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Unresectable Malignant Gastrointestinal Stromal Tumor

MedGen UID:
1670607
Concept ID:
C4725953
Neoplastic Process
Synonym: Unresectable Gastrointestinal Stromal Tumor

Definition

Malignant gastrointestinal stromal tumor that is not amenable to surgical resection. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVUnresectable Malignant Gastrointestinal Stromal Tumor

Professional guidelines

PubMed

Naito Y, Nishida T, Doi T
Gastric Cancer 2023 May;26(3):339-351. Epub 2023 Mar 13 doi: 10.1007/s10120-023-01381-6. PMID: 36913072Free PMC Article
Foo T, Goldstein D, Segelov E, Shapiro J, Pavlakis N, Desai J, Yip D, Zalcberg J, Price TJ, Nagrial A, Chantrill L, Burge M, Karapetis CS, Tebbutt N, Roy AC
Target Oncol 2022 Mar;17(2):95-110. Epub 2022 Mar 15 doi: 10.1007/s11523-022-00869-y. PMID: 35290591Free PMC Article
Qian XH, Yan YC, Gao BQ, Wang WL
World J Gastroenterol 2020 Oct 28;26(40):6195-6206. doi: 10.3748/wjg.v26.i40.6195. PMID: 33177793Free PMC Article

Recent clinical studies

Etiology

Naito Y, Nishida T, Doi T
Gastric Cancer 2023 May;26(3):339-351. Epub 2023 Mar 13 doi: 10.1007/s10120-023-01381-6. PMID: 36913072Free PMC Article
Foo T, Goldstein D, Segelov E, Shapiro J, Pavlakis N, Desai J, Yip D, Zalcberg J, Price TJ, Nagrial A, Chantrill L, Burge M, Karapetis CS, Tebbutt N, Roy AC
Target Oncol 2022 Mar;17(2):95-110. Epub 2022 Mar 15 doi: 10.1007/s11523-022-00869-y. PMID: 35290591Free PMC Article
Heinrich MC, Jones RL, von Mehren M, Schöffski P, Serrano C, Kang YK, Cassier PA, Mir O, Eskens F, Tap WD, Rutkowski P, Chawla SP, Trent J, Tugnait M, Evans EK, Lauz T, Zhou T, Roche M, Wolf BB, Bauer S, George S
Lancet Oncol 2020 Jul;21(7):935-946. doi: 10.1016/S1470-2045(20)30269-2. PMID: 32615108
Ozkan EE
Chin Med J (Engl) 2018 Jan 20;131(2):235-240. doi: 10.4103/0366-6999.222344. PMID: 29336374Free PMC Article
Demetri GD, Reichardt P, Kang YK, Blay JY, Rutkowski P, Gelderblom H, Hohenberger P, Leahy M, von Mehren M, Joensuu H, Badalamenti G, Blackstein M, Le Cesne A, Schöffski P, Maki RG, Bauer S, Nguyen BB, Xu J, Nishida T, Chung J, Kappeler C, Kuss I, Laurent D, Casali PG; GRID study investigators
Lancet 2013 Jan 26;381(9863):295-302. Epub 2012 Nov 22 doi: 10.1016/S0140-6736(12)61857-1. PMID: 23177515Free PMC Article

Diagnosis

von Mehren M, Kane JM, Riedel RF, Sicklick JK, Pollack SM, Agulnik M, Bui MM, Carr-Ascher J, Choy E, Connelly M, Dry S, Ganjoo KN, Gonzalez RJ, Holder A, Homsi J, Keedy V, Kelly CM, Kim E, Liebner D, McCarter M, McGarry SV, Mesko NW, Meyer C, Pappo AS, Parkes AM, Petersen IA, Poppe M, Schuetze S, Shabason J, Spraker MB, Zimel M, Bergman MA, Sundar H, Hang LE
J Natl Compr Canc Netw 2022 Nov;20(11):1204-1214. doi: 10.6004/jnccn.2022.0058. PMID: 36351335Free PMC Article
Qian XH, Yan YC, Gao BQ, Wang WL
World J Gastroenterol 2020 Oct 28;26(40):6195-6206. doi: 10.3748/wjg.v26.i40.6195. PMID: 33177793Free PMC Article
Sanchez-Hidalgo JM, Duran-Martinez M, Molero-Payan R, Rufian-Peña S, Arjona-Sanchez A, Casado-Adam A, Cosano-Alvarez A, Briceño-Delgado J
World J Gastroenterol 2018 May 14;24(18):1925-1941. doi: 10.3748/wjg.v24.i18.1925. PMID: 29760538Free PMC Article
Iorio N, Sawaya RA, Friedenberg FK
Aliment Pharmacol Ther 2014 Jun;39(12):1376-86. Epub 2014 Apr 20 doi: 10.1111/apt.12761. PMID: 24749828
Beham AW, Schaefer IM, Schüler P, Cameron S, Ghadimi BM
Int J Colorectal Dis 2012 Jun;27(6):689-700. Epub 2011 Nov 29 doi: 10.1007/s00384-011-1353-y. PMID: 22124674Free PMC Article

Therapy

Naito Y, Nishida T, Doi T
Gastric Cancer 2023 May;26(3):339-351. Epub 2023 Mar 13 doi: 10.1007/s10120-023-01381-6. PMID: 36913072Free PMC Article
Jones RL, Serrano C, von Mehren M, George S, Heinrich MC, Kang YK, Schöffski P, Cassier PA, Mir O, Chawla SP, Eskens FALM, Rutkowski P, Tap WD, Zhou T, Roche M, Bauer S
Eur J Cancer 2021 Mar;145:132-142. Epub 2021 Jan 16 doi: 10.1016/j.ejca.2020.12.008. PMID: 33465704Free PMC Article
Heng DY, Kollmannsberger C
Recent Results Cancer Res 2010;184:71-82. doi: 10.1007/978-3-642-01222-8_6. PMID: 20072832
Demetri GD, van Oosterom AT, Garrett CR, Blackstein ME, Shah MH, Verweij J, McArthur G, Judson IR, Heinrich MC, Morgan JA, Desai J, Fletcher CD, George S, Bello CL, Huang X, Baum CM, Casali PG
Lancet 2006 Oct 14;368(9544):1329-38. doi: 10.1016/S0140-6736(06)69446-4. PMID: 17046465
Demetri GD, von Mehren M, Blanke CD, Van den Abbeele AD, Eisenberg B, Roberts PJ, Heinrich MC, Tuveson DA, Singer S, Janicek M, Fletcher JA, Silverman SG, Silberman SL, Capdeville R, Kiese B, Peng B, Dimitrijevic S, Druker BJ, Corless C, Fletcher CD, Joensuu H
N Engl J Med 2002 Aug 15;347(7):472-80. doi: 10.1056/NEJMoa020461. PMID: 12181401

Prognosis

Naito Y, Nishida T, Doi T
Gastric Cancer 2023 May;26(3):339-351. Epub 2023 Mar 13 doi: 10.1007/s10120-023-01381-6. PMID: 36913072Free PMC Article
Jones RL, Serrano C, von Mehren M, George S, Heinrich MC, Kang YK, Schöffski P, Cassier PA, Mir O, Chawla SP, Eskens FALM, Rutkowski P, Tap WD, Zhou T, Roche M, Bauer S
Eur J Cancer 2021 Mar;145:132-142. Epub 2021 Jan 16 doi: 10.1016/j.ejca.2020.12.008. PMID: 33465704Free PMC Article
Qian XH, Yan YC, Gao BQ, Wang WL
World J Gastroenterol 2020 Oct 28;26(40):6195-6206. doi: 10.3748/wjg.v26.i40.6195. PMID: 33177793Free PMC Article
Heinrich MC, Jones RL, von Mehren M, Schöffski P, Serrano C, Kang YK, Cassier PA, Mir O, Eskens F, Tap WD, Rutkowski P, Chawla SP, Trent J, Tugnait M, Evans EK, Lauz T, Zhou T, Roche M, Wolf BB, Bauer S, George S
Lancet Oncol 2020 Jul;21(7):935-946. doi: 10.1016/S1470-2045(20)30269-2. PMID: 32615108
Demetri GD, Reichardt P, Kang YK, Blay JY, Rutkowski P, Gelderblom H, Hohenberger P, Leahy M, von Mehren M, Joensuu H, Badalamenti G, Blackstein M, Le Cesne A, Schöffski P, Maki RG, Bauer S, Nguyen BB, Xu J, Nishida T, Chung J, Kappeler C, Kuss I, Laurent D, Casali PG; GRID study investigators
Lancet 2013 Jan 26;381(9863):295-302. Epub 2012 Nov 22 doi: 10.1016/S0140-6736(12)61857-1. PMID: 23177515Free PMC Article

Clinical prediction guides

Senchak J, Ahr K, von Mehren M
Curr Treat Options Oncol 2022 May;23(5):749-761. Epub 2022 Mar 28 doi: 10.1007/s11864-022-00958-0. PMID: 35349049
Vallilas C, Sarantis P, Kyriazoglou A, Koustas E, Theocharis S, Papavassiliou AG, Karamouzis MV
Int J Mol Sci 2021 Jan 6;22(2) doi: 10.3390/ijms22020493. PMID: 33419029Free PMC Article
Heinrich MC, Jones RL, von Mehren M, Schöffski P, Serrano C, Kang YK, Cassier PA, Mir O, Eskens F, Tap WD, Rutkowski P, Chawla SP, Trent J, Tugnait M, Evans EK, Lauz T, Zhou T, Roche M, Wolf BB, Bauer S, George S
Lancet Oncol 2020 Jul;21(7):935-946. doi: 10.1016/S1470-2045(20)30269-2. PMID: 32615108
Grothey A, Blay JY, Pavlakis N, Yoshino T, Bruix J
Cancer Treat Rev 2020 Jun;86:101993. Epub 2020 Feb 20 doi: 10.1016/j.ctrv.2020.101993. PMID: 32199197
Rajendra R, Pollack SM, Jones RL
Future Oncol 2013 Feb;9(2):193-206. doi: 10.2217/fon.12.178. PMID: 23414470

Recent systematic reviews

Bellefkih FZ, Benchakroun N, Lalya I, Amaoui B, El Kacemi H, Acharki A, El Hfid M, El Mazghi A, Chekrine T, Bouchbika Z, Jouhadi H, Sahraoui S, Tawfiq N, Michalet M
Cancer Radiother 2023 Sep;27(6-7):622-637. Epub 2023 Jul 25 doi: 10.1016/j.canrad.2023.06.010. PMID: 37500390
Hislop J, Quayyum Z, Elders A, Fraser C, Jenkinson D, Mowatt G, Sharma P, Vale L, Petty R
Health Technol Assess 2011 Jun;15(25):1-178. doi: 10.3310/hta15250. PMID: 21689502Free PMC Article
Cirocchi R, Farinella E, La Mura F, Cavaliere D, Avenia N, Verdecchia GM, Giustozzi G, Noya G, Sciannameo F
Tumori 2010 May-Jun;96(3):392-9. doi: 10.1177/030089161009600303. PMID: 20845798
Ye YJ, Gao ZD, Poston GJ, Wang S
Eur J Surg Oncol 2009 Aug;35(8):787-92. Epub 2009 Jan 29 doi: 10.1016/j.ejso.2009.01.003. PMID: 19185444
Wilson J, Connock M, Song F, Yao G, Fry-Smith A, Raftery J, Peake D
Health Technol Assess 2005 Jul;9(25):1-142. doi: 10.3310/hta9250. PMID: 15985189

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