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Adult Desmoplastic Small Round Cell Tumor

MedGen UID:
272294
Concept ID:
C1332199
Neoplastic Process

Definition

A desmoplastic small round cell tumor occurring in adults. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVAdult Desmoplastic Small Round Cell Tumor

Professional guidelines

PubMed

Suchar AM, Lane J, King AC, Hayes AA, Phelps JR
Paediatr Anaesth 2023 Mar;33(3):193-200. Epub 2022 Sep 8 doi: 10.1111/pan.14551. PMID: 36052662
Jordan AH, Pappo A
J Pediatr Hematol Oncol 2012 May;34 Suppl 2:S73-5. doi: 10.1097/MPH.0b013e31824e38ad. PMID: 22525411
Hayes-Jordan A, Anderson PM
Curr Opin Oncol 2011 Jul;23(4):385-9. doi: 10.1097/CCO.0b013e3283477aab. PMID: 21577112

Recent clinical studies

Etiology

Wang LL, Ji ZH, Gao Y, Chang H, Sun PP, Li Y
World J Surg Oncol 2021 Jun 30;19(1):193. doi: 10.1186/s12957-021-02310-6. PMID: 34193155Free PMC Article
Xiang T, Zhang SY, Wang SS, Fei RS, Li H
Medicine (Baltimore) 2020 Jul 24;99(30):e21337. doi: 10.1097/MD.0000000000021337. PMID: 32791732Free PMC Article
Morani AC, Bathala TK, Surabhi VR, Yedururi S, Jensen CT, Huh WW, Prasad S, Hayes-Jordan A
AJR Am J Roentgenol 2019 Mar;212(3):W45-W54. Epub 2019 Jan 23 doi: 10.2214/AJR.18.20179. PMID: 30673334
Scheer M, Vokuhl C, Blank B, Hallmen E, von Kalle T, Münter M, Wessalowski R, Hartwig M, Sparber-Sauer M, Schlegel PG, Kramm CM, Kontny U, Spriewald B, Kegel T, Bauer S, Kazanowska B, Niggli F, Ladenstein R, Ljungman G, Jahnukainen K, Fuchs J, Bielack SS, Klingebiel T, Koscielniak E; Cooperative Weichteilsarkom Studiengruppe [CWS]
Cancer Med 2019 Feb;8(2):527-542. Epub 2019 Jan 16 doi: 10.1002/cam4.1940. PMID: 30652419Free PMC Article
Leuschner I, Radig K, Harms D
Semin Diagn Pathol 1996 Aug;13(3):204-12. PMID: 8875710

Diagnosis

Jayakrishnan T, Moll R, Sandhu A, Sanguino A, Kaur G, Mao S
Anticancer Res 2021 Aug;41(8):3859-3866. doi: 10.21873/anticanres.15179. PMID: 34281846
Jin D, Chen M, Wang B, Gou Y
Medicine (Baltimore) 2020 Oct 30;99(44):e22921. doi: 10.1097/MD.0000000000022921. PMID: 33126354Free PMC Article
Sbaraglia M, Righi A, Gambarotti M, Dei Tos AP
Virchows Arch 2020 Jan;476(1):109-119. Epub 2019 Dec 4 doi: 10.1007/s00428-019-02720-8. PMID: 31802230
Thway K, Noujaim J, Zaidi S, Miah AB, Benson C, Messiou C, Jones RL, Fisher C
Int J Surg Pathol 2016 Dec;24(8):672-684. Epub 2016 Sep 12 doi: 10.1177/1066896916668637. PMID: 27621277
Hayes-Jordan A, Anderson PM
Curr Opin Oncol 2011 Jul;23(4):385-9. doi: 10.1097/CCO.0b013e3283477aab. PMID: 21577112

Therapy

Hovsepyan S, Giani C, Pasquali S, Di Giannatale A, Chiaravalli S, Colombo C, Orbach D, Bergamaschi L, Vennarini S, Gatz SA, Gasparini P, Berlanga P, Casanova M, Ferrari A
Expert Rev Anticancer Ther 2023 May;23(5):471-484. Epub 2023 Apr 10 doi: 10.1080/14737140.2023.2200171. PMID: 37017324
Jayakrishnan T, Moll R, Sandhu A, Sanguino A, Kaur G, Mao S
Anticancer Res 2021 Aug;41(8):3859-3866. doi: 10.21873/anticanres.15179. PMID: 34281846
Hendricks A, Boerner K, Germer CT, Wiegering A
Cancer Treat Rev 2021 Feb;93:102140. Epub 2020 Dec 24 doi: 10.1016/j.ctrv.2020.102140. PMID: 33388539
Jin D, Chen M, Wang B, Gou Y
Medicine (Baltimore) 2020 Oct 30;99(44):e22921. doi: 10.1097/MD.0000000000022921. PMID: 33126354Free PMC Article
Ahmed N, Brawley VS, Hegde M, Robertson C, Ghazi A, Gerken C, Liu E, Dakhova O, Ashoori A, Corder A, Gray T, Wu MF, Liu H, Hicks J, Rainusso N, Dotti G, Mei Z, Grilley B, Gee A, Rooney CM, Brenner MK, Heslop HE, Wels WS, Wang LL, Anderson P, Gottschalk S
J Clin Oncol 2015 May 20;33(15):1688-96. Epub 2015 Mar 23 doi: 10.1200/JCO.2014.58.0225. PMID: 25800760Free PMC Article

Prognosis

Hovsepyan S, Giani C, Pasquali S, Di Giannatale A, Chiaravalli S, Colombo C, Orbach D, Bergamaschi L, Vennarini S, Gatz SA, Gasparini P, Berlanga P, Casanova M, Ferrari A
Expert Rev Anticancer Ther 2023 May;23(5):471-484. Epub 2023 Apr 10 doi: 10.1080/14737140.2023.2200171. PMID: 37017324
Jayakrishnan T, Moll R, Sandhu A, Sanguino A, Kaur G, Mao S
Anticancer Res 2021 Aug;41(8):3859-3866. doi: 10.21873/anticanres.15179. PMID: 34281846
Jin D, Chen M, Wang B, Gou Y
Medicine (Baltimore) 2020 Oct 30;99(44):e22921. doi: 10.1097/MD.0000000000022921. PMID: 33126354Free PMC Article
Sbaraglia M, Righi A, Gambarotti M, Dei Tos AP
Virchows Arch 2020 Jan;476(1):109-119. Epub 2019 Dec 4 doi: 10.1007/s00428-019-02720-8. PMID: 31802230
Thway K, Noujaim J, Zaidi S, Miah AB, Benson C, Messiou C, Jones RL, Fisher C
Int J Surg Pathol 2016 Dec;24(8):672-684. Epub 2016 Sep 12 doi: 10.1177/1066896916668637. PMID: 27621277

Clinical prediction guides

Jin D, Chen M, Wang B, Gou Y
Medicine (Baltimore) 2020 Oct 30;99(44):e22921. doi: 10.1097/MD.0000000000022921. PMID: 33126354Free PMC Article
Chow WA, Yee JK, Tsark W, Wu X, Qin H, Guan M, Ross JS, Ali SM, Millis SZ
BMC Med Genet 2020 May 11;21(1):101. doi: 10.1186/s12881-020-01034-w. PMID: 32393201Free PMC Article
Yamamoto Y, Nishijima-Matsunobu A, Hiroshima Y, Enomoto K, Inoue M, Muto O, Suzuki M, Nanjo H, Shibata H, Omori Y
Pathol Int 2020 Mar;70(3):171-178. Epub 2020 Jan 15 doi: 10.1111/pin.12897. PMID: 31944485
Sbaraglia M, Righi A, Gambarotti M, Dei Tos AP
Virchows Arch 2020 Jan;476(1):109-119. Epub 2019 Dec 4 doi: 10.1007/s00428-019-02720-8. PMID: 31802230
Chang F
Arch Pathol Lab Med 2006 May;130(5):728-32. doi: 10.5858/2006-130-728-DSRCTC. PMID: 16683894

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