U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Abnormal superior vena cava morphology

MedGen UID:
1631787
Concept ID:
C4703393
Anatomical Abnormality
HPO: HP:0025575

Definition

Any structural anomaly of the principal vein draining blood from the upper portion of the body and delivering it to the right ventricle of the heart. [from HPO]

Professional guidelines

PubMed

Durand I, Hazelzet T, Gillibert A, Parrod C, David N, El Youssef F, Brehin AC, Barre E
Arch Cardiovasc Dis 2022 Jun-Jul;115(6-7):335-347. Epub 2022 May 14 doi: 10.1016/j.acvd.2022.03.005. PMID: 35660361
Keleş A, Yılmaz O, Dağdeviren G, Çelik ÖY, Yücel A, Şahin D
Fetal Pediatr Pathol 2022 Aug;41(4):592-602. Epub 2021 Jun 9 doi: 10.1080/15513815.2021.1933662. PMID: 34106033
Harrison B, Hao F, Koney N, McWilliams J, Moriarty JM
Tech Vasc Interv Radiol 2018 Jun;21(2):65-77. Epub 2018 Mar 9 doi: 10.1053/j.tvir.2018.03.002. PMID: 29784124

Recent clinical studies

Etiology

Esin D, Aslan Çetin B, Şenol G, Selçuki NFT, Gedik Özköse Z, Acar Z, Yüksel MA
J Gynecol Obstet Hum Reprod 2022 Apr;51(4):102332. Epub 2022 Feb 2 doi: 10.1016/j.jogoh.2022.102332. PMID: 35123124
Keleş A, Yılmaz O, Dağdeviren G, Çelik ÖY, Yücel A, Şahin D
Fetal Pediatr Pathol 2022 Aug;41(4):592-602. Epub 2021 Jun 9 doi: 10.1080/15513815.2021.1933662. PMID: 34106033
Minsart AF, Boucoiran I, Delrue MA, Audibert F, Abadir S, Lapierre C, Lemyre E, Raboisson MJ
Pediatr Cardiol 2020 Feb;41(2):230-236. Epub 2019 Nov 13 doi: 10.1007/s00246-019-02246-5. PMID: 31720744
Ramakrishnan D, Chidambarathanu S, Murli L, Micheal J, Jagadeesh S, Suresh I, Seshadri S
Fetal Pediatr Pathol 2017 Aug;36(4):304-310. Epub 2017 Jun 1 doi: 10.1080/15513815.2017.1324546. PMID: 28569558
Chaoui R, Heling KS, Karl K
Ultraschall Med 2014 Aug;35(4):302-18; quiz 319-21. Epub 2014 Aug 15 doi: 10.1055/s-0034-1366848. PMID: 25127225

Diagnosis

Durand I, Hazelzet T, Gillibert A, Parrod C, David N, El Youssef F, Brehin AC, Barre E
Arch Cardiovasc Dis 2022 Jun-Jul;115(6-7):335-347. Epub 2022 May 14 doi: 10.1016/j.acvd.2022.03.005. PMID: 35660361
Esin D, Aslan Çetin B, Şenol G, Selçuki NFT, Gedik Özköse Z, Acar Z, Yüksel MA
J Gynecol Obstet Hum Reprod 2022 Apr;51(4):102332. Epub 2022 Feb 2 doi: 10.1016/j.jogoh.2022.102332. PMID: 35123124
Keleş A, Yılmaz O, Dağdeviren G, Çelik ÖY, Yücel A, Şahin D
Fetal Pediatr Pathol 2022 Aug;41(4):592-602. Epub 2021 Jun 9 doi: 10.1080/15513815.2021.1933662. PMID: 34106033
Ramakrishnan D, Chidambarathanu S, Murli L, Micheal J, Jagadeesh S, Suresh I, Seshadri S
Fetal Pediatr Pathol 2017 Aug;36(4):304-310. Epub 2017 Jun 1 doi: 10.1080/15513815.2017.1324546. PMID: 28569558
Sonavane SK, Milner DM, Singh SP, Abdel Aal AK, Shahir KS, Chaturvedi A
Radiographics 2015 Nov-Dec;35(7):1873-92. Epub 2015 Oct 9 doi: 10.1148/rg.2015150056. PMID: 26452112

Therapy

Steckiewicz R, Stolarz P, Marchel M, Michalak M, Konecki D, Szczerba E, Kowara M, Grabowska-Derlatka L, Grabowski M
Folia Morphol (Warsz) 2022;81(4):1066-1071. Epub 2021 Oct 26 doi: 10.5603/FM.a2021.0108. PMID: 34699053
Rudrappa SC, Aggarwal N, Joshi R, Joshi R
Semin Thorac Cardiovasc Surg 2019 Autumn;31(3):571-572. Epub 2019 Apr 19 doi: 10.1053/j.semtcvs.2019.04.009. PMID: 31005577
Emmi G, Bettiol A, Silvestri E, Di Scala G, Becatti M, Fiorillo C, Prisco D
Intern Emerg Med 2019 Aug;14(5):645-652. Epub 2018 Nov 29 doi: 10.1007/s11739-018-1991-y. PMID: 30499073
Aguilar JM, Rodríguez-Serrano F, Ferreiro-Marzal A, Esteban-Molina M, Gabucio A, García E, Boni L, Garrido JM
Arch Cardiovasc Dis 2019 Feb;112(2):135-143. Epub 2018 Sep 1 doi: 10.1016/j.acvd.2018.05.007. PMID: 30181052
Harrison B, Hao F, Koney N, McWilliams J, Moriarty JM
Tech Vasc Interv Radiol 2018 Jun;21(2):65-77. Epub 2018 Mar 9 doi: 10.1053/j.tvir.2018.03.002. PMID: 29784124

Prognosis

Esin D, Aslan Çetin B, Şenol G, Selçuki NFT, Gedik Özköse Z, Acar Z, Yüksel MA
J Gynecol Obstet Hum Reprod 2022 Apr;51(4):102332. Epub 2022 Feb 2 doi: 10.1016/j.jogoh.2022.102332. PMID: 35123124
Batouty NM, Sobh DM, Gadelhak B, Sobh HM, Mahmoud W, Tawfik AM
Radiol Med 2020 Mar;125(3):237-246. Epub 2019 Dec 10 doi: 10.1007/s11547-019-01114-9. PMID: 31823296
Derbel B, Krarti N, Ghedira F, Ben Mrad M, Hedhli M, Ziadi J, Denguir R
J Med Vasc 2019 Sep;44(5):354-358. Epub 2019 Aug 7 doi: 10.1016/j.jdmv.2019.06.005. PMID: 31474348
Nair V, Yusuf K, Yu W, AlAwad H, Paul K, Al Awad E
Pediatr Dev Pathol 2017 Mar-Apr;20(2):182-185. Epub 2017 Jan 25 doi: 10.1177/1093526616686008. PMID: 28326958
Rossi SE, McAdams HP, Rosado-de-Christenson ML, Franks TJ, Galvin JR
Radiographics 2001 May-Jun;21(3):737-57. doi: 10.1148/radiographics.21.3.g01ma17737. PMID: 11353121

Clinical prediction guides

Esin D, Aslan Çetin B, Şenol G, Selçuki NFT, Gedik Özköse Z, Acar Z, Yüksel MA
J Gynecol Obstet Hum Reprod 2022 Apr;51(4):102332. Epub 2022 Feb 2 doi: 10.1016/j.jogoh.2022.102332. PMID: 35123124
Hasegawa M, Tominaga Y, Watanabe T, Ueno T, Taira M, Miyagawa S
Ann Thorac Surg 2022 Jul;114(1):e9-e11. Epub 2021 Nov 13 doi: 10.1016/j.athoracsur.2021.09.074. PMID: 34780765
Derbel B, Krarti N, Ghedira F, Ben Mrad M, Hedhli M, Ziadi J, Denguir R
J Med Vasc 2019 Sep;44(5):354-358. Epub 2019 Aug 7 doi: 10.1016/j.jdmv.2019.06.005. PMID: 31474348
Tyrak KW, Holda J, Holda MK, Koziej M, Piatek K, Klimek-Piotrowska W
Cardiovasc J Afr 2017 May 23;28(3):e1-e4. doi: 10.5830/CVJA-2016-084. PMID: 28759082Free PMC Article
Li J, Mao Q, Sun Z, Li Q
Surg Radiol Anat 2017 Jan;39(1):107-109. Epub 2016 Jun 1 doi: 10.1007/s00276-016-1705-y. PMID: 27250599

Recent systematic reviews

Al-Sinan A, Chan KH, Young GD, Martin A, Sepahpour A, Sy RW
J Cardiovasc Electrophysiol 2022 Jun;33(6):1300-1311. Epub 2022 Apr 30 doi: 10.1111/jce.15505. PMID: 35441755Free PMC Article

Supplemental Content

Table of contents

    Clinical resources

    Practice guidelines

    • PubMed
      See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.
    • Bookshelf
      See practice and clinical guidelines in NCBI Bookshelf. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Consumer resources

    Recent activity

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...