrosarcoma. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVConventional Extraskeletal Myxoid Chondrosarcoma

Recent clinical studies

Etiology

Terlizzi M, Le Pechoux C, Salas S, Rapeaud E, Lerouge D, Sunyach MP, Vogin G, Sole CV, Zilli T, Lutsyk M, Mampuya A, Calvo FA, Attal J, Karahissarlian V, De Bari B, Ozsahin M, Baumard F, Krengli M, Gomez-Brouchet A, Sargos P, Rochcongar G, Bazille C, Roth V, Salleron J, Thariat J
Int J Radiat Oncol Biol Phys 2020 Jul 15;107(4):726-735. Epub 2020 Apr 11 doi: 10.1016/j.ijrobp.2020.03.041. PMID: 32289473
Chow W, Frankel P, Ruel C, Araujo DM, Milhem M, Okuno S, Hartner L, Undevia S, Staddon A
Cancer 2020 Jan 1;126(1):105-111. Epub 2019 Sep 11 doi: 10.1002/cncr.32515. PMID: 31509242
Jones RL, Katz D, Loggers ET, Davidson D, Rodler ET, Pollack SM
Med Oncol 2017 Aug 29;34(10):167. doi: 10.1007/s12032-017-1030-2. PMID: 28852958Free PMC Article
Rekhi B, Vogel U, Basak R, Desai SB, Jambhekar NA
Pathol Oncol Res 2014 Jul;20(3):503-16. Epub 2013 Nov 30 doi: 10.1007/s12253-013-9721-2. PMID: 24293381
Chow WA
Curr Opin Oncol 2007 Jul;19(4):371-6. doi: 10.1097/CCO.0b013e32812143d9. PMID: 17545802

Diagnosis

Toland AMS, Lam SW, Varma S, Wang A, Howitt BE, Kunder CA, Kerr DA, Szuhai K, Bovée JVMG, Charville GW
Am J Surg Pathol 2022 Oct 1;46(10):1407-1414. Epub 2022 Jun 1 doi: 10.1097/PAS.0000000000001921. PMID: 35650682Free PMC Article
Lanic MD, Le Loarer F, Rainville V, Sater V, Viennot M, Beaussire L, Viailly PJ, Angot E, Hostein I, Jardin F, Ruminy P, Laé M
Mod Pathol 2022 May;35(5):649-663. Epub 2022 Jan 24 doi: 10.1038/s41379-021-00980-x. PMID: 35075283
Veselis CA, Awan O, Thomas A, Ling S, Jonnalagadda P, Aneja A, Ali S
Curr Probl Diagn Radiol 2021 May-Jun;50(3):419-429. Epub 2020 Jun 26 doi: 10.1067/j.cpradiol.2020.06.004. PMID: 32665061
Velz J, Agaimy A, Frontzek K, Neidert MC, Bozinov O, Wagner U, Fritz C, Coras R, Hofer S, Bode-Lesniewska B, Rushing E
J Neuropathol Exp Neurol 2018 Aug 1;77(8):727-735. doi: 10.1093/jnen/nly050. PMID: 29924341
Okamoto S, Hisaoka M, Ishida T, Imamura T, Kanda H, Shimajiri S, Hashimoto H
Hum Pathol 2001 Oct;32(10):1116-24. doi: 10.1053/hupa.2001.28226. PMID: 11679947

Therapy

Chow W, Frankel P, Ruel C, Araujo DM, Milhem M, Okuno S, Hartner L, Undevia S, Staddon A
Cancer 2020 Jan 1;126(1):105-111. Epub 2019 Sep 11 doi: 10.1002/cncr.32515. PMID: 31509242
Jones RL, Katz D, Loggers ET, Davidson D, Rodler ET, Pollack SM
Med Oncol 2017 Aug 29;34(10):167. doi: 10.1007/s12032-017-1030-2. PMID: 28852958Free PMC Article

Prognosis

Veselis CA, Awan O, Thomas A, Ling S, Jonnalagadda P, Aneja A, Ali S
Curr Probl Diagn Radiol 2021 May-Jun;50(3):419-429. Epub 2020 Jun 26 doi: 10.1067/j.cpradiol.2020.06.004. PMID: 32665061
Velz J, Agaimy A, Frontzek K, Neidert MC, Bozinov O, Wagner U, Fritz C, Coras R, Hofer S, Bode-Lesniewska B, Rushing E
J Neuropathol Exp Neurol 2018 Aug 1;77(8):727-735. doi: 10.1093/jnen/nly050. PMID: 29924341
Chow WA
Curr Opin Oncol 2007 Jul;19(4):371-6. doi: 10.1097/CCO.0b013e32812143d9. PMID: 17545802
Murphey MD, Walker EA, Wilson AJ, Kransdorf MJ, Temple HT, Gannon FH
Radiographics 2003 Sep-Oct;23(5):1245-78. doi: 10.1148/rg.235035134. PMID: 12975513
González-Lois C, Cuevas C, Abdullah O, Ricoy JR
Acta Neurochir (Wien) 2002 Jul;144(7):735-40. doi: 10.1007/s00701-002-0949-y. PMID: 12181708

Clinical prediction guides

Toland AMS, Lam SW, Varma S, Wang A, Howitt BE, Kunder CA, Kerr DA, Szuhai K, Bovée JVMG, Charville GW
Am J Surg Pathol 2022 Oct 1;46(10):1407-1414. Epub 2022 Jun 1 doi: 10.1097/PAS.0000000000001921. PMID: 35650682Free PMC Article
Velz J, Agaimy A, Frontzek K, Neidert MC, Bozinov O, Wagner U, Fritz C, Coras R, Hofer S, Bode-Lesniewska B, Rushing E
J Neuropathol Exp Neurol 2018 Aug 1;77(8):727-735. doi: 10.1093/jnen/nly050. PMID: 29924341
Shon W, Folpe AL, Fritchie KJ
J Clin Pathol 2015 Feb;68(2):125-9. Epub 2014 Nov 5 doi: 10.1136/jclinpath-2014-202601. PMID: 25378537
Hemmi A, Osaka S, Sunagawa K, Kikuchi K, Ohno N, Terada N, Fujii Y, Ohno S, Nemoto N
Med Mol Morphol 2009 Sep;42(3):180-4. Epub 2009 Sep 26 doi: 10.1007/s00795-009-0438-y. PMID: 19784746
Goh YW, Spagnolo DV, Platten M, Caterina P, Fisher C, Oliveira AM, Nascimento AG
Histopathology 2001 Nov;39(5):514-24. doi: 10.1046/j.1365-2559.2001.01277.x. PMID: 11737310

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